Both granulocytic and non-granulocytic blood cells are affected in patients with severe congenital neutropenia and their non-neutropenic family members: An evaluation of morphology, function, and cell death;Ciddi konjenital nötropenisi olan hastalarda ve nötropenik olmayan ebeveynlerinde hem granülositik hem granülositik olmayan kan hücreleri etkilenir: Morfoloji, fonksiyon ve hücre ölümü yönünden bir değerlendirme

Turkish Journal of Hematology

Volumn 35, Issue 4, 2018, Pages 229-259

  Olcay, Lale ^a   Ünal, Şule ^b   Onay, Hüseyin ^c   Erdemli, Esra ^d   Öztürk, Ayşenur ^d   Billur, Deniz ^d   Metin, Ayşe ^e   Okur, Hamza ^b   Yıldırmak, Yıldız ^f   Büyükaşık, Yahya ^b   İkincioğulları, Aydan ^d   Falay, Mesude ^g   Özet, Gülsüm ^g,h   Yetgin, Sevgi ^b  

^a ANKARA ONCOLOGY EDUCATION AND RESEARCH HOSPITAL   (Turkey)

^b HACETTEPE UNIVERSITY   (Turkey)

^c EGE UNIVERSITY   (Turkey)

^d ANKARA UNIVERSITY   (Turkey)

^e Ankara Children's Diseases and Hematology Oncology Training Hospital   (Turkey)

^f Sisli Etfal Children Hospital   (Turkey)

^g ANKARA TRAINING AND RESEARCH HOSPITAL   (Turkey)

^h YILDIRIM BEYAZIT UNIVERSITY   (Turkey)

Author keywords

Apoptosis; Family; Lymphocytes; Monocytes; NK cells; Parents; Phagocytes; Senescence; Severe congenital neutropenia; Thrombocytes

Indexed keywords

COLONY STIMULATING FACTOR RECEPTOR; FAS LIGAND; GRANULOCYTE COLONY STIMULATING FACTOR; HCLS1 ASSOCIATED PROTEIN X 1; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; LIPOCORTIN 5; PROPIDIUM IODIDE; PROTEIN JAGGED 1; TUMOR NECROSIS FACTOR RECEPTOR SUPERFAMILY MEMBER 6; UNCLASSIFIED DRUG;

ADOLESCENT; ADULT; ARTICLE; BLEEDING TENDENCY; BLEEDING TIME; BONE MARROW BIOPSY; CELL AGING; CELL DEATH; CELL FUNCTION; CELL PROLIFERATION; CELL STRUCTURE; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; CSF3R GENE; CYTOPENIA; ELANE GENE; FEMALE; FLOW CYTOMETRY; FLUORESCENCE MICROSCOPY; G6PC3 GENE; GENE; GENE MUTATION; GRANULOCYTE; HAX1 GENE; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE TEST; JAGN1 GENE; LEUKOCYTE COUNT; MALE; MEGAKARYOPOIESIS; MONOCYTE COUNT; NEUTROPHIL COUNT; SEVERE CONGENITAL NEUTROPENIA; THROMBOCYTE; THROMBOCYTE AGGREGATION; THROMBOCYTE FUNCTION; TRANSMISSION ELECTRON MICROSCOPY; YOUNG ADULT; INFANT; LYMPHOCYTE; METABOLISM; MIDDLE AGED; NEUTROPENIA; NEUTROPHIL; PATHOLOGY; PRESCHOOL CHILD;

ADOLESCENT; ADULT; CELL DEATH; CHILD; CHILD, PRESCHOOL; FEMALE; GRANULOCYTES; HUMANS; INFANT; LYMPHOCYTES; MALE; MIDDLE AGED; NEUTROPENIA; NEUTROPHILS; YOUNG ADULT;

EID: 85056297204     PISSN: 13007777     EISSN: 13085263     Source Type: Journal    
DOI: 10.4274/tjh.2017.0160     Document Type: Article

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