Motor neuron mitochondrial dysfunction in spinal muscular atrophy

Human Molecular Genetics

Volumn 25, Issue 16, 2016, Pages 3395-3406

  Miller, Nimrod ^a   Shi, Han ^a   Zelikovich, Aaron S ^a   Ma, Yong Chao ^a  

^a NORTHWESTERN UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

TRANSCRIPTOME;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOENERGY; CELL FUNCTION; COMPARATIVE STUDY; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FEMALE; FLUORESCENCE; GENETIC ASSOCIATION; LAMELLAR BODY; MALE; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MITOCHONDRION; MOTOR NEURON MITOCHONDRIAL DYSFUNCTION; MOUSE; NERVE FIBER TRANSPORT; NONHUMAN; OXIDATION REDUCTION REACTION; OXIDATIVE STRESS; PRIORITY JOURNAL; RETROGRADE NERVE FIBER TRANSPORT; SPINAL CORD MOTONEURON; SPINAL MUSCULAR ATROPHY; TRANSMISSION ELECTRON MICROSCOPY; ANIMAL; CARDIAC MUSCLE; DISEASE MODEL; ELECTRON MICROSCOPY; GENETICS; HIGH THROUGHPUT SEQUENCING; HUMAN; METABOLISM; MOTONEURON; PATHOLOGY; PATHOPHYSIOLOGY; SKELETAL MUSCLE; SPINAL CORD; ULTRASTRUCTURE;

ANIMALS; DISEASE MODELS, ANIMAL; HIGH-THROUGHPUT NUCLEOTIDE SEQUENCING; HUMANS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MICE; MICROSCOPY, ELECTRON; MITOCHONDRIA; MOTOR NEURONS; MUSCLE, SKELETAL; MUSCULAR ATROPHY, SPINAL; MYOCARDIUM; OXIDATIVE STRESS; SPINAL CORD; TRANSCRIPTOME;

EID: 85014409973     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw262     Document Type: Article

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