Effect of genetic background on the phenotype of the Smn2B/- mouse model of spinal muscular atrophy

Human Molecular Genetics

Volumn 25, Issue 20, 2016, Pages 4494-4506

  Eshraghi, Mehdi ^a,b   McFall, Emily ^a,b   Gibeault, Sabrina ^a,b   Kothary, Rashmi ^a,b  

^a OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF OTTAWA   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ACTIN; SURVIVAL MOTOR NEURON PROTEIN; SURVIVAL MOTOR NEURON PROTEIN 2B; UNCLASSIFIED DRUG; SMN1 PROTEIN, MOUSE; SURVIVAL MOTOR NEURON PROTEIN 1;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LOSS; COMPARATIVE STUDY; CONTROLLED STUDY; DISEASE SEVERITY; FEMALE; GENE; GENE CONTROL; GENETIC BACKGROUND; GROWTH; LOCOMOTION; MALE; MODIFIER GENE; MOTONEURON; MOUSE; MOUSE MODEL; MUSCLE ATROPHY; MUSCLE STRENGTH; NEUROMUSCULAR JUNCTION; NONHUMAN; PATHOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; SMN 2B GENE; SPINAL CORD; SPINAL MUSCULAR ATROPHY; SURVIVAL; WEIGHT REDUCTION; ANIMAL; DISEASE MODEL; GENETICS; INBRED MOUSE STRAIN; METABOLISM;

ANIMALS; DISEASE MODELS, ANIMAL; FEMALE; GENETIC BACKGROUND; MALE; MICE; MICE, INBRED STRAINS; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; NEUROMUSCULAR JUNCTION; PHENOTYPE; SURVIVAL OF MOTOR NEURON 1 PROTEIN;

EID: 85014357717     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddw278     Document Type: Article

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