CLPP coordinates mitoribosomal assembly through the regulation of ERAL1 levels

EMBO Journal

Volumn 35, Issue 23, 2016, Pages 2566-2583

  Szczepanowska, Karolina ^a,b   Maiti, Priyanka ^a,b   Kukat, Alexandra ^a,b   Hofsetz, Eduard ^a,b   Nolte, Hendrik ^a,b   Senft, Katharina ^a,b   Becker, Christina ^a,b   Ruzzenente, Benedetta ^c   Hornig Do, Hue Tran ^a,b   Wibom, Rolf ^d   Wiesner, Rudolf J ^a,b   Krüger, Marcus ^a,b   Trifunovic, Aleksandra ^a,b  

^a UNIVERSITY OF COLOGNE   (Germany)

^b UNIVERSITY OF COLOGNE   (Germany)

^c MAX PLANCK INSTITUTE FOR BIOLOGY OF AGEING   (Germany)

^d KAROLINSKA INSTITUTE   (Sweden)

Author keywords

CLPP; ERAL1; mitochondrial ribosome assembly; OXPHOS deficiency

Indexed keywords

ACTIN; CHAPERONE; ENDOPEPTIDASE CLP; ENDOPEPTIDASE CLPX; ERAL1 PROTEIN; MESSENGER RNA; MITOCHONDRIAL PROTEIN; MITOCHONDRIAL RNA; RIBOSOME RNA; UNCLASSIFIED DRUG; CLPP PROTEIN, MOUSE; ERA PROTEIN, MOUSE; GUANINE NUCLEOTIDE BINDING PROTEIN; RNA BINDING PROTEIN;

ANIMAL EXPERIMENT; ARTICLE; HEART MITOCHONDRION; KNOCKOUT MOUSE; METABOLISM; MITOCHONDRIAL RIBOSOME; MITOCHONDRION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN SYNTHESIS; RESPIRATORY CHAIN; RESPIRATORY FAILURE; SMALL RIBOSOMAL SUBUNIT; ANIMAL; CELL CULTURE; FIBROBLAST; PHYSIOLOGY; RIBOSOME;

ANIMALS; CELLS, CULTURED; ENDOPEPTIDASE CLP; FIBROBLASTS; GTP-BINDING PROTEINS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; PROTEIN BIOSYNTHESIS; RIBOSOMES; RNA-BINDING PROTEINS;

EID: 84997521955     PISSN: 02614189     EISSN: 14602075     Source Type: Journal    
DOI: 10.15252/embj.201694253     Document Type: Article

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