Tendon extracellular matrix alterations in ullrich congenital muscular dystrophy

Frontiers in Aging Neuroscience

Volumn 8, Issue JUN, 2016, Pages

  Sardone, Francesca ^a,b   Traina, Francesco ^c   Bondi, Alice ^c   Merlini, Luciano ^d   Santi, Spartaco ^b,e   Maraldi, Nadir Mario ^b,e   Faldini, Cesare ^c   Sabatelli, Patrizia ^b,e  

^a UNIVERSITY OF PADOVA   (Italy)

^b CNR   (Italy)

^c UNIVERSITY OF BOLOGNA   (Italy)

^d Villa Erbosa Hospital   (Italy)

^e RIZZOLI ORTHOPAEDIC INSTITUTE   (Italy)

Author keywords

Collagen VI; Metalloproteinases; Pericellular matrix; Tendon; Ullrich congenital muscular dystrophy (UCMD)

Indexed keywords

COLLAGEN TYPE 1; COLLAGEN TYPE 6; FIBRONECTIN; GELATINASE A;

ADOLESCENT; ADULT; ARTICLE; CELL SURFACE; COL6A2 GENE; CONTROLLED STUDY; EXTRACELLULAR MATRIX; GENE; GENE MUTATION; HETEROZYGOSITY; HUMAN; HUMAN CELL; HUMAN TISSUE; MUSCLE CELL; MUSCULAR DYSTROPHY; PATHOGENESIS; PERONEUS MUSCLE; PROTEIN ASSEMBLY; TENDON; TENOCYTE; ULLRICH CONGENITAL MUSCULAR DYSTROPHY; YOUNG ADULT;

EID: 84980340006     PISSN: None     EISSN: 16634365     Source Type: Journal    
DOI: 10.3389/fnagi.2016.00131     Document Type: Article

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