Genetic analysis of the contribution of LTBP-3 to thoracic aneurysm in Marfan syndrome

Proceedings of the National Academy of Sciences of the United States of America

Volumn 112, Issue 45, 2015, Pages 14012-14017

  Zilberberg, Lior ^a   Phoon, Colin K L ^a   Robertson, Ian ^a   Dabovic, Branka ^a   Ramirez, Francesco ^b   Rifkin, Daniel B ^a  

^a NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COLLAGEN TYPE 1; CONNECTIVE TISSUE GROWTH FACTOR; ELASTIN; FIBRILLIN 1; FIBRONECTIN; LATENT TRANSFORMING GROWTH FACTOR BETA BINDING PROTEIN 3; MACROPHAGE ELASTASE; MESSENGER RNA; MITOGEN ACTIVATED PROTEIN KINASE 1; MITOGEN ACTIVATED PROTEIN KINASE 3; PLASMINOGEN ACTIVATOR INHIBITOR 1; SMAD2 PROTEIN; SMAD3 PROTEIN; TRANSFORMING GROWTH FACTOR BETA; UNCLASSIFIED DRUG; ACTIN BINDING PROTEIN; COMPLEMENTARY DNA; FBN1 PROTEIN, MOUSE; FIBRILLIN; LATENT TRANSFORMING GROWTH FACTOR BETA BINDING PROTEIN; LTBP3 PROTEIN, MOUSE; MULTIPROTEIN COMPLEX;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; AORTA; ASCENDING AORTA; CONFERENCE PAPER; ELASTIC FIBER; ENZYME ACTIVATION; GENE DELETION; GENE EXPRESSION; GENETIC ANALYSIS; IMMUNOREACTIVITY; MARFAN SYNDROME; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; SIGNAL TRANSDUCTION; THORACIC AORTA ANEURYSM; TRANSTHORACIC ECHOCARDIOGRAPHY; WESTERN BLOTTING; ANALYSIS OF VARIANCE; ANIMAL; AORTIC ANEURYSM, THORACIC; BIOSYNTHESIS; COMPLICATION; CYTOLOGY; DEFICIENCY; GENETICS; IMMUNOHISTOCHEMISTRY; METABOLISM; REAL TIME POLYMERASE CHAIN REACTION; VASCULAR SMOOTH MUSCLE;

ANALYSIS OF VARIANCE; ANIMALS; AORTIC ANEURYSM, THORACIC; DNA, COMPLEMENTARY; FIBRILLIN-1; FIBRILLINS; IMMUNOHISTOCHEMISTRY; LATENT TGF-BETA BINDING PROTEINS; MARFAN SYNDROME; MICE; MICROFILAMENT PROTEINS; MULTIPROTEIN COMPLEXES; MUSCLE, SMOOTH, VASCULAR; REAL-TIME POLYMERASE CHAIN REACTION; TRANSFORMING GROWTH FACTOR BETA;

EID: 84946781153     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1507652112     Document Type: Article

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