Latent TGF-β binding protein-2 is essential for the development of ciliary zonule microfibrils

Human Molecular Genetics

Volumn 23, Issue 21, 2014, Pages 5672-5682

  Inoue, Tadashi ^a   Ohbayashi, Tetsuya ^b   Fujikawa, Yusuke ^a   Yoshida, Hideyuki ^a   Akama, Tomoya O ^a,c   Noda, Kazuo ^a,d   Horiguchi, Masahito ^e   Kameyama, Katsuro ^b   Hata, Yoshio ^b   Takahashi, Kanji ^a   Kusumoto, Kenji ^a   Nakamura, Tomoyuki ^a  

^a KANSAI MEDICAL UNIVERSITY   (Japan)

^b TOTTORI UNIVERSITY   (Japan)

^c BURNHAM INSTITUTE   (United States)

^d KYOTO UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

^e NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FIBRILLIN 1; MUTANT PROTEIN; SMALL INTERFERING RNA; TRANSFORMING GROWTH FACTOR BETA2; ACTIN BINDING PROTEIN; FIBRILLIN; LATENT TRANSFORMING GROWTH FACTOR BETA BINDING PROTEIN; LTBP2 PROTEIN, HUMAN; PROTEIN BINDING;

ADULT; ADULTHOOD; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BINDING SITE; CELL STRUCTURE; CILIARY ZONULE MICROFIBRIL; CONTROLLED STUDY; CULTURE MEDIUM; EPITHELIUM CELL; FIBER; GLAUCOMA; HUMAN; HUMAN CELL; HUMAN TISSUE; LENS LUXATION; MOUSE; MUTANT; NONHUMAN; ORGAN CULTURE; PHENOTYPE; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN SECRETION; PROTEIN STRUCTURE; ANIMAL; CELL LINE; ECTOPIA LENTIS; EUKARYOTIC FLAGELLUM; GENE INACTIVATION; GENE TARGETING; GENETICS; GENOTYPE; KNOCKOUT MOUSE; METABOLISM; MUTATION; PATHOLOGY;

ANIMALS; CELL LINE; CILIA; ECTOPIA LENTIS; EPITHELIAL CELLS; GENE KNOCKOUT TECHNIQUES; GENE TARGETING; GENOTYPE; GLAUCOMA; HUMANS; LATENT TGF-BETA BINDING PROTEINS; MICE; MICE, KNOCKOUT; MICROFIBRILS; MICROFILAMENT PROTEINS; MUTATION; PHENOTYPE; PROTEIN BINDING;

EID: 84911448979     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddu283     Document Type: Article

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