Endurance training ameliorates complex 3 deficiency in a mouse model of Barth syndrome

Journal of Inherited Metabolic Disease

Volumn 38, Issue 5, 2015, Pages 915-922

  Soustek, Meghan S ^a   Baligand, Celine ^b   Falk, Darin J ^a   Walter, Glenn A ^b   Lewin, Alfred S ^b   Byrne, Barry J ^a,b  

^a UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

^b UNIVERSITY OF FLORIDA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA; PROTEIN; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); TAFAZZIN; UBIQUINOL CYTOCHROME C REDUCTASE; UNCLASSIFIED DRUG; TAZ PROTEIN, MOUSE; TRANSCRIPTION FACTOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BARTH SYNDROME; CARDIOVASCULAR MAGNETIC RESONANCE; CELL PH; COMPLEX III DEFICIENCY; CONTROLLED STUDY; ELECTROSTIMULATION; ENDURANCE TRAINING; ENZYME ACTIVITY; GASTROCNEMIUS MUSCLE; GENE MUTATION; GENOTYPE; HEART EJECTION FRACTION; HEART LEFT VENTRICLE ENDDIASTOLIC VOLUME; HEART LEFT VENTRICLE MASS; HEART MUSCLE; HEART STROKE VOLUME; HEART VENTRICLE HYPERTROPHY; KNOCKOUT GENE; MOUSE; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PHENOTYPE; PHOSPHORUS NUCLEAR MAGNETIC RESONANCE; SKELETAL MUSCLE; SOLEUS MUSCLE; TIBIALIS ANTERIOR MUSCLE; WESTERN BLOTTING; ANIMAL; DEFICIENCY; DISEASE MODEL; ENDURANCE; EXERCISE; EXERCISE TOLERANCE; GENETICS; HUMAN; KNOCKOUT MOUSE; METABOLISM; PATHOLOGY; PHYSIOLOGY;

ANIMALS; BARTH SYNDROME; DISEASE MODELS, ANIMAL; ELECTRON TRANSPORT COMPLEX III; EXERCISE; EXERCISE TOLERANCE; HUMANS; MICE; MICE, KNOCKOUT; PHYSICAL CONDITIONING, ANIMAL; PHYSICAL ENDURANCE; REACTIVE OXYGEN SPECIES; TRANSCRIPTION FACTORS;

EID: 84940378089     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-015-9834-8     Document Type: Article

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