Primary immunodeficiency update: Part II. Syndromes associated with mucocutaneous candidiasis and noninfectious cutaneous manifestations

Journal of the American Academy of Dermatology

Volumn 73, Issue 3, 2015, Pages 367-381

  Pichard, Dominique C ^a   Freeman, Alexandra F ^b   Cowen, Edward W ^a  

^a NATIONAL CANCER INSTITUTE   (United States)

^b NATIONAL INSTITUTE OF ALLERGY AND INFECTIOUS DISEASES   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

INTERLEUKIN 17; INTERLEUKIN 17 RECEPTOR; PLERIXAFOR;

ACUTE MYELOBLASTIC LEUKEMIA; ADDISON DISEASE; ADENOSINE DEAMINASE DEFICIENCY; ALOPECIA; ATAXIA TELANGIECTASIA; AUTOIMMUNE DISEASE; AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY; AUTOSOMAL DOMINANT DISORDER; AUTOSOMAL RECESSIVE DISORDER; CANDIDIASIS; CARD9 DEFICIENCY; CARD9 GENE; CHRONIC GRANULOMATOUS DISEASE; COLD URTICARIA; COMMON VARIABLE IMMUNODEFICIENCY; DECTIN 1 GENE; DERMATITIS; DERMATOFIBROSARCOMA PROTUBERANS; DERMATOPHYTOSIS; ECTODERMAL DYSPLASIA; ECZEMA; GAIN OF FUNCTION MUTATION; GENE; GENE MUTATION; GRANULOMA; GRANULOMATOUS SKIN DISEASE; HIGH RISK PATIENT; HUMAN; HUMORAL IMMUNE DEFICIENCY; HYPOPARATHYROIDISM; IMMUNE DEFICIENCY; IMMUNOGLOBULIN DEFICIENCY; IMMUNOLOGICAL TOLERANCE; MEDICAL EDUCATION; MONOGENIC DISORDER; MUCOCUTANEOUS CANDIDIASIS; MYELODYSPLASTIC SYNDROME; NAIL DYSTROPHY; NIJMEGEN BREAKAGE SYNDROME; ONSET AGE; PAPILLOMAVIRUS INFECTION; PATHOPHYSIOLOGY; POLYENDOCRINOPATHY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; RAG GENE; RECURRENT INFECTION; REVIEW; SKIN LUPUS ERYTHEMATOSUS; STAT1 GENE; SYSTEMIC MYCOSIS; TRANSCRIPTION FACTOR GATA 2 DEFICIENCY; VITILIGO; WHIM SYNDROME; CANDIDIASIS, CUTANEOUS; COMORBIDITY; FEMALE; FOLLOW UP; IMMUNOLOGIC DEFICIENCY SYNDROMES; INCIDENCE; MALE; MOLECULARLY TARGETED THERAPY; PATHOLOGY; PROCEDURES; SEVERITY OF ILLNESS INDEX;

CANDIDIASIS, CUTANEOUS; COMORBIDITY; ECZEMA; EDUCATION, MEDICAL, CONTINUING; FEMALE; FOLLOW-UP STUDIES; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; INCIDENCE; MALE; MOLECULAR TARGETED THERAPY; SEVERITY OF ILLNESS INDEX;

EID: 84939430185     PISSN: 01909622     EISSN: 10976787     Source Type: Journal    
DOI: 10.1016/j.jaad.2015.01.055     Document Type: Review

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