Tolerance and autoimmunity in primary immunodeficiency disease: A comprehensive review

Clinical Reviews in Allergy and Immunology

Volumn 45, Issue 2, 2013, Pages 162-169

  Gupta, Sudhir ^a   Louis, Ankmalika Gupta ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

AIRE; ALPS; APECED; CVID; IgA deficiency; IPEX; STAT5b; Treg; WAS

Indexed keywords

AUTOIMMUNE REGULATOR PROTEIN; INTERFERON CONSENSUS SEQUENCE BINDING PROTEIN; INTERLEUKIN 2 RECEPTOR ALPHA; STAT5B PROTEIN; STROMAL INTERACTION MOLECULE 1; TRANSCRIPTION FACTOR FOXP3; TRANSCRIPTION FACTOR GATA 2;

APOPTOSIS; AUTOIMMUNE DISEASE; AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME; AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY; AUTOIMMUNITY; B LYMPHOCYTE; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CELLULAR IMMUNODEFICIENCY; CENTRAL IMMUNOLOGICAL TOLERANCE; CHRONIC GRANULOMATOUS DISEASE; COMMON VARIABLE IMMUNODEFICIENCY; COMPLEMENT DEFICIENCY; DENDRITIC CELL; DENDRITIC CELL DEFICIENCY; EPITHELIUM CELL; GENE MUTATION; HUMAN; HYPER IGE SYNDROME; HYPER IGM SYNDROME; IMMUNE DEFICIENCY; IMMUNOGLOBULIN A DEFICIENCY; IMMUNOLOGICAL TOLERANCE; INTERLEUKIN 2 RECEPTOR ALPHA DEFICIENCY; IPEX SYNDROME; LYMPHOCYTE DIFFERENTIATION; NATURAL KILLER CELL; NONHUMAN; OMENN SYNDROME; PERIPHERAL IMMUNOLOGICAL TOLERANCE; PROTEIN DEFICIENCY; REGULATORY T LYMPHOCYTE; REVIEW; STAT5B PROTEIN DEFICIENCY; T LYMPHOCYTE; TRANSCRIPTION REGULATION; WISKOTT ALDRICH SYNDROME;

ANIMALS; AUTOIMMUNITY; B-LYMPHOCYTES; CENTRAL TOLERANCE; HUMANS; IMMUNOLOGIC DEFICIENCY SYNDROMES; LYMPHOCYTE SUBSETS; PERIPHERAL TOLERANCE; T-LYMPHOCYTES, REGULATORY; THYMUS GLAND;

EID: 84884908862     PISSN: 10800549     EISSN: 15590267     Source Type: Journal    
DOI: 10.1007/s12016-012-8345-8     Document Type: Review

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