Maternal T-cell engraftment associated with severe hemophagocytosis of the bone marrow in untreated X-linked severe combined immunodeficiency

Journal of Pediatric Hematology/Oncology

Volumn 30, Issue 5, 2008, Pages 396-400

  Dvorak, Christopher C ^a,c   Sandford, Amanda ^a   Fong, Abraham ^a   Cowan, Morton J ^b   George, Tracy I ^a   Lewis, David B ^a  

^a STANFORD UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c Division of Pediatric Blood and Marrow Transplantation   (United States)

Author keywords

Graft versus host disease; Hemophagocytosis; Immunity maternally acquired; Severe combined immunodeficiency

Indexed keywords

CYCLOSPORIN; FLUDARABINE; HEMOGLOBIN GAMMA CHAIN; OKT 3; PERFORIN;

ANEMIA; ARTICLE; B CELL LYMPHOMA; B LYMPHOCYTE; BONE MARROW BIOPSY; CASE REPORT; CD8+ T LYMPHOCYTE; DNA SEQUENCE; ERYTHROPHAGOCYTOSIS; GENE LOCUS; GENE MUTATION; GRAFT VERSUS HOST REACTION; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HEMOPHAGOCYTIC SYNDROME; HUMAN; INFANT; LEUKAPHERESIS; MALE; NATURAL KILLER CELL; NEUTROPENIA; PERINATAL PERIOD; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; T LYMPHOCYTE; THROMBOCYTOPENIA; X LINKED SEVERE COMBINED IMMUNODEFICIENCY;

BONE MARROW; HUMANS; IMMUNOGLOBULIN GAMMA-CHAINS; INFANT; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; LYMPHOMA, B-CELL; MALE; SEVERE COMBINED IMMUNODEFICIENCY; T-LYMPHOCYTES; TREATMENT OUTCOME; X-LINKED COMBINED IMMUNODEFICIENCY DISEASES;

EID: 43149121774     PISSN: 10774114     EISSN: 15363678     Source Type: Journal    
DOI: 10.1097/MPH.0b013e318168e7a0     Document Type: Article

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