Hemophagocytic lymphohistiocytosis: Updates and evolving concepts

Current Opinion in Pediatrics

Volumn 24, Issue 1, 2012, Pages 9-15

  Risma, Kimberly ^a   Jordan, Michael B ^a  

^a UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

hemophagocytic lymphohistiocytosis; hemophagocytosis; hypomorphic mutations; perforin dependent cytotoxic function

Indexed keywords

CLINICAL FEATURE; GENE MUTATION; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; INFLAMMATORY DISEASE; INNATE IMMUNITY; MACROPHAGE ACTIVATION; PRIORITY JOURNAL; REVIEW; T LYMPHOCYTE ACTIVATION;

CHILD; CHILD, PRESCHOOL; CYTOTOXICITY, IMMUNOLOGIC; FEMALE; HUMANS; INFANT; INFANT, NEWBORN; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MACROPHAGES; MALE; PERFORIN; PROGNOSIS;

EID: 84856108251     PISSN: 10408703     EISSN: 1531698X     Source Type: Journal    
DOI: 10.1097/MOP.0b013e32834ec9c1     Document Type: Review

References (34)

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