Leiomodin-3-deficient mice display nemaline myopathy with fast-myofiber atrophy

DMM Disease Models and Mechanisms

Volumn 8, Issue 6, 2015, Pages 635-641

  Tian, Lei ^a,b   Ding, Sheng ^a,b   You, Yun ^b   Li, Tong Ruei ^a,b   Liu, Yan ^a,b   Wu, Xiaohui ^a   Sun, Ling ^a   Xu, Tian ^a,b  

^a FUDAN UNIVERSITY   (China)

^b YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Fast myofiber atrophy; Leiomodin 3; Mouse; Nemaline myopathy

Indexed keywords

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CACHEXIA; CONTROLLED STUDY; DISEASE SEVERITY; ELECTRON MICROSCOPY; FAST FIBER ATROPHY; GENE; GROWTH RETARDATION; IMMUNOFLUORESCENCE; LEIOMODIN 3 GENE; MALE; MOUSE; MOUSE MUTANT; MUSCLE ATROPHY; MUSCLE WEAKNESS; NEMALINE MYOPATHY; NONHUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; POSTNATAL GROWTH; PRIORITY JOURNAL; SARCOMERE; SARCOPENIA; SKELETAL MUSCLE; TRANSPOSON; ANIMAL; C57BL MOUSE; COMPLICATION; DEFICIENCY; FAST MUSCLE FIBER; METABOLISM; PATHOLOGY;

ANIMALIA; MUS;

ACTIN BINDING PROTEIN; LEIOMODIN-3 PROTEIN, MOUSE;

ANIMALS; MICE, INBRED C57BL; MICROFILAMENT PROTEINS; MUSCLE FIBERS, FAST-TWITCH; MUSCLE WEAKNESS; MUSCULAR ATROPHY; MYOPATHIES, NEMALINE; SARCOMERES;

EID: 84930592400     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.019430     Document Type: Article

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