-
2
-
-
0035722282
-
Thrombotic microangiopathy, hemolytic uremic syndrome, and thrombotic thrombocytopenic purpura
-
DOI 10.1046/j.1523-1755.2001.060003831.x
-
Ruggenenti P, Noris M, Remuzzi G: Thrombotic microangiopathy, hemolytic uremic syndrome, and thrombotic thrombocytopenic purpura. Kidney Int 2001;60:831-846. (Pubitemid 34205784)
-
(2001)
Kidney International
, vol.60
, Issue.3
, pp. 831-846
-
-
Ruggenenti, P.1
Noris, M.2
Remuzzi, G.3
-
3
-
-
0344624868
-
The pathogenesis and treatment of hemolytic uremic syndrome
-
Kaplan BS, Meyers KE, Schulman SL: The pathogenesis and treatment of hemolytic uremic syndrome. J Am Soc Nephrol 1998;9:1126-1133.
-
(1998)
J Am Soc Nephrol
, vol.9
, pp. 1126-1133
-
-
Kaplan, B.S.1
Meyers, K.E.2
Schulman, S.L.3
-
4
-
-
33746508999
-
A classification of hemolytic uremic syndrome and thrombotic thrombocytopenic purpura and related disorders
-
Besbas N, et al: A classification of hemolytic uremic syndrome and thrombotic thrombocytopenic purpura and related disorders. Kidney Int 2006;70:423-431.
-
(2006)
Kidney Int
, vol.70
, pp. 423-431
-
-
Besbas, N.1
-
5
-
-
0032569840
-
Antibodies to von Willebrand factor- cleaving protease in acute thrombotic thrombocytopenic purpura
-
Tsai HM, Lian EC: Antibodies to von Willebrand factor- cleaving protease in acute thrombotic thrombocytopenic purpura. N Engl J Med 1998;339:1585-1594.
-
(1998)
N. Engl. J. Med.
, vol.339
, pp. 1585-1594
-
-
Tsai, H.M.1
Lian, E.C.2
-
6
-
-
59449089457
-
Inherited thrombotic thrombocytopenic purpura
-
Galbusera M, Noris M, Remuzzi G: Inherited thrombotic thrombocytopenic purpura. Haematologica 2009;94:166-170.
-
(2009)
Haematologica
, vol.94
, pp. 166-170
-
-
Galbusera, M.1
Noris, M.2
Remuzzi, G.3
-
7
-
-
2342618145
-
Shiga toxin- producing escherichia coli infection
-
Thorpe CM: Shiga toxin- producing Escherichia coli infection. Clin Infect Dis 2004;38:1298-1303.
-
(2004)
Clin. Infect. Dis.
, vol.38
, pp. 1298-1303
-
-
Thorpe, C.M.1
-
8
-
-
0020657059
-
Sporadic cases of haemolytic- uraemic syndrome associated with faecal cytotoxin and cytotoxin- producing escherichia coli in stools
-
Karmali MA, et al: Sporadic cases of haemolytic- uraemic syndrome associated with faecal cytotoxin and cytotoxin- producing Escherichia coli in stools. Lancet 1983;1:619-20.
-
(1983)
Lancet
, vol.1
, pp. 619-620
-
-
Karmali, M.A.1
-
9
-
-
0020647208
-
Hemorrhagic colitis associated with a rare escherichia coli serotype
-
Riley L.W. et al.
-
Riley LW, et al: Hemorrhagic colitis associated with a rare Escherichia coli serotype. N Engl J Med 1983;308:681-685.
-
(1983)
N. Engl. J. Med.
, vol.308
, pp. 681-685
-
-
-
10
-
-
22544461682
-
Hemolytic uremic syndrome
-
Noris M, Remuzzi G: Hemolytic uremic syndrome. J Am Soc Nephrol 2005;16:1035-1050.
-
(2005)
J Am Soc Nephrol
, vol.16
, pp. 1035-1050
-
-
Noris, M.1
Remuzzi, G.2
-
11
-
-
2542420109
-
Nonenteropathic hemolytic uremic syndrome: causes and short- term course
-
Constantinescu AR, et al: Nonenteropathic hemolytic uremic syndrome: causes and short- term course. Am J Kidney Dis 2004;43:976-982.
-
(2004)
Am. J. Kidney Dis.
, vol.43
, pp. 976-982
-
-
Constantinescu, A.R.1
-
12
-
-
70350279315
-
Atypical hemolytic uremic syndrome
-
Noris M, Remuzzi G: Atypical hemolytic uremic syndrome. New Engl J Med 2009;361:1676-1687.
-
(2009)
New Engl. J. Med.
, vol.361
, pp. 1676-1687
-
-
Noris, M.1
Remuzzi, G.2
-
13
-
-
34548358982
-
Where next with atypical hemolytic uremic syndrome
-
Jokiranta TS, et al: Where next with atypical hemolytic uremic syndrome? Mol Immunol 2007;44:3889-3900.
-
(2007)
Mol. Immunol.
, vol.44
, pp. 3889-3900
-
-
Jokiranta, T.S.1
-
14
-
-
34548400755
-
Outcome of renal transplantation in patients with non- Shiga toxin- associated haemolytic uremic syndrome: Prognostic significance of genetic background
-
Bresin E, et al: Outcome of renal transplantation in patients with non- Shiga toxin- associated haemolytic uremic syndrome: prognostic significance of genetic background. Clin J Am Soc Nephrol 2006;1:88-99.
-
(2006)
Clin J Am Soc Nephrol
, vol.1
, pp. 88-99
-
-
Bresin, E.1
-
15
-
-
53749084348
-
Complement and the atypical hemolytic uremic syndrome in children
-
Loirat C, Noris M, Fremeaux- Bacchi V: Complement and the atypical hemolytic uremic syndrome in children. Pediatr Nephrol 2008;23:1957-1972.
-
(2008)
Pediatr. Nephrol.
, vol.23
, pp. 1957-1972
-
-
Loirat, C.1
Noris, M.2
Fremeaux- Bacchi, V.3
-
16
-
-
61549117207
-
Guideline for the investigation and initial therapy of diarrhea- negative hemolytic uremic syndrome
-
Ariceta B, et al: Guideline for the investigation and initial therapy of diarrhea- negative hemolytic uremic syndrome. Pediatr Nephrol 2009;24:687-696.
-
(2009)
Pediatr. Nephrol.
, vol.24
, pp. 687-696
-
-
Ariceta, B.1
-
17
-
-
0037968640
-
Adamts13 activity in thrombotic thrombocytopenic purpura- hemolytic uremic syndrome: Relation to presenting features and clinical outcomes in a prospective cohort of 142 patients
-
Vesely SK, et al: ADAMTS13 activity in thrombotic thrombocytopenic purpura- hemolytic uremic syndrome: relation to presenting features and clinical outcomes in a prospective cohort of 142 patients. Blood 2003;102:60-68.
-
(2003)
Blood
, vol.102
, pp. 60-68
-
-
Vesely, S.K.1
-
18
-
-
2542490269
-
Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity inhibitor level and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura
-
Zheng XL, et al: Effect of plasma exchange on plasma ADAMTS13 metalloprotease activity, inhibitor level, and clinical outcome in patients with idiopathic and nonidiopathic thrombotic thrombocytopenic purpura. Blood 2004;103:4043-4049.
-
(2004)
Blood
, vol.103
, pp. 4043-4049
-
-
Zheng, X.L.1
-
19
-
-
51549116628
-
Treatment and outcome of Shiga- toxin- associated hemolytic uremic syndrome hus
-
Scheiring J, Andreoli SP, Zimmerhackl LB: Treatment and outcome of Shiga- toxin- associated hemolytic uremic syndrome (HUS). Pediatr Nephrol 2008;23:1749-1760.
-
(2008)
Pediatr. Nephrol.
, vol.23
, pp. 1749-1760
-
-
Scheiring, J.1
Andreoli, S.P.2
Zimmerhackl, L.B.3
-
20
-
-
0034729744
-
The risk of the hemolytic- uremic syndrome after antibiotic treatment of escherichia col O157:H7 infections
-
Wong CS, et al: The risk of the hemolytic- uremic syndrome after antibiotic treatment of Escherichia coli O157:H7 infections. N Engl J Med 2000;342:1930-1936.
-
(2000)
N. Engl. J. Med.
, Issue.342
, pp. 1930-1936
-
-
Wong, C.S.1
-
21
-
-
15244348050
-
Shiga- toxin- producing escherichia coli and haemolytic uraemic syndrome
-
Tarr PI, Gordon CA, Chandler WL: Shiga- toxin- producing Escherichia coli and haemolytic uraemic syndrome. Lancet 2005;365:1073-1086.
-
(2005)
Lancet
, vol.365
, pp. 1073-1086
-
-
Tarr, P.I.1
Gordon, C.A.2
Chandler, W.L.3
-
22
-
-
33747159590
-
Genetics of hus: The impact of MCP CFH and if mutations on clinical presentation response to treatment and outcome
-
Caprioli J, et al: Genetics of HUS: the impact of MCP, CFH, and IF mutations on clinical presentation, response to treatment, and outcome. Blood 2006;108:1267-1279.
-
(2006)
Blood
, vol.108
, pp. 1267-1279
-
-
Caprioli, J.1
-
23
-
-
0032569884
-
Von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome
-
DOI 10.1056/NEJM199811263392202
-
Furlan M, et al: von Willebrand factor- cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic- uremic syndrome. N Engl J Med 1998;339:1578-1584. (Pubitemid 28536132)
-
(1998)
New England Journal of Medicine
, vol.339
, Issue.22
, pp. 1578-1584
-
-
Furlan, M.1
Robles, R.2
Galbusera, M.3
Remuzzi, G.4
Kyrle, P.A.5
Brenner, B.6
Krause, M.7
Scharrer, I.8
Aumann, V.9
Mittler, U.10
Solenthaler, M.11
Lammle, B.12
-
24
-
-
12344296265
-
Interplay between adamts13 and von Willebrand factor in inherited and acquired thrombotic microangiopathies
-
Soejima K, Nakagaki T: Interplay between ADAMTS13 and von Willebrand factor in inherited and acquired thrombotic microangiopathies. Semin Hematol 2005;42:56-62.
-
(2005)
Semin. Hematol.
, vol.42
, pp. 56-62
-
-
Soejima, K.1
Nakagaki, T.2
-
25
-
-
0018098453
-
Congenital deficiency of a factor in normal plasma that reverses microangiopathic hemolysis and thrombocytopenia
-
Upshaw JD Jr: Congenital deficiency of a factor in normal plasma that reverses microangiopathic hemolysis and thrombocytopenia. N Engl J Med 1978;298:1350-1352.
-
(1978)
N. Engl. J. Med.
, vol.298
, pp. 1350-1352
-
-
Upshaw Jr., J.D.1
-
26
-
-
0037158606
-
Thrombotic microangiopathies
-
Moake JL: Thrombotic microangiopathies. N Engl J Med 2002;347:589-600.
-
(2002)
N. Engl. J. Med.
, vol.347
, pp. 589-600
-
-
Moake, J.L.1
-
27
-
-
0037015057
-
Mutations and common polymorphisms in adamts13 gene responsible for von Willebrand factor- cleaving protease activity
-
USA
-
Kokame K, et al: Mutations and common polymorphisms in ADAMTS13 gene responsible for von Willebrand factor- cleaving protease activity. Proc Natl Acad Sci USA 2002;99:11902-11907.
-
(2002)
Proc. Natl. Acad. Sci.
, vol.99
, pp. 11902-11907
-
-
Kokame, K.1
-
28
-
-
10744226155
-
Molecular characterization of adamts13 gene mutations in Japanese patients with Upshaw- Schulman syndrome
-
Matsumoto M, et al: Molecular characterization of ADAMTS13 gene mutations in Japanese patients with Upshaw- Schulman syndrome. Blood 2004;103:1305-1310.
-
(2004)
Blood
, vol.103
, pp. 1305-1310
-
-
Matsumoto, M.1
-
29
-
-
4644271599
-
Identification of novel mutations in adamts13 in an adult patient with congenital thrombotic thrombocytopenic purpura
-
Uchida T, et al: Identification of novel mutations in ADAMTS13 in an adult patient with congenital thrombotic thrombocytopenic purpura. Blood 2004;104:2081-2083.
-
(2004)
Blood
, vol.104
, pp. 2081-2083
-
-
Uchida, T.1
-
30
-
-
33749872079
-
In- vitro and invivo consequences of mutations in the von Willebrand factor cleaving protease adamts13 in thrombotic thrombocytopenic purpura
-
Donadelli R, et al: In- vitro and invivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTS13 in thrombotic thrombocytopenic purpura. Thromb Haemost 2006;96:454-464.
-
(2006)
Thromb. Haemost.
, vol.96
, pp. 454-464
-
-
Donadelli, R.1
-
31
-
-
74049164674
-
Genotypephenotype correlation in congenital adamts13 deficient patients
-
ASH Annual Meeting Abstracts
-
Lotta LA GI, Cairo A, Klaassen R, Metin A, Gurgey A, et al: Genotypephenotype correlation in congenital ADAMTS13 deficient patients. Blood 2008; ASH Annual Meeting Abstracts (112):273.
-
(2008)
Blood
, vol.112
, pp. 273
-
-
Lotta La, G.I.1
Cairo, A.2
Klaassen, R.3
Metin, A.4
Gurgey, A.5
-
32
-
-
33746742947
-
A common origin of the 4143insA adamts13 mutation
-
Schneppenheim R, et al: A common origin of the 4143insA ADAMTS13 mutation. Thromb Haemost 2006;96:3-6.
-
(2006)
Thromb. Haemost.
, vol.96
, pp. 3-6
-
-
Schneppenheim, R.1
-
33
-
-
55549087548
-
Nonsense- mediated mRNA decay in the adamts13 gene caused by a 29- nucleotide deletion
-
Garagiola I, et al: Nonsense- mediated mRNA decay in the ADAMTS13 gene caused by a 29- nucleotide deletion. Haematologica 2008;93:1678-1685.
-
(2008)
Haematologica
, vol.93
, pp. 1678-1685
-
-
Garagiola, I.1
-
34
-
-
0036893186
-
Adamts- 13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions
-
Dong JF, et al: ADAMTS- 13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions. Blood 2002;100:4033-4039.
-
(2002)
Blood
, vol.100
, pp. 4033-4039
-
-
Dong, J.F.1
-
35
-
-
26444551183
-
Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible adamts13- deficient mice
-
Motto DG, et al: Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13- deficient mice. J Clin Invest 2005;115:2752-2761.
-
(2005)
J. Clin. Invest.
, vol.115
, pp. 2752-2761
-
-
Motto, D.G.1
-
36
-
-
3142677941
-
Identification of strainspecific variants of mouse adamts13 gene encoding von willebrand factor- cleaving protease
-
Banno F, et al: Identification of strainspecific variants of mouse Adamts13 gene encoding von Willebrand factor- cleaving protease. J Biol Chem 2004;279:30896-30903.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 30896-30903
-
-
Banno, F.1
-
37
-
-
33645728657
-
Complete deficiency in adamts13 is prothrombotic but it alone is not sufficient to cause thrombotic thrombocytopenic purpura
-
Banno F, et al: Complete deficiency in ADAMTS13 is prothrombotic, but it alone is not sufficient to cause thrombotic thrombocytopenic purpura. Blood 2006;107:3161-3166.
-
(2006)
Blood
, vol.107
, pp. 3161-3166
-
-
Banno, F.1
-
38
-
-
70449710864
-
Adenoviral- mediated gene transfer restores plasma adamts13 antigen activity in adamts13 knockout mice
-
Trionfini P, Tomasoni S, Galbusera M, et al: Adenoviral- mediated gene transfer restores plasma ADAMTS13 antigen activity in ADAMTS13 knockout mice. Gene Ther 2009;16:1373-1379.
-
(2009)
Gene. Ther.
, vol.16
, pp. 1373-1379
-
-
Trionfini, P.1
Tomasoni, S.2
Galbusera, M.3
-
39
-
-
58149267411
-
Correction of adamts13 deficiency by in utero gene transfer of lentiviral vector encoding adamts13 genes
-
Niiya M, et al: Correction of ADAMTS13 deficiency by in utero gene transfer of lentiviral vector encoding ADAMTS13 genes. Mol Ther 2009;17:34-41.
-
(2009)
Mol Ther
, vol.17
, pp. 34-41
-
-
Niiya, M.1
-
40
-
-
64049108912
-
Correction of murine adamts13 deficiency by hematopoietic progenitor cell- mediated gene therapy
-
Laje P, et al: Correction of murine ADAMTS13 deficiency by hematopoietic progenitor cell- mediated gene therapy. Blood 2009;113:2172-2180.
-
(2009)
Blood
, vol.113
, pp. 2172-2180
-
-
Laje, P.1
-
41
-
-
0033534406
-
Mvwf a dominant modifier of murine von Willebrand factor results from altered lineagespecific expression of a glycosyltransferase
-
Mohlke KL, et al: Mvwf, a dominant modifier of murine von Willebrand factor, results from altered lineagespecific expression of a glycosyltransferase. Cell 1999;96:111-120.
-
(1999)
Cell
, vol.96
, pp. 111-120
-
-
Mohlke, K.L.1
-
42
-
-
43549084421
-
The combined roles of adamts13 and vwf in murine models of TTP endotoxemia and thrombosis
-
Chauhan AK, et al: The combined roles of ADAMTS13 and VWF in murine models of TTP, endotoxemia, and thrombosis. Blood 2008;111:3452-3457.
-
(2008)
Blood
, vol.111
, pp. 3452-3457
-
-
Chauhan, A.K.1
-
43
-
-
0020000118
-
Pathologic effects of plasma from patients with thrombotic thrombocytopenic purpura on platelets and cultured vascular endothelial cells
-
Burns ER, Zucker- Franklin D: Pathologic effects of plasma from patients with thrombotic thrombocytopenic purpura on platelets and cultured vascular endothelial cells. Blood 1982;60:1030-1037.
-
(1982)
Blood
, vol.60
, pp. 1030-1037
-
-
Burns, E.R.1
Zucker-Franklin, D.2
-
44
-
-
33645090687
-
Systemic antithrombotic effects of adamts13
-
Chauhan AK, et al: Systemic antithrombotic effects of ADAMTS13. J Exp Med 2006;203:767-776.
-
(2006)
J. Exp. Med.
, vol.203
, pp. 767-776
-
-
Chauhan, A.K.1
-
45
-
-
0035312984
-
The united states national prospective hemolytic uremic syndrome study: Microbiologic serologic clinical and epidemiologic findings
-
Banatvala N, et al: The United States National Prospective Hemolytic Uremic Syndrome Study: microbiologic, serologic, clinical and epidemiologic findings. J Infect Dis 2001;183:1063-1070.
-
(2001)
J. Infect. Dis.
, vol.183
, pp. 1063-1070
-
-
Banatvala, N.1
-
46
-
-
0032505655
-
Escherichia coli O157:H7
-
Mead PS, Griffin PM: Escherichia coli O157:H7. Lancet 1998;352:1207-1212.
-
(1998)
Lancet
, Issue.352
, pp. 1207-1212
-
-
Mead, P.S.1
Griffin, P.M.2
-
47
-
-
28244445165
-
The hemolytic uremic syndromes in the united kingdom
-
in Kaplan BS, Trompeter RS, Moake JL (eds) Marcel Dekker Inc. New York
-
Milford D: The hemolytic uremic syndromes in the United Kingdom; in Kaplan BS, Trompeter RS, Moake JL (eds): Hemolytic Uremic Syndrome and Thrombotic Thrombocytopenic Purpura. New York, Marcel Dekker Inc., 1992, pp 39- 59.
-
(1992)
Hemolytic Uremic Syndrome and Thrombotic Thrombocytopenic Purpura
, pp. 39-59
-
-
Milford, D.1
-
48
-
-
0041411081
-
Long- term renal prognosis of diarrhea- associated hemolytic uremic syndrome: A systematic review meta- analysis, and metaregression
-
Garg AX, et al: Long- term renal prognosis of diarrhea- associated hemolytic uremic syndrome: a systematic review, meta- analysis, and metaregression. JAMA 2003;290:1360-1370.
-
(2003)
JAMA
, vol.290
, pp. 1360-1370
-
-
Garg, A.X.1
-
49
-
-
0027235835
-
Role of the eaeA gene in experimental enteropathogenic escherichia coli infection
-
Donnenberg MS, et al: Role of the eaeA gene in experimental enteropathogenicEscherichia coli infection. J Clin Invest 1993;92: 1412-1417.
-
(1993)
J. Clin. Invest.
, vol.92
, pp. 1412-1417
-
-
Donnenberg, M.S.1
-
50
-
-
0034819738
-
Shiga toxin translocation across intestinal epithelial cells is enhanced by neutrophil transmigration
-
Hurley BP, Thorpe CM, Acheson DW: Shiga toxin translocation across intestinal epithelial cells is enhanced by neutrophil transmigration. Infect Immun 2001;69:6148-6155.
-
(2001)
Infect. Immun.
, vol.69
, pp. 6148-6155
-
-
Hurley, B.P.1
Thorpe, C.M.2
Acheson, D.W.3
-
51
-
-
0035900715
-
Kinetic analysis of binding between shiga toxin and receptor glycolipid gb3cer by surface plasmon resonance
-
Nakajima H, et al: Kinetic analysis of binding between Shiga toxin and receptor glycolipid Gb3Cer by surface plasmon resonance. J Biol Chem 2001;276:42915-42922.
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 42915-42922
-
-
Nakajima, H.1
-
52
-
-
0023268257
-
The mode of action of Shiga toxin on peptide elongation of eukaryotic protein synthesis
-
Obrig TG, Moran TP, Brown JE: The mode of action of Shiga toxin on peptide elongation of eukaryotic protein synthesis. Biochem J 1987;244:287-294.
-
(1987)
Biochem. J.
, vol.244
, pp. 287-294
-
-
Obrig, T.G.1
Moran, T.P.2
Brown, J.E.3
-
53
-
-
0035885951
-
Verotoxin- 1- induced up- regulation of adhesive molecules renders microvascular endothelial cells thrombogenic at high shear stress
-
Morigi M, et al: Verotoxin- 1- induced up- regulation of adhesive molecules renders microvascular endothelial cells thrombogenic at high shear stress. Blood 2001;98:1828-1835.
-
(2001)
Blood
, vol.98
, pp. 1828-1835
-
-
Morigi, M.1
-
54
-
-
28244446734
-
Endothelial cells: They only look all alike
-
Ruggeri Z: Endothelial cells: they only look all alike. Blood 2001;98:1644.
-
(2001)
Blood
, vol.98
, pp. 1644
-
-
Ruggeri, Z.1
-
55
-
-
0026660303
-
Experimental verocytotoxemia in rabbits
-
Richardson SE, et al: Experimental verocytotoxemia in rabbits. Infect Immun 1992;60:4154-4167.
-
(1992)
Infect. Immun.
, vol.60
, pp. 4154-4167
-
-
Richardson, S.E.1
-
56
-
-
0002509959
-
Quantitation and localization of shiga toxin/shiga-like toxin-binding glycolipid receptors in human and babbon tissues
-
Elsevier Science BV edited by Karmali MA, Goglio AG, Bergamo, Italy
-
Tesh VL, Samuel JE, Burris JA, Owens JW, Taylor FBJ, Siegler RL: Quantitation and localization of shiga toxin/shiga-like toxin-binding glycolipid receptors in human and babbon tissues. in: Recent Advances in Verocytotoxin-Producing Escherichia Coli Infections, edited by Karmali MA, Goglio AG, Bergamo, Italy, Elsevier Science BV, 1994, pp 189-192.
-
(1994)
Recent Advances in Verocytotoxin-Producing Escherichia Coli Infections
, pp. 189-192
-
-
Tesh, V.L.1
Samuel, J.E.2
Burris, J.A.3
Owens, J.W.4
Taylor, F.B.J.5
Siegler, R.L.6
-
57
-
-
0032947477
-
A laboratory model of toxin- induced hemolytic uremic syndrome
-
Taylor CM, et al: A laboratory model of toxin- induced hemolytic uremic syndrome. Kidney Int 1999;55:1367-1374.
-
(1999)
Kidney Int
, vol.55
, pp. 1367-1374
-
-
Taylor, C.M.1
-
58
-
-
0034926743
-
Response to single and divided doses of shiga toxin- 1 in a primate model of hemolytic uremic syndrome
-
Siegler RL, et al: Response to single and divided doses of Shiga toxin- 1 in a primate model of hemolytic uremic syndrome. J Am Soc Nephrol 2001;12:1458-1467.
-
(2001)
J Am Soc Nephrol
, vol.12
, pp. 1458-1467
-
-
Siegler, R.L.1
-
59
-
-
0035743193
-
Response to Shiga toxin- 1 with and without lipopolysaccharide in a primate model ofhemolytic uremic syndrome
-
Siegler RL, et al: Response to Shiga toxin- 1, with and without lipopolysaccharide, in a primate model ofhemolytic uremic syndrome. Am J Nephrol 2001;21:420-425.
-
(2001)
Am. J. Nephrol.
, vol.21
, pp. 420-425
-
-
Siegler, R.L.1
-
60
-
-
0042328609
-
Response to Shiga toxin 1 and 2 in a baboon model of hemolytic uremic syndrome
-
Siegler RL, et al: Response to Shiga toxin 1 and 2 in a baboon model of hemolytic uremic syndrome. Pediatr Nephrol 2003;18:92-96.
-
(2003)
Pediatr. Nephrol.
, vol.18
, pp. 92-96
-
-
Siegler, R.L.1
-
61
-
-
0027178560
-
Comparison of the relative toxicities of shiga- like toxins type I and type II for mice
-
Tesh VL, et al: Comparison of the relative toxicities of Shiga- like toxins type I and type II for mice. Infect Immun 1993;61:3392-3402.
-
(1993)
Infect. Immun.
, vol.61
, pp. 3392-3402
-
-
Tesh, V.L.1
-
62
-
-
0026704042
-
Shiga toxin: Biochemistry genetics mode of action and role in pathogenesis
-
OBrien AD, et al: Shiga toxin: biochemistry, genetics, mode of action, and role in pathogenesis. Curr Top Microbiol Immunol 1992;180:65-94.
-
(1992)
Curr. Top. Microbiol. Immunol.
, vol.180
, pp. 65-94
-
-
O'Brien, A.D.1
-
63
-
-
0024114030
-
Idiopathic cutaneous and renal glomerular vasculopathy of greyhounds
-
Carpenter JL, et al: Idiopathic cutaneous and renal glomerular vasculopathy of greyhounds. Vet Pathol 1988;25:401-407.
-
(1988)
Vet. Pathol.
, vol.25
, pp. 401-407
-
-
Carpenter, J.L.1
-
64
-
-
0029366108
-
Glomerular ultrastructural lesions of idiopathic cutaneous and renal glomerular vasculopathy of greyhounds
-
Hertzke DM, et al: Glomerular ultrastructural lesions of idiopathic cutaneous and renal glomerular vasculopathy of greyhounds. Vet Pathol 1995;32:451-459.
-
(1995)
Vet. Pathol.
, vol.32
, pp. 451-459
-
-
Hertzke, D.M.1
-
65
-
-
0025676410
-
Acute renal tubular necrosis and death of mice orally infected with escherichia coli strains that produce Shiga- like toxin type II
-
Wadolkowski EA, et al: Acute renal tubular necrosis and death of mice orally infected with Escherichia coli strains that produce Shiga- like toxin type II. Infect Immun 1990;58:3959-3965.
-
(1990)
Infect. Immun.
, vol.58
, pp. 3959-3965
-
-
Wadolkowski, E.A.1
-
66
-
-
16944365096
-
The role of lipopolysaccharide and Shigalike toxin in a mouse model of escherichia coli O157:H7 infection
-
Karpman D, et al: The role of lipopolysaccharide and Shigalike toxin in a mouse model of Escherichia coli O157:H7 infection. J Infect Dis 1997;175:611-620.
-
(1997)
J. Infect. Dis.
, Issue.175
, pp. 611-620
-
-
Karpman, D.1
-
67
-
-
0025370411
-
Mouse model for colonization and disease caused by enterohemorrhagic escherichia coli O157:H7
-
Wadolkowski EA, Burris JA, and OBrien AD, Mouse model for colonization and disease caused by enterohemorrhagic Escherichia coli O157:H7. Infect Immun 1990;58:2438-2445.
-
(1990)
Infect. Immun.
, Issue.58
, pp. 2438-2445
-
-
Wadolkowski, E.A.1
Burris, J.A.2
O'Brien, A.D.3
-
68
-
-
0036419885
-
Differential tissue targeting and pathogenesis of verotoxins 1 and 2 in the mouse animal model
-
Rutjes NW, et al: Differential tissue targeting and pathogenesis of verotoxins 1 and 2 in the mouse animal model. Kidney Int 2002;62:832-845.
-
(2002)
Kidney Int
, vol.62
, pp. 832-845
-
-
Rutjes, N.W.1
-
69
-
-
0036025003
-
Tumour necrosis factor alpha is not an essential component of verotoxin 1- induced toxicity in mice
-
Wolski VM, Soltyk AM, Brunton JL: Tumour necrosis factor alpha is not an essential component of verotoxin 1- induced toxicity in mice. Microb Pathog 2002;32:263-271.
-
(2002)
Microb. Pathog.
, vol.32
, pp. 263-271
-
-
Wolski, V.M.1
Soltyk, A.M.2
Brunton, J.L.3
-
70
-
-
0036378186
-
Protective role of nitric oxide in mice with Shiga toxininduced hemolytic uremic syndrome
-
Dran GI, et al: Protective role of nitric oxide in mice with Shiga toxininduced hemolytic uremic syndrome. Kidney Int 2002;62:1338-1348.
-
(2002)
Kidney Int
, vol.62
, pp. 1338-1348
-
-
Dran, G.I.1
-
71
-
-
33845243385
-
A murine model of hus: Shiga toxin with lipopolysaccharide mimics the renal damage and physiologic response of human disease
-
Keepers TR, et al: A murine model of HUS: Shiga toxin with lipopolysaccharide mimics the renal damage and physiologic response of human disease. J Am Soc Nephrol 2006;17: 3404-3414.
-
(2006)
J Am Soc Nephrol
, vol.17
, pp. 3404-3414
-
-
Keepers, T.R.1
-
72
-
-
49049104863
-
Fractalkine and cx3cr1 mediate leukocyte capture by endothelium in response to shiga toxin
-
Zanchi C, et al: Fractalkine and CX3CR1 mediate leukocyte capture by endothelium in response to Shiga toxin. J Immunol 2008;181:1460-1469.
-
(2008)
J. Immunol.
, vol.181
, pp. 1460-1469
-
-
Zanchi, C.1
-
73
-
-
0025344791
-
Hemolytic- uremic syndrome during an outbreak of escherichia coli O157:H7 infections in institutions for mentally retarded persons: Clinical and epidemiologic observations
-
Pavia AT, et al: Hemolytic- uremic syndrome during an outbreak of Escherichia coli O157:H7 infections in institutions for mentally retarded persons: clinical and epidemiologic observations. J Pediatr 1990;116: 544-551.
-
(1990)
J. Pediatr.
, Issue.116
, pp. 544-551
-
-
Pavia, A.T.1
-
74
-
-
0034924996
-
Localization of shiga toxins of enterohaemorrhagic escherichia coli in kidneys of paediatric and geriatric patients with fatal haemolytic uraemic syndrome
-
Chaisri U, et al: Localization of Shiga toxins of enterohaemorrhagic Escherichia coli in kidneys of paediatric and geriatric patients with fatal haemolytic uraemic syndrome. Microb Pathog 2001;31:59-67.
-
(2001)
Microb. Pathog.
, vol.31
, pp. 59-67
-
-
Chaisri, U.1
-
75
-
-
62449248428
-
Shiga toxin 2 targets the murine renal collecting duct epithelium
-
Psotka MA, et al: Shiga toxin 2 targets the murine renal collecting duct epithelium. Infect Immun 2009;77:959-969.
-
(2009)
Infect. Immun.
, vol.77
, pp. 959-969
-
-
Psotka, M.A.1
-
76
-
-
58149314122
-
Shiga toxin- 2 results in renal tubular injury but not thrombotic microangiopathy in heterozygous factor H- deficient mice
-
Paixao- Cavalcante D, et al: Shiga toxin- 2 results in renal tubular injury but not thrombotic microangiopathy in heterozygous factor H- deficient mice. Clin Exp Immunol 2009;155:339-347.
-
(2009)
Clin. Exp. Immunol.
, vol.155
, pp. 339-347
-
-
Paixao-Cavalcante, D.1
-
77
-
-
0033030437
-
Depletion of liver and splenic macrophages reduces the lethality of Shiga toxin- 2 in a mouse model
-
Palermo MS, et al: Depletion of liver and splenic macrophages reduces the lethality of Shiga toxin- 2 in a mouse model. Clin Exp Immunol 1999;116:462-467.
-
(1999)
Clin. Exp. Immunol.
, vol.116
, pp. 462-467
-
-
Palermo, M.S.1
-
78
-
-
0033984719
-
Pretreatment of mice with lipopolysaccharide LPS or IL- 1beta exerts dose- dependent opposite effects on Shiga toxin- 2 lethality
-
Palermo M, et al: Pretreatment of mice with lipopolysaccharide (LPS) or IL- 1beta exerts dose- dependent opposite effects on Shiga toxin- 2 lethality. Clin Exp Immunol 2000; 119:77-83.
-
(2000)
Clin. Exp. Immunol.
, vol.119
, pp. 77-83
-
-
Palermo, M.1
-
79
-
-
2342452514
-
Hemolytic uremic syndrome induced by lipopolysaccharide and Shiga- like toxin
-
Ikeda M, Ito S, Honda M: Hemolytic uremic syndrome induced by lipopolysaccharide and Shiga- like toxin. Pediatr Nephrol 2004;19:485-489.
-
(2004)
Pediatr. Nephrol.
, vol.19
, pp. 485-489
-
-
Ikeda, M.1
Ito, S.2
Honda, M.3
-
80
-
-
33947539473
-
Cxcl1/KC and Cxcl2/MIP- 2 are critical effectors and potential targets for therapy of escherichia coli O157:H7- associated renal inflammation
-
Roche JK, et al: CXCL1/KC and CXCL2/MIP- 2 are critical effectors and potential targets for therapy of Escherichia coli O157:H7- associated renal inflammation. Am J Pathol 2007;170:526-537.
-
(2007)
Am. J. Pathol.
, Issue.170
, pp. 526-537
-
-
Roche, J.K.1
-
81
-
-
0027363238
-
A reporter transgene indicates renal- specific induction of tumor necrosis factor TNF by Shiga- like toxin. Possible involvement of TNF in hemolytic uremic syndrome
-
Harel Y, et al: A reporter transgene indicates renal- specific induction of tumor necrosis factor (TNF) by Shiga- like toxin. Possible involvement of TNF in hemolytic uremic syndrome. J Clin Invest 1993;92:2110-2116.
-
(1993)
J. Clin. Invest.
, vol.92
, pp. 2110-2116
-
-
Harel, Y.1
-
82
-
-
0032911088
-
Recruitment of renal tubular epithelial cells expressing verotoxin- 1 Stx1 receptors in HIV- 1 transgenic mice with renal disease
-
Liu XH, Lingwood CA, Ray PE: Recruitment of renal tubular epithelial cells expressing verotoxin- 1 (Stx1) receptors in HIV- 1 transgenic mice with renal disease. Kidney Int 1999;55:554-561.
-
(1999)
Kidney Int
, vol.55
, pp. 554-561
-
-
Liu, X.H.1
Lingwood, C.A.2
Ray, P.E.3
-
83
-
-
29144451448
-
Lipopolysaccharide upregulates renal Shiga toxin receptors in a primate model of hemolytic uremic syndrome
-
Clayton F, et al: Lipopolysaccharide upregulates renal Shiga toxin receptors in a primate model of hemolytic uremic syndrome. Am J Nephrol 2005;25:536-540.
-
(2005)
Am. J. Nephrol.
, vol.25
, pp. 536-540
-
-
Clayton, F.1
-
84
-
-
0030935633
-
Effects of TNF alpha on verocytotoxin cytotoxicity in purified human glomerular microvascular endothelial cells
-
van Setten PA, et al: Effects of TNF alpha on verocytotoxin cytotoxicity in purified human glomerular microvascular endothelial cells. Kidney Int 1997;51:1245-1256.
-
(1997)
Kidney Int
, vol.51
, pp. 1245-1256
-
-
Van Setten, P.A.1
-
85
-
-
0034098986
-
Effect of antibiotics, levofloxacin and fosfomycin on a mouse model with escherichia coli O157 infection
-
Isogai E, et al: Effect of antibiotics, levofloxacin and fosfomycin, on a mouse model with Escherichia coli O157 infection. Microbiol Immunol 2000;44:89-95.
-
(2000)
Microbiol. Immunol.
, vol.44
, pp. 89-95
-
-
Isogai, E.1
-
86
-
-
61849147904
-
Gnotobiotic piglet infection model for evaluating the safe use of antibiotics against escherichia coli O157:H7 infection
-
Zhang Q, et al: Gnotobiotic piglet infection model for evaluating the safe use of antibiotics against Escherichia coli O157:H7 infection. J Infect Dis 2009;199:486-493.
-
(2009)
J. Infect. Dis.
, Issue.199
, pp. 486-493
-
-
Zhang, Q.1
-
87
-
-
61849179644
-
Immunogenicity of a novel Stx2B- Stx1B fusion protein in a mice model of enterohemorrhagic escherichia coli fvn1 O157:H7 infection
-
Gao X, et al: Immunogenicity of a novel Stx2B- Stx1B fusion protein in a mice model of Enterohemorrhagic Escherichia coli O157:H7 infection. Vaccine 2009;27:2070-2076.
-
(2009)
Vaccine
, Issue.27
, pp. 2070-2076
-
-
Gao, X.1
-
88
-
-
68849089748
-
Enterohemorrhagic escherichia coli trivalent recombinant vaccine containing EspA intimin and Stx2 induces strong humoral immune response and confers protection in mice
-
Gu J, et al: Enterohemorrhagic Escherichia coli trivalent recombinant vaccine containing EspA, intimin and Stx2 induces strong humoral immune response and confers protection in mice. Microbes Infect 2009;11:835-841.
-
(2009)
Microbes. Infect.
, vol.11
, pp. 835-841
-
-
Gu, J.1
-
89
-
-
0032950690
-
Hypocomplementemia discloses genetic predisposition to hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: role of factor H abnormalities
-
Italian Registry of Familial and Recurrent Hemolytic Uremic Syndrome/Thrombotic Thrombocytopenic Purpura.
-
Noris M, et al: Hypocomplementemia discloses genetic predisposition to hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: role of factor H abnormalities. Italian Registry of Familial and Recurrent Hemolytic Uremic Syndrome/Thrombotic Thrombocytopenic Purpura. J Am Soc Nephrol 1999;10:281-293.
-
(1999)
J Am Soc Nephrol
, vol.10
, pp. 281-293
-
-
Noris, M.1
-
90
-
-
0031970553
-
Genetic studies into inherited and sporadic hemolytic uremic syndrome
-
Warwicker P, et al: Genetic studies into inherited and sporadic hemolytic uremic syndrome. Kidney Int 1998;53:836-844.
-
(1998)
Kidney Int
, vol.53
, pp. 836-844
-
-
Warwicker, P.1
-
91
-
-
0019387503
-
Hypo complementaemia due to a genetic deficiency of beta 1H globulin
-
Thompson RA, Winterborn MH: Hypo complementaemia due to a genetic deficiency of beta 1H globulin. Clin Exp Immunol 1981;46:110-119.
-
(1981)
Clin. Exp. Immunol.
, vol.46
, pp. 110-119
-
-
Thompson, R.A.1
Winterborn, M.H.2
-
92
-
-
0027948289
-
Familial hemolyticuremic syndrome and homozygous factor H deficiency
-
Pichette V, et al: Familial hemolyticuremic syndrome and homozygous factor H deficiency. Am J Kidney Dis 1994;24:936-941.
-
(1994)
Am. J. Kidney Dis.
, vol.24
, pp. 936-941
-
-
Pichette, V.1
-
93
-
-
0031724313
-
Human complement factor H deficiency associated with hemolytic uremic syndrome
-
Rougier N, et al: Human complement factor H deficiency associated with hemolytic uremic syndrome. J Am Soc Nephrol 1998;9:2318-2326.
-
(1998)
J Am Soc Nephrol
, vol.9
, pp. 2318-2326
-
-
Rougier, N.1
-
94
-
-
67651166873
-
Thrombomodulin mutations in atypical hemolytic uremic syndrome
-
Delvaeye M, et al: Thrombomodulin mutations in atypical hemolytic uremic syndrome. New Engl J Med 2009;361:345-357.
-
(2009)
New Engl. J. Med.
, vol.361
, pp. 345-357
-
-
Delvaeye, M.1
-
95
-
-
54049137505
-
Mutations in complement C3 predispose to development of atypical hemolytic uremic syndrome
-
Fremeaux- Bacchi V, et al: Mutations in complement C3 predispose to development of atypical hemolytic uremic syndrome. Blood 2008;112:4948-4952.
-
(2008)
Blood
, vol.112
, pp. 4948-4952
-
-
Fremeaux-Bacchi, V.1
-
96
-
-
20544437666
-
Anti-Factor H autoantibodies associated with atypical hemolytic uremic syndrome
-
Dragon- Durey MA, et al: Anti- Factor H autoantibodies associated with atypical hemolytic uremic syndrome. J Am Soc Nephrol 2005;16:555-563.
-
(2005)
J Am Soc Nephrol
, vol.16
, pp. 555-563
-
-
Dragon-Durey, M.A.1
-
97
-
-
43949161834
-
Complement factor H and related proteins: An expanding family of complementregulatory proteins
-
Zipfel PF, Skerka C: Complement factor H and related proteins: an expanding family of complementregulatory proteins? Immunol Today 1994;15:121-126.
-
(1994)
Immunol. Today
, vol.15
, pp. 121-126
-
-
Zipfel, P.F.1
Skerka, C.2
-
98
-
-
2442433542
-
The human complement factor H: Functional roles genetic variations and disease associations
-
Rodriguez de Cordoba S, et al: The human complement factor H: functional roles, genetic variations and disease associations. Mol Immunol 2004;41:355-367.
-
(2004)
Mol. Immunol.
, vol.41
, pp. 355-367
-
-
Rodriguez De Cordoba, S.1
-
99
-
-
0037396993
-
Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome
-
Manuelian T, et al: Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome. J Clin Invest 2003;111:1181-1190.
-
(2003)
J. Clin. Invest.
, vol.111
, pp. 1181-1190
-
-
Manuelian, T.1
-
100
-
-
2342582709
-
Functional analysis in serum from atypical hemolytic uremic syndrome patients reveals impaired protection of host cells associated with mutations in factor H
-
Sanchez- Corral P, et al: Functional analysis in serum from atypical hemolytic uremic syndrome patients reveals impaired protection of host cells associated with mutations in factor H. Mol Immunol 2004;41:81-84.
-
(2004)
Mol. Immunol.
, vol.41
, pp. 81-84
-
-
Sanchez-Corral, P.1
-
101
-
-
1642518600
-
Attachment of the soluble complement regulator factor H to cell and tissue surfaces: Relevance for pathology
-
Jozsi M, et al: Attachment of the soluble complement regulator factor H to cell and tissue surfaces: relevance for pathology. Histol Histopathol 2004;19:251-258.
-
(2004)
Histol. Histopathol.
, vol.19
, pp. 251-258
-
-
Jozsi, M.1
-
102
-
-
23944468114
-
Membranoproliferative glomerulonephritis type II dense deposit disease: An update
-
Appel GB, et al: Membranoproliferative glomerulonephritis type II (dense deposit disease): an update. J Am Soc Nephrol 2005; 16:1392-1403.
-
(2005)
J Am Soc Nephrol
, vol.16
, pp. 1392-1403
-
-
Appel, G.B.1
-
103
-
-
0034954060
-
Structure and composition of drusen associated with glomerulonephritis: Implications for the role of complement activation in drusen biogenesis
-
Lond
-
Mullins RF, Aptsiauri N, Hageman GS: Structure and composition of drusen associated with glomerulonephritis: implications for the role of complement activation in drusen biogenesis. Eye (Lond) 2001;15:390-395.
-
(2001)
Eye
, vol.15
, pp. 390-395
-
-
Mullins, R.F.1
Aptsiauri, N.2
Hageman, G.S.3
-
104
-
-
22544431912
-
Complement and diseases: Defective alternative pathway control results in kidney and eye diseases
-
Zipfel PF, et al: Complement and diseases: defective alternative pathway control results in kidney and eye diseases. Mol Immunol 2006;43:97-106.
-
(2006)
Mol. Immunol.
, vol.43
, pp. 97-106
-
-
Zipfel, P.F.1
-
105
-
-
41849110155
-
Genetic deficiency of complement factor H in a patient with age- related macular degeneration and membranoproliferative glomerulonephritis
-
Montes T, et al: Genetic deficiency of complement factor H in a patient with age- related macular degeneration and membranoproliferative glomerulonephritis. Mol Immunol 2008;45:2897-2904.
-
(2008)
Mol. Immunol.
, vol.45
, pp. 2897-2904
-
-
Montes, T.1
-
106
-
-
0030823285
-
Human factor H deficiency mutations in framework cysteine residues and block in H protein secretion and intracellular catabolism
-
Ault BH, et al: Human factor H deficiency. Mutations in framework cysteine residues and block in H protein secretion and intracellular catabolism. J Biol Chem 1997;272: 25168-25175.
-
(1997)
J. Biol. Chem.
, vol.272
, pp. 25168-25175
-
-
Ault, B.H.1
-
107
-
-
1542318912
-
Heterozygous and homozygous factor H deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: Report and genetic analysis of 16 cases
-
Dragon- Durey MA, et al: Heterozygous and homozygous factor H deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases. J Am Soc Nephrol, 2004;15:787-795.
-
(2004)
J Am Soc Nephrol
, vol.15
, pp. 787-795
-
-
Dragon-Durey, M.A.1
-
108
-
-
0027743352
-
Extensive complement activation in hereditary porcine membranoproliferative glomerulonephritis type II porcine dense deposit disease
-
Jansen JH, Hogasen K, Mollnes TE: Extensive complement activation in hereditary porcine membranoproliferative glomerulonephritis type II (porcine dense deposit disease). Am J Pathol 1993;143:1356-1365.
-
(1993)
Am. J. Pathol.
, vol.143
, pp. 1356-1365
-
-
Jansen, J.H.1
Hogasen, K.2
Mollnes, T.E.3
-
109
-
-
0031885010
-
In situ complement activation in porcine membranoproliferative glomerulonephritis type II
-
Jansen JH, et al: In situ complement activation in porcine membranoproliferative glomerulonephritis type II. Kidney Int 1998;53:331-349.
-
(1998)
Kidney Int
, Issue.53
, pp. 331-349
-
-
Jansen, J.H.1
-
110
-
-
0028952777
-
Hereditary porcine membranoproliferative glomerulonephritis type II is caused by factor H deficiency
-
Hogasen K, et al: Hereditary porcine membranoproliferative glomerulonephritis type II is caused by factor H deficiency. J Clin Invest 1995;95:1054-1061.
-
(1995)
J. Clin. Invest.
, vol.95
, pp. 1054-1061
-
-
Hogasen, K.1
-
111
-
-
0029633133
-
Porcine membranoproliferative glomerulonephritis type II: An autosomal recessive deficiency of factor H
-
Jansen JH, Hogasen K, Grondahl AM: Porcine membranoproliferative glomerulonephritis type II: an autosomal recessive deficiency of factor H. Vet Rec 1995;137:240-244.
-
(1995)
Vet. Rec.
, vol.137
, pp. 240-244
-
-
Jansen, J.H.1
Hogasen, K.2
Grondahl, A.M.3
-
112
-
-
0036900126
-
The molecular basis for hereditary porcine membranoproliferative glomerulonephritis type II: Point mutations in the factor H coding sequence block protein secretion
-
Hegasy GA, et al: The molecular basis for hereditary porcine membranoproliferative glomerulonephritis type II: point mutations in the factor H coding sequence block protein secretion. Am J Pathol 2002;161:2027-2034.
-
(2002)
Am. J. Pathol.
, vol.161
, pp. 2027-2034
-
-
Hegasy, G.A.1
-
113
-
-
1542601241
-
Eradication of porcine factor H deficiency in Norway
-
Hogasen K, Jansen JH, Harboe M: Eradication of porcine factor H deficiency in Norway. Vet Rec 1997;140:392-395.
-
(1997)
Vet. Rec.
, vol.140
, pp. 392-395
-
-
Hogasen, K.1
Jansen, J.H.2
Harboe, M.3
-
114
-
-
0036699540
-
Uncontrolled C3 activation causes membranoproliferative glomerulonephritis in mice deficient in complement factor H
-
Pickering MC, et al: Uncontrolled C3 activation causes membranoproliferative glomerulonephritis in mice deficient in complement factor H. Nat Genet 2002;31:424-428.
-
(2002)
Nat. Genet.
, vol.31
, pp. 424-428
-
-
Pickering, M.C.1
-
115
-
-
34250329129
-
Spontaneous hemolytic uremic syndrome triggered by complement factor H lacking surface recognition domains
-
Pickering MC, et al: Spontaneous hemolytic uremic syndrome triggered by complement factor H lacking surface recognition domains. J Exp Med 2007;204:1249-1256.
-
(2007)
J. Exp. Med.
, vol.204
, pp. 1249-1256
-
-
Pickering, M.C.1
-
116
-
-
79551491041
-
Insights into the role of complement dysregulation in atypical haemolytic uremic syndrome
-
Jorge E, Cook HT, Botto M, Pickering MC: Insights into the role of complement dysregulation in atypical haemolytic uremic syndrome. Mol Immunol 2009;46:2851.
-
(2009)
Mol. Immunol.
, vol.46
, pp. 2851
-
-
Jorge, E.1
Cook, H.T.2
Botto, M.3
Pickering, M.C.4
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