Molecular regulators of nerve conduction - Lessons from inherited neuropathies and rodent genetic models

Experimental Neurology

Volumn 267, Issue , 2015, Pages 209-218

  Li, Jun ^a,b  

^a VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b Tennessee Valley Healthcare System   (United States)

Author keywords

Action potential; Adherens junction; Axonal degeneration; Caspr; Charcot Marie Tooth disease; CMT1A; CMT2; CMTX1; Compound muscle action potential; Connexin 1; Demyelination; Hereditary neuropathy with liability to pressure palsies; HNPP; Inherited neuropathy; Ion channel; Juxtaparanode; Myelination; Nerve conduction study; Node of Ranvier; Paranode; PMP22; Polyneuropathy; Sensory nerve action potential; Septate like junction; Tight junction; Voltage gated potassium channel; Voltage gated sodium channel

Indexed keywords

LIPID; MYELIN; NEU DIFFERENTIATION FACTOR; NEUROFILAMENT PROTEIN; REGULATOR PROTEIN; MYELIN PROTEIN;

DISEASE COURSE; ELECTRIC CAPACITANCE; GENETIC DISORDER; GENETIC MODEL; HUMAN; MOLECULAR GENETICS; MYELINATED NERVE; NERVE CONDUCTION; NERVE FIBER; NERVE POTENTIAL; NERVOUS SYSTEM ELECTROPHYSIOLOGY; NERVOUS SYSTEM PARAMETERS; NEUROBIOLOGY; NONHUMAN; NONMYELINATED NERVE; PATHOPHYSIOLOGY; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; PROTEIN STRUCTURE; REGULATORY MECHANISM; REVIEW; RODENT; VELOCITY; ACTION POTENTIAL; ANIMAL; DISEASE MODEL; GENETICS; METABOLISM; PATHOLOGY;

ACTION POTENTIALS; ANIMALS; DISEASE MODELS, ANIMAL; MYELIN PROTEINS; NERVE FIBERS, MYELINATED; NEURAL CONDUCTION; PERIPHERAL NERVOUS SYSTEM DISEASES; RODENTIA;

EID: 84925776984     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2015.03.009     Document Type: Review

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