Abnormal junctions and permeability of myelin in PMP22-deficient nerves

Annals of Neurology

Volumn 75, Issue 2, 2014, Pages 255-265

  Guo, Jiasong ^b   Wang, Leiming ^a,b   Zhang, Yang ^b   Wu, Jiawen ^b   Arpag, Sezgi ^b   Hu, Bo ^b   Imhof, Beat A ^c   Tian, Xinxia ^a   Carter, Bruce D ^d   Suter, Ueli ^e   Li, Jun ^b,f,g  

^a PEKING UNIVERSITY HEALTH SCIENCE CENTER   (China)

^b VANDERBILT UNIVERSITY MEDICAL CENTER   (United States)

^c UNIVERSITY OF GENEVA   (Switzerland)

^d VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

^e ETH ZURICH   (Switzerland)

^f Tennessee Valley Healthcare System Nashville VA   (United States)

^g SOUTHERN MEDICAL UNIVERSITY   (China)

Author keywords

[No Author keywords available]

Indexed keywords

IMMUNOGLOBULIN; JUNCTIONAL ADHESION MOLECULE C; MYELIN ASSOCIATED GLYCOPROTEIN; PERIPHERAL MYELIN PROTEIN 22; TIGHT JUNCTION PROTEIN;

ACTION POTENTIAL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL JUNCTION; ELECTROPHYSIOLOGY; MEMBRANE PERMEABILITY; MEMBRANE POTENTIAL; MOLECULAR MECHANICS; MOUSE; NERVE CONDUCTION; NEUROPATHY; NONHUMAN; PERIPHERAL NERVE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN INTERACTION; TIGHT JUNCTION;

ACTION POTENTIALS; AGE FACTORS; ANIMALS; ARTHROGRYPOSIS; AXONS; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION; HEK293 CELLS; HEREDITARY SENSORY AND MOTOR NEUROPATHY; HUMANS; JUNCTIONAL ADHESION MOLECULES; MICE; MICE, TRANSGENIC; MUTATION; MYELIN PROTEINS; MYELIN SHEATH; NEURAL CONDUCTION; PERIPHERAL NERVES; POTASSIUM; TIGHT JUNCTION PROTEINS; TIGHT JUNCTIONS;

EID: 84896547826     PISSN: 03645134     EISSN: 15318249     Source Type: Journal    
DOI: 10.1002/ana.24086     Document Type: Article

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