In vitro studies in VCP-associated multisystem proteinopathy suggest altered mitochondrial bioenergetics

Mitochondrion

Volumn 22, Issue , 2015, Pages 1-8

  Nalbandian, Angèle ^a   Llewellyn, Katrina J ^a   Gomez, Arianna ^a   Walker, Naomi ^a   Su, Hailing ^a   Dunnigan, Andrew ^a   Chwa, Marilyn ^a   Vesa, Jouni ^a   Kenney, M C ^a   Kimonis, Virginia E ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

ALS; Frontotemporal dementia; Inclusion body myopathy; Mitochondrial bioenergetics; Paget's disease of the bone; Valosin containing protein

Indexed keywords

ADENOSINE TRIPHOSPHATE; CELL PROTEIN; LIGHT CHAIN 3 I; LIGHT CHAIN 3 II; MITOCHONDRIAL ENZYME; MITOCHONDRIAL ENZYME II; MITOCHONDRIAL ENZYME III; MITOCHONDRIAL ENZYME IV; PROTEIN P62; TAR DNA BINDING PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG; VALOSIN CONTAINING PROTEIN; ADENOSINE TRIPHOSPHATASE; CDC48 PROTEIN; CELL CYCLE PROTEIN; MULTIENZYME COMPLEX;

ANIMAL CELL; ARTICLE; BIOENERGY; BIOLOGICAL MODEL; CELL ENERGY; CELLULAR PARAMETERS; CLINICAL FEATURE; COMPARATIVE STUDY; CONTROLLED STUDY; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; EXTRACELLULAR ACIDIFICATION RATE; FIBROBLAST; FIRST DEGREE RELATIVE; GLYCOLYSIS; HUMAN; HUMAN CELL; IMMUNOCYTOCHEMISTRY; IN VITRO STUDY; MITOCHONDRIAL DYNAMICS; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; MOUSE; MYOBLAST; NONHUMAN; OXIDATIVE PHOSPHORYLATION; OXYGEN CONSUMPTION; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; UPREGULATION; VALOSIN CONTAINING PROTEIN ASSOCIATED MULTISYSTEM PROTEINOPATHY; ANIMAL; DEGENERATIVE DISEASE; DISEASE MODEL; ENERGY METABOLISM; ENZYMOLOGY; METABOLISM; MITOCHONDRION; PATHOLOGY; PHYSIOLOGY; PROTEOSTASIS DEFICIENCY;

ADENOSINE TRIPHOSPHATASES; ADENOSINE TRIPHOSPHATE; ANIMALS; CELL CYCLE PROTEINS; DISEASE MODELS, ANIMAL; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; ENERGY METABOLISM; FIBROBLASTS; HUMANS; MEMBRANE POTENTIAL, MITOCHONDRIAL; MICE; MITOCHONDRIA; MYOBLASTS; NEURODEGENERATIVE DISEASES; PROTEOSTASIS DEFICIENCIES;

EID: 84924270124     PISSN: 15677249     EISSN: 18728278     Source Type: Journal    
DOI: 10.1016/j.mito.2015.02.004     Document Type: Article

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