Slow development of ALS-like spinal cord pathology in mutant valosin-containing protein gene knock-in mice

Cell Death and Disease

Volumn 3, Issue 8, 2012, Pages

  Yin, H Z ^a   Nalbandian, A ^a   Hsu, C I ^a   Li, S ^a   Llewellyn, K J ^a   Mozaffar, T ^a   Kimonis, V E ^a   Weiss, J H ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Amyotrophic lateral sclerosis; Animal models; Motor neuron; SOD1; TDP 43

Indexed keywords

TAR DNA BINDING PROTEIN; VALOSIN CONTAINING PROTEIN; DNA BINDING PROTEIN; PEPTIDE; PROTEIN TDP-43; UBIQUITIN; VALOSIN;

AGE; AGED; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; CELL AGGREGATION; CONTROLLED STUDY; CYTOSOL; DENERVATION; DISEASE COURSE; ELECTROMYOGRAPHY; FEMALE; HISTOPATHOLOGY; MALE; MITOCHONDRION; MOTONEURON; MOUSE; NONHUMAN; PRIORITY JOURNAL; SPINAL CORD ATROPHY; SPINAL CORD DISEASE; SPINAL CORD VENTRAL HORN; WEAKNESS; ANIMAL; DISEASE MODEL; FRONTOTEMPORAL DEMENTIA; GENE TARGETING; GENETICS; HETEROZYGOTE; HUMAN; METABOLISM; MUTATION; PATHOLOGY; SPINAL CORD;

ANIMALIA; MUS;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; FRONTOTEMPORAL DEMENTIA; GENE KNOCK-IN TECHNIQUES; HETEROZYGOTE; HUMANS; MICE; MOTOR NEURONS; MUTATION; PEPTIDES; SPINAL CORD; UBIQUITIN;

EID: 84865752018     PISSN: None     EISSN: 20414889     Source Type: Journal    
DOI: 10.1038/cddis.2012.115     Document Type: Article

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