Modulation of the secretory pathway rescues zebrafish polycystic kidney disease pathology

Journal of the American Society of Nephrology

Volumn 25, Issue 8, 2014, Pages 1749-1759

  Le Corre, Stéphanie ^a   Eyre, David ^b   Drummond, Iain A ^a  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

^b UNIVERSITY OF WASHINGTON   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BREFELDIN A; COAT PROTEIN COMPLEX II; COLLAGEN TYPE 2; MATRIX METALLOPROTEINASE; MESSENGER RNA; POLYCYSTIN 2; CARRIER PROTEIN; POLYCYSTIC KIDNEY DISEASE 1 PROTEIN; POLYCYSTIC KIDNEY DISEASE 2 PROTEIN; POLYCYSTIN; PROTEIN SYNTHESIS INHIBITOR; VESICULAR TRANSPORT PROTEIN; ZEBRAFISH PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; COLLAGEN SYNTHESIS; CONTROLLED STUDY; EMBRYO; ENZYME ACTIVITY; GOLGI COMPLEX; KIDNEY CYST; KIDNEY POLYCYSTIC DISEASE; NONHUMAN; NOTOCHORD; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; RNA TRANSLATION; SECRETORY PATHWAY; UPREGULATION; ZEBRA FISH; ANIMAL; DRUG EFFECTS; METABOLISM; PATHOLOGY; PHYSIOLOGY; POLYCYSTIC KIDNEY DISEASES; TRANSGENIC ANIMAL;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BREFELDIN A; CARRIER PROTEINS; COLLAGEN TYPE II; NOTOCHORD; POLYCYSTIC KIDNEY DISEASES; PROTEIN SYNTHESIS INHIBITORS; SECRETORY PATHWAY; TRPP CATION CHANNELS; VESICULAR TRANSPORT PROTEINS; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 84921662373     PISSN: 10466673     EISSN: 15333450     Source Type: Journal    
DOI: 10.1681/ASN.2013101060     Document Type: Article

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