Modeling the natural history of Pelizaeus-Merzbacher disease

Neurobiology of Disease

Volumn 75, Issue , 2015, Pages 115-130

  Mayer, Joshua A ^a   Griffiths, Ian R ^b   Goldman, James E ^c   Smith, Chelsey M ^a   Cooksey, Elizabeth ^a   Radcliff, Abigail B ^a   Duncan, Ian D ^a  

^a UNIVERSITY OF WISCONSIN MADISON   (United States)

^b UNIVERSITY OF GLASGOW   (United Kingdom)

^c Department of Medicine   (United States)

Author keywords

Axon; Hypomyelination; Oligodendrocyte; PLP1; X linked

Indexed keywords

MYELIN; PROTEOLIPID PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL DENSITY; CELL DIVISION; CELL ULTRASTRUCTURE; CONTROLLED STUDY; DISEASE COURSE; GENE; HISTOPATHOLOGY; IN SITU HYBRIDIZATION; MYELINATION; NERVE CELL DIFFERENTIATION; NERVE CELL NECROSIS; NERVE FIBER; NONHUMAN; OLIGODENDROGLIA; PELIZAEUS MERZBACHER DISEASE; PLP1 GENE; ROUGH ENDOPLASMIC RETICULUM; ANIMAL; ASTROCYTE; BRAIN; CELL DEATH; DISEASE MODEL; DOG; FEMALE; GENETICS; MALE; METABOLISM; MUTATION; MYELIN SHEATH; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; SPINAL CORD;

ANIMALS; ASTROCYTES; AXONS; BRAIN; CELL DEATH; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; DOGS; FEMALE; MALE; MUTATION; MYELIN PROTEOLIPID PROTEIN; MYELIN SHEATH; OLIGODENDROGLIA; PELIZAEUS-MERZBACHER DISEASE; SPINAL CORD;

EID: 84921476801     PISSN: 09699961     EISSN: 1095953X     Source Type: Journal    
DOI: 10.1016/j.nbd.2014.12.023     Document Type: Article

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