Rabbit paralytic tremor phenotype - A plp1 gene mutation as a model of human Pelizaeus-Merzbacher disease

Acta Neurobiologiae Experimentalis

Volumn 65, Issue 2, 2005, Pages 221-229

  Sypecka, Joanna ^a   Domańska Janik, Krystyna ^a  

^a MOSSAKOWSKI MEDICAL RESEARCH CENTRE   (Poland)

Author keywords

Hypomyelination; Paralytic tremor rabbit; plp gene mutation; PMD

Indexed keywords

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; CELL MATURATION; CELL STRUCTURE; GENE; GENE MUTATION; HUMAN; MYELIN SHEATH; MYELINATION; NERVE CELL DIFFERENTIATION; NONHUMAN; OLIGODENDROGLIA; PARALYSIS; PELIZAEUS MERZBACHER DISEASE; PHENOTYPE; PLP1 GENE; POINT MUTATION; RABBIT; REVIEW; TREMOR;

ANIMALS; DEMYELINATING DISEASES; DISEASE MODELS, ANIMAL; HUMANS; MEMBRANE PROTEINS; MYELIN PROTEOLIPID PROTEIN; PARESIS; PELIZAEUS-MERZBACHER DISEASE; PHENOTYPE; POINT MUTATION; RABBITS; TREMOR;

EID: 21044455661     PISSN: 00651400     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Review

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