The role of proteases in excitation-contraction coupling failure in muscular dystrophy

American Journal of Physiology - Cell Physiology

Volumn 308, Issue 1, 2015, Pages C33-C40

  Mázala, Davi A G ^a   Grange, Robert W ^b   Chin, Eva R ^a  

^a UNIVERSITY OF MARYLAND   (United States)

^b VIRGINIA POLYTECHNIC INSTITUTE AND STATE UNIVERSITY   (United States)

Author keywords

Duchenne muscular dystrophy; Excitation contraction coupling; Intracellular Ca2+; Protease(s)

Indexed keywords

CALCIUM ION; CALPAIN; DYSTROPHIN; FURA 2; PROTEINASE; UTROPHIN; CALCIUM; PEPTIDE HYDROLASE; PROTEINASE INHIBITOR;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BODY MASS; CALCIUM CELL LEVEL; CONTROLLED STUDY; DISEASE SEVERITY; DUCHENNE MUSCULAR DYSTROPHY; ELECTROSTIMULATION; ENZYME ACTIVATION; EX VIVO STUDY; EXCITATION CONTRACTION COUPLING; EXTENSOR DIGITORUM LONGUS MUSCLE; FATIGUE; FEMALE; MALE; MOUSE; MUSCLE CELL; MUSCLE TETANIC CONTRACTION; MUSCLE WEAKNESS; NONHUMAN; PLANTARIS MUSCLE; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEINASE INHIBITION; ANIMAL; DEFICIENCY; DISEASE MODEL; DRUG EFFECTS; ENZYMOLOGY; GENETICS; KNOCKOUT MOUSE; METABOLISM; MUSCLE STRENGTH; MUSCULAR DYSTROPHY, DUCHENNE; PATHOPHYSIOLOGY; SKELETAL MUSCLE; SKELETAL MUSCLE CELL; TIME FACTOR; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ANIMALIA; MUS;

ANIMALS; CALCIUM; DISEASE MODELS, ANIMAL; ELECTRIC STIMULATION; EXCITATION CONTRACTION COUPLING; MICE, INBRED MDX; MICE, KNOCKOUT; MUSCLE FIBERS, SKELETAL; MUSCLE STRENGTH; MUSCLE WEAKNESS; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE; PEPTIDE HYDROLASES; PROTEASE INHIBITORS; TIME FACTORS; UTROPHIN;

EID: 84920915025     PISSN: 03636143     EISSN: 15221563     Source Type: Journal    
DOI: 10.1152/ajpcell.00267.2013     Document Type: Article

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