Fibulin-4 and fibulin-5 in elastogenesis and beyond: Insights from mouse and human studies

Matrix Biology

Volumn 37, Issue , 2014, Pages 142-149

  Papke, Christina L ^a   Yanagisawa, Hiromi ^a  

^a UNIVERSITY OF TEXAS SOUTHWESTERN MEDICAL CENTER   (United States)

Author keywords

Aortic aneurysm; Collagen fibers; Cutis laxa; ECM; Elastic fibers; Integrin

Indexed keywords

ANGIOTENSIN; ELASTIN; FIBULIN; FIBULIN 4; FIBULIN 5; MICRORNA 29B; PROTEINASE; TRANSFORMING GROWTH FACTOR BETA; TROPOELASTIN; UNCLASSIFIED DRUG; FBLN5 PROTEIN, HUMAN; FIBULIN-4; INTEGRIN; MICRORNA; MIRN29 MICRORNA, HUMAN; PEPTIDE HYDROLASE; SCLEROPROTEIN;

AORTA RUPTURE; ARTICLE; BIOLOGICAL FUNCTIONS; ELASTIC FIBER; ELASTOGENESIS; ENZYME REGULATION; EXTRACELLULAR MATRIX; HISTOGENESIS; HUMAN; LOSS OF FUNCTION MUTATION; NONHUMAN; PERINATAL PERIOD; PROTEIN ANALYSIS; PROTEIN BINDING; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; ANIMAL; AORTA; BIOSYNTHESIS; EMBRYOLOGY; GENE EXPRESSION REGULATION; GENETICS; IMMUNOLOGY; KNOCKOUT MOUSE; METABOLISM; MOUSE; PHYSIOLOGY; SIGNAL TRANSDUCTION; SMOOTH MUSCLE FIBER;

ANIMALS; AORTA; ELASTIN; EXTRACELLULAR MATRIX PROTEINS; GENE EXPRESSION REGULATION, ENZYMOLOGIC; HUMANS; INTEGRINS; MICE; MICE, KNOCKOUT; MICRORNAS; MYOCYTES, SMOOTH MUSCLE; PEPTIDE HYDROLASES; SIGNAL TRANSDUCTION;

EID: 84908290110     PISSN: 0945053X     EISSN: 15691802     Source Type: Journal    
DOI: 10.1016/j.matbio.2014.02.004     Document Type: Review

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