Pseudoachondroplasia/COMP - translating from the bench to the bedside

Matrix Biology

Volumn 37, Issue , 2014, Pages 167-173

  Posey, Karen LaShea ^a   Alcorn, Joseph L ^a   Hecht, Jacqueline T ^a,b  

^a UNIVERSITY OF TEXAS MEDICAL SCHOOL   (United States)

^b Shriners Hospital for Children   (United States)

Author keywords

Chondrocyte; Growth plate and COMP; Mouse model; PSACH; Pseudoachondroplasia; TSP 5

Indexed keywords

CARTILAGE OLIGOMERIC MATRIX PROTEIN; CASPASE 12; COLLAGEN TYPE 2; INITIATION FACTOR 2ALPHA; SIGNAL PEPTIDE; TETRACYCLINE;

ACHONDROPLASIA; ARTICLE; CARTILAGE CELL; ENDOPLASMIC RETICULUM STRESS; HUMAN; MOLECULAR PATHOLOGY; MOUSE MODEL; NONHUMAN; OXIDATIVE STRESS; PHENOTYPE; PROMOTER REGION; PSEUDOACHONDROPLASIA; TRANSGENIC MOUSE; UNFOLDED PROTEIN RESPONSE; ANIMAL; DISEASE MODEL; GENE DELETION; GENETICS; METABOLISM; MOUSE; PATHOLOGY; PHYSIOLOGY;

ACHONDROPLASIA; ANIMALS; CARTILAGE OLIGOMERIC MATRIX PROTEIN; CHONDROCYTES; DISEASE MODELS, ANIMAL; ENDOPLASMIC RETICULUM STRESS; HUMANS; MICE; MICE, TRANSGENIC; SEQUENCE DELETION;

EID: 84908270157     PISSN: 0945053X     EISSN: 15691802     Source Type: Journal    
DOI: 10.1016/j.matbio.2014.05.006     Document Type: Review

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