Pseudoachondroplasia is caused through both intra- and extracellular pathogenic pathways

Journal of Clinical Investigation

Volumn 110, Issue 4, 2002, Pages 505-513

  Dinser, Robert ^a,d   Zaucke, Frank ^a   Kreppe, Florian ^b   Hultenby, Kjell ^c   Kochanek, Stefan ^b   Paulsson, Mats ^a   Maurer, Patrik ^a  

^a UNIVERSITY OF COLOGNE   (Germany)

^b UNIVERSITY OF COLOGNE   (Germany)

^c KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^d SAARLAND UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CARTILAGE OLIGOMERIC MATRIX PROTEIN; CHAPERONE; COLLAGEN FIBER; MUTANT PROTEIN;

ACHONDROPLASIA; ANIMAL CELL; ARTICLE; CARTILAGE CELL; CATTLE; CELL CULTURE; CELL DEATH; CELL VIABILITY; CONTROLLED STUDY; DOSE RESPONSE; ENDOPLASMIC RETICULUM; EXTRACELLULAR MATRIX; GENE MUTATION; GENE OVEREXPRESSION; GROWTH PLATE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN SECRETION; PSEUDOACHONDROPLASIA; STORAGE DISEASE;

EID: 0036679151     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI0214386     Document Type: Article

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