A functional anatomic defect of the cystic fibrosis airway

American Journal of Respiratory and Critical Care Medicine

Volumn 190, Issue 4, 2014, Pages 421-432

  Birket, Susan E ^a   Chu, Kengyeh K ^b,c   Liu, Linbo ^b   Houser, Grace H ^d   Diephuis, Bradford J ^b,c,e   Wilsterman, Eric J ^b   Dierksen, Gregory ^b   Mazur, Marina ^f   Shastry, Suresh ^a,f   Li, Yao ^a,f   Watson, John D ^a   Smith, Alexander T ^a   Schuster, Benjamin S ^g   Hanes, Justin ^g,h   Grizzle, William E ⁱ   Sorscher, Eric J ^a,f,j   Tearney, Guillermo J ^b,c,e   Rowe, Steven M ^a,d,f,j  

^a University of Alabama at Birmingham   (United States)

^b MASSACHUSETTS GENERAL HOSPITAL   (United States)

^c HARVARD MEDICAL SCHOOL   (United States)

^d University of Alabama at Birmingham   (United States)

^e HARVARD MIT DIVISION OF HEALTH SCIENCES AND TECHNOLOGY   (United States)

^f UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^g JOHNS HOPKINS HOSPITAL   (United States)

^h Johns Hopkins University   (United States)

ⁱ University of Alabama at Birmingham   (United States)

^j UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

more..

Author keywords

Airway epithelium; Cystic fibrosis; Mucus transport; Optical coherence tomography; Viscosity

Indexed keywords

ACETAZOLAMIDE; BICARBONATE; BUMETANIDE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR;

ADULT; AIRWAY; ANATOMICAL VARIATION; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANION TRANSPORT; ARTICLE; BLEACHING; COMPARATIVE STUDY; CONTROLLED STUDY; CYSTIC FIBROSIS; EX VIVO STUDY; HISTOPATHOLOGY; HUMAN; HUMAN CELL; IMAGE ANALYSIS; IMAGE RECONSTRUCTION; IN VITRO STUDY; MUCOCILIARY TRANSPORT; NONHUMAN; OPTICAL COHERENCE TOMOGRAPHY; PRIORITY JOURNAL; QUANTITATIVE ANALYSIS; RESPIRATORY EPITHELIUM; SHEAR STRESS; TISSUE CULTURE; TRACHEA; VISCOSITY; ANIMAL; CELL CULTURE; DISEASE MODEL; EPITHELIUM; METHODOLOGY; MUCOCILIARY CLEARANCE; MUCUS TRANSPORT; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; SWINE;

AIRWAY EPITHELIUM; CYSTIC FIBROSIS; MUCUS TRANSPORT; OPTICAL COHERENCE TOMOGRAPHY; VISCOSITY;

ANIMALS; CELLS, CULTURED; CYSTIC FIBROSIS; DISEASE MODELS, ANIMAL; EPITHELIUM; HUMANS; MUCOCILIARY CLEARANCE; SWINE; TOMOGRAPHY, OPTICAL COHERENCE; TRACHEA;

EID: 84907833958     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.201404-0670OC     Document Type: Article

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