Strain-dependent brain defects in mouse models of primary ciliary dyskinesia with mutations in Pcdp1 and Spef2

Neuroscience

Volumn 277, Issue , 2014, Pages 552-567

  Finn, R ^a   Evans, C C ^a   Lee, L ^a,b  

^a SANFORD RESEARCH   (United States)

^b UNIVERSITY OF SOUTH DAKOTA   (United States)

Author keywords

Cfap221; Cilia; Hydrocephalus; Pcdp1; Primary ciliary dyskinesia; Spef2

Indexed keywords

BROMETHOL; PCDP1 PROTEIN, MOUSE; PROTEIN; SPEF2 PROTEIN, MOUSE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; BRAIN DAMAGE; BRAIN NERVE CELL; CELL ACTIVATION; CELL POPULATION; CEREBROSPINAL FLUID FLOW; CILIARY DYSKINESIA; COGNITIVE DEFECT; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE SEVERITY; DNA MODIFICATION; EPENDYMA; EX VIVO STUDY; GENE; GENE FUNCTION; GENE MUTATION; HISTOPATHOLOGY; HYDROCEPHALUS; IMMUNOHISTOCHEMISTRY; IN VIVO STUDY; MICROGLIA; MOUSE; MYELINATION; NONHUMAN; PCDP1 GENE; PRIORITY JOURNAL; SPEF2 GENE; 129S6/SVEVTAC MOUSE; C57BL 6 MOUSE; CILIARY MOTILITY; STRAIN DIFFERENCE; 129 MOUSE; ANIMAL; BRAIN; C57BL MOUSE; CEREBROSPINAL FLUID; DISEASE MODEL; GENETIC PREDISPOSITION; GENETICS; KARTAGENER SYNDROME; METABOLISM; MUTATION; NERVE CELL; OLIGODENDROGLIA; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; SEVERITY OF ILLNESS INDEX; SPECIES DIFFERENCE; TRANSGENIC MOUSE;

ANIMALS; BRAIN; CEREBROSPINAL FLUID; DISEASE MODELS, ANIMAL; GENETIC PREDISPOSITION TO DISEASE; HYDROCEPHALUS; IMMUNOHISTOCHEMISTRY; KARTAGENER SYNDROME; MICE, 129 STRAIN; MICE, INBRED C57BL; MICE, TRANSGENIC; MUTATION; NEURONS; OLIGODENDROGLIA; PROTEINS; SEVERITY OF ILLNESS INDEX; SPECIES SPECIFICITY;

EID: 84907033632     PISSN: 03064522     EISSN: 18737544     Source Type: Journal    
DOI: 10.1016/j.neuroscience.2014.07.029     Document Type: Article

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