Hematopoietic stem cell dysfunction underlies the progressive lymphocytopenia in XLF/Cernunnos deficiency

Blood

Volumn 124, Issue 10, 2014, Pages 1622-1625

  Avagyan, Serine ^a,b   Churchill, Michael ^a   Yamamoto, Kenta ^a,b   Crowe, Jennifer L ^a,b   Li, Chen ^b   Lee, Brian J ^b   Zheng, Tian ^c   Mukherjee, Siddhartha ^a   Zha, Shan ^a,b  

^a Columbia University Medical Center ^*  (United States)

^b NewYork Presbyterian Hospital   (United States)

^c Och Spine at New York Presbyterian Hospitals   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; UNCLASSIFIED DRUG; XRCC4 LIKE FACTOR; DNA BINDING PROTEIN; XLF PROTEIN, MOUSE;

AGED; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL AGING; CELL RENEWAL; CONTROLLED STUDY; DISEASE COURSE; DNA END JOINING REPAIR; FUNCTIONAL STATUS; GENE REARRANGEMENT; HEMATOPOIETIC STEM CELL; IMMUNE RESPONSE; LYMPHOCYTOPENIA; MOUSE; NONHUMAN; PREMATURE AGING; PROTEIN DEFICIENCY; VDJ RECOMBINATION; XRCC4 LIKE FACTOR DEFICIENCY; AGING; ANIMAL; C57BL MOUSE; CELL CULTURE; GENETICS; IMMUNOLOGY; KNOCKOUT MOUSE; PATHOPHYSIOLOGY; PHYSIOLOGY;

AGING; ANIMALS; CELL AGING; CELLS, CULTURED; DISEASE PROGRESSION; DNA-BINDING PROTEINS; HEMATOPOIETIC STEM CELLS; LYMPHOPENIA; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT;

EID: 84907013527     PISSN: 00064971     EISSN: 15280020     Source Type: Journal    
DOI: 10.1182/blood-2014-05-574863     Document Type: Article

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