메뉴 건너뛰기




Volumn 189, Issue 10, 2014, Pages 1181-1186

Update in cystic fibrosis 2013

Author keywords

[No Author keywords available]

Indexed keywords

AZITHROMYCIN; CHLORIDE; CIGARETTE SMOKE; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; GLUTATHIONE; INDOLEAMINE 2,3 DIOXYGENASE; INTERLEUKIN 17; INTERLEUKIN 17F; INTERLEUKIN 1BETA; INTERLEUKIN 23; INTERLEUKIN 6; IVACAFTOR; LEUKOCYTE ELASTASE; PLACEBO;

EID: 84901008941     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.201402-0203UP     Document Type: Article
Times cited : (23)

References (48)
  • 2
    • 84866097633 scopus 로고    scopus 로고
    • Personalized medicine in cystic fibrosis: Dawning of a new era
    • Clancy JP, Jain M. Personalized medicine in cystic fibrosis: dawning of a new era. Am J Respir Crit Care Med 2012;186:593-597.
    • (2012) Am J Respir Crit Care Med , vol.186 , pp. 593-597
    • Clancy, J.P.1    Jain, M.2
  • 6
    • 0032081281 scopus 로고    scopus 로고
    • Activation of NFkappaB by adherent Pseudomonas aeruginosa in normal and cystic fibrosis respiratory epithelial cells
    • DiMango E, Ratner AJ, Bryan R, Tabibi S, Prince A. Activation of NFkappaB by adherent Pseudomonas aeruginosa in normal and cystic fibrosis respiratory epithelial cells. J Clin Invest 1998;101: 2598-2605.
    • (1998) J Clin Invest , vol.101 , pp. 2598-2605
    • Dimango, E.1    Ratner, A.J.2    Bryan, R.3    Tabibi, S.4    Prince, A.5
  • 7
    • 0034939593 scopus 로고    scopus 로고
    • Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na(1)] and pH but elevated viscosity
    • Jayaraman S, Joo NS, Reitz B, Wine JJ, Verkman AS. Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na(1)] and pH but elevated viscosity. Proc Natl Acad Sci USA 2001;98: 8119-8123.
    • (2001) Proc Natl Acad Sci USA , vol.98 , pp. 8119-8123
    • Jayaraman, S.1    Joo, N.S.2    Reitz, B.3    Wine, J.J.4    Verkman, A.S.5
  • 8
    • 0022485439 scopus 로고
    • Lysosomal enzymes from polymorphonuclear leukocytes and proteinase inhibitors in patients with cystic fibrosis
    • Goldstein W, Döring G. Lysosomal enzymes from polymorphonuclear leukocytes and proteinase inhibitors in patients with cystic fibrosis. Am Rev Respir Dis 1986;134:49-56.
    • (1986) Am Rev Respir Dis , vol.134 , pp. 49-56
    • Goldstein, W.1    Döring, G.2
  • 9
    • 0026681802 scopus 로고
    • Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line
    • Nakamura H, Yoshimura K, McElvaney NG, Crystal RG. Neutrophil elastase in respiratory epithelial lining fluid of individuals with cystic fibrosis induces interleukin-8 gene expression in a human bronchial epithelial cell line. J Clin Invest 1992;89:1478-1484.
    • (1992) J Clin Invest , vol.89 , pp. 1478-1484
    • Nakamura, H.1    Yoshimura, K.2    McElvaney, N.G.3    Crystal, R.G.4
  • 13
    • 84890539467 scopus 로고    scopus 로고
    • Trouble from the start: Airway structural anomalies present at birth in the cystic fibrosis piglet
    • Teague WG. Trouble from the start: airway structural anomalies present at birth in the cystic fibrosis piglet. Am J Respir Crit Care Med 2013; 188:1391-1392.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 1391-1392
    • Teague, W.G.1
  • 18
    • 84890042333 scopus 로고    scopus 로고
    • Are the smoking-induced diseases an acquired form of cystic fibrosis?
    • Crystal RG. Are the smoking-induced diseases an acquired form of cystic fibrosis? Am J Respir Crit Care Med 2013;188:1277-1278.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 1277-1278
    • Crystal, R.G.1
  • 23
    • 84872563157 scopus 로고    scopus 로고
    • The yin and yang of cystic fibrosis transmembrane conductance regulator function: Implications for chronic lung disease
    • Vij N, Downey GP. The yin and yang of cystic fibrosis transmembrane conductance regulator function: implications for chronic lung disease. Am J Respir Crit Care Med 2013;187:120-122.
    • (2013) Am J Respir Crit Care Med , vol.187 , pp. 120-122
    • Vij, N.1    Downey, G.P.2
  • 24
    • 80051554943 scopus 로고    scopus 로고
    • Lack of cystic fibrosis transmembrane conductance regulator in CD31 lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses
    • Mueller C, Braag SA, Keeler A, Hodges C, Drumm M, Flotte TR. Lack of cystic fibrosis transmembrane conductance regulator in CD31 lymphocytes leads to aberrant cytokine secretion and hyperinflammatory adaptive immune responses. Am J Respir Cell Mol Biol 2011;44:922-929.
    • (2011) Am J Respir Cell Mol Biol , vol.44 , pp. 922-4929
    • Mueller, C.1    Braag, S.A.2    Keeler, A.3    Hodges, C.4    Drumm, M.5    Flotte, T.R.6
  • 28
    • 84875204704 scopus 로고    scopus 로고
    • T-cell immunotherapy in cystic fibrosis: Weighing the risk/reward
    • Robinson KM, Alcorn JF. T-cell immunotherapy in cystic fibrosis: weighing the risk/reward. Am J Respir Crit Care Med 2013;187: 564-566.
    • (2013) Am J Respir Crit Care Med , vol.187 , pp. 564-566
    • Robinson, K.M.1    Alcorn, J.F.2
  • 30
    • 84890066658 scopus 로고    scopus 로고
    • Hypoxia, receptor for advanced glycation end products, and cystic fibrosis: A pathway to chronic inflammation?
    • McGuire JK. Hypoxia, receptor for advanced glycation end products, and cystic fibrosis: a pathway to chronic inflammation? Am J Respir Crit Care Med 2013;188:1280-1281.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 1280-1281
    • McGuire, J.K.1
  • 36
    • 84882715662 scopus 로고    scopus 로고
    • Early intervention for newborns screened for cystic fibrosis
    • Beydon N, Robinson PD. Early intervention for newborns screened for cystic fibrosis. Am J Respir Crit Care Med 2013;188:409-410.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 409-410
    • Beydon, N.1    Robinson, P.D.2
  • 37
    • 84885071273 scopus 로고    scopus 로고
    • Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: A randomised controlled trial
    • Davies J, Sheridan H, Bell N, Cunningham S, Davis SD, Elborn JS, Milla CE, Starner TD, Weiner DJ, Lee PS, et al. Assessment of clinical response to ivacaftor with lung clearance index in cystic fibrosis patients with a G551D-CFTR mutation and preserved spirometry: a randomised controlled trial. Lancet Respir Med 2013; 1:630-638.
    • (2013) Lancet Respir Med , vol.1 , pp. 630-638
    • Davies, J.1    Sheridan, H.2    Bell, N.3    Cunningham, S.4    Davis, S.D.5    Elborn, J.S.6    Milla, C.E.7    Starner, T.D.8    Weiner, D.J.9    Lee, P.S.10
  • 40
    • 0028129568 scopus 로고
    • Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
    • The Pulmozyme Study Group
    • Fuchs HJ, Borowitz DS, Christiansen DH, Morris EM, Nash ML, Ramsey BW, Rosenstein BJ, Smith AL, Wohl ME; The Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med 1994;331:637-642.
    • (1994) N Engl J Med , vol.331 , pp. 637-642
    • Fuchs, H.J.1    Borowitz, D.S.2    Christiansen, D.H.3    Morris, E.M.4    Nash, M.L.5    Ramsey, B.W.6    Rosenstein, B.J.7    Smith, A.L.8    Wohl, M.E.9
  • 42
    • 84884605636 scopus 로고    scopus 로고
    • Faster, higher, stronger
    • Rubin BK. Faster, higher, stronger. Am J Respir Crit Care Med 2013; 188:634-635.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 634-635
    • Rubin, B.K.1
  • 44
    • 84877584233 scopus 로고    scopus 로고
    • Whole-genome sequencing to identify transmission of Mycobacterium abscessus between patients with cystic fibrosis: A retrospective cohort study
    • Bryant JM, Grogono DM, Greaves D, Foweraker J, Roddick I, Inns T, Reacher M, Haworth CS, Curran MD, Harris SR, et al. Whole-genome sequencing to identify transmission of Mycobacterium abscessus between patients with cystic fibrosis: a retrospective cohort study. Lancet 2013;381:1551-1560.
    • (2013) Lancet , vol.381 , pp. 1551-1560
    • Bryant, J.M.1    Grogono, D.M.2    Greaves, D.3    Foweraker, J.4    Roddick, I.5    Inns, T.6    Reacher, M.7    Haworth, C.S.8    Curran, M.D.9    Harris, S.R.10
  • 46
    • 84885183409 scopus 로고    scopus 로고
    • Epidemiology of nontuberculous mycobacterial infections and associated chronic macrolide use among persons with cystic fibrosis
    • Binder AM, Adjemian J, Olivier KN, Prevots DR. Epidemiology of nontuberculous mycobacterial infections and associated chronic macrolide use among persons with cystic fibrosis. Am J Respir Crit Care Med 2013;188:807-812.
    • (2013) Am J Respir Crit Care Med , vol.188 , pp. 807-812
    • Binder, A.M.1    Adjemian, J.2    Olivier, K.N.3    Prevots, D.R.4
  • 48
    • 84879582796 scopus 로고    scopus 로고
    • Should adults with cystic fibrosis receive lung transplants? Outcomes versus progression of disease
    • Garrity ER Jr. Should adults with cystic fibrosis receive lung transplants? Outcomes versus progression of disease. Am J Respir Crit Care Med 2013;187:1283-1284.
    • (2013) Am J Respir Crit Care Med , vol.187 , pp. 1283-1284
    • Garrity Jr., E.R.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.