-
1
-
-
33144473276
-
Mucus properties in children with primary ciliary dyskinesia: Comparison with cystic fibrosis
-
Bush A, Payne D, Pike S, Jenkins G, Henke MO, Rubin BK. Mucus properties in children with primary ciliary dyskinesia: comparison with cystic fibrosis. Chest 2006;129:118-123.
-
(2006)
Chest
, vol.129
, pp. 118-123
-
-
Bush, A.1
Payne, D.2
Pike, S.3
Jenkins, G.4
Henke, M.O.5
Rubin, B.K.6
-
2
-
-
0442313529
-
Primary ciliary dyskinesia: Diagnostic and phenotypic features
-
Noone PG, Leigh MW, Sannuti A, Minnix SL, Carson JL, Hazucha M, Zariwala MA, Knowles MR. Primary ciliary dyskinesia: diagnostic and phenotypic features. Am J Respir Crit Care Med 2004;169:459-467.
-
(2004)
Am J Respir Crit Care Med
, vol.169
, pp. 459-467
-
-
Noone, P.G.1
Leigh, M.W.2
Sannuti, A.3
Minnix, S.L.4
Carson, J.L.5
Hazucha, M.6
Zariwala, M.A.7
Knowles, M.R.8
-
3
-
-
18844406237
-
Correlation between cough frequency and airway inflammation in children with primary ciliary dyskinesia
-
Zihlif N, Paraskakis E, Lex C, Van de Pohl LA, Bush A. Correlation between cough frequency and airway inflammation in children with primary ciliary dyskinesia. Pediatr Pulmonol 2005;39:551-557.
-
(2005)
Pediatr Pulmonol
, vol.39
, pp. 551-557
-
-
Zihlif, N.1
Paraskakis, E.2
Lex, C.3
Van De Pohl, L.A.4
Bush, A.5
-
4
-
-
33744498612
-
Markers of airway inflammation in primary ciliary dyskinesia studied using exhaled breath condensate
-
Zihlif N, Paraskakis E, Tripoli C, Lex C, Bush A. Markers of airway inflammation in primary ciliary dyskinesia studied using exhaled breath condensate. Pediatr Pulmonol 2006;41:509-514.
-
(2006)
Pediatr Pulmonol
, vol.41
, pp. 509-514
-
-
Zihlif, N.1
Paraskakis, E.2
Tripoli, C.3
Lex, C.4
Bush, A.5
-
5
-
-
36048972322
-
Airway remodelling in children with cystic fibrosis
-
Hilliard TN, Regamey N, Shute JK, Nicholson AG, Alton EW, Bush A, Davies JC. Airway remodelling in children with cystic fibrosis. Thorax 2007;62:1074-1080.
-
(2007)
Thorax
, vol.62
, pp. 1074-1080
-
-
Hilliard, T.N.1
Regamey, N.2
Shute, J.K.3
Nicholson, A.G.4
Alton, E.W.5
Bush, A.6
Davies, J.C.7
-
6
-
-
0030698259
-
Longitudinal study of lung function in a cohort of primary ciliary dyskinesia
-
Ellerman A, Bisgaard H. Longitudinal study of lung function in a cohort of primary ciliary dyskinesia. Eur Respir J 1997;10:2376-2379.
-
(1997)
Eur Respir J
, vol.10
, pp. 2376-2379
-
-
Ellerman, A.1
Bisgaard, H.2
-
7
-
-
9644259076
-
Multiple breath inert gas washout as a measure of ventilation distribution in children with cystic fibrosis
-
Aurora P, Gustafsson P, Bush A, Lindblad A, Oliver C, Wallis CE, Stocks J. Multiple breath inert gas washout as a measure of ventilation distribution in children with cystic fibrosis. Thorax 2004;59:1068-1073.
-
(2004)
Thorax
, vol.59
, pp. 1068-1073
-
-
Aurora, P.1
Gustafsson, P.2
Bush, A.3
Lindblad, A.4
Oliver, C.5
Wallis, C.E.6
Stocks, J.7
-
8
-
-
39049084491
-
Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis
-
Gustafsson PM, De Jong PA, Tiddens HA, Lindblad A. Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis. Thorax 2008;63:129-134.
-
(2008)
Thorax
, vol.63
, pp. 129-134
-
-
Gustafsson, P.M.1
De Jong, P.A.2
Tiddens, H.A.3
Lindblad, A.4
-
9
-
-
0347766074
-
Progressive damage on high resolution computed tomography despite stable lung function in cystic fibrosis
-
de Jong PA, Nakano Y, Lequin MH, Mayo JR, Woods R, Paré PD, Tiddens HA. Progressive damage on high resolution computed tomography despite stable lung function in cystic fibrosis. Eur Respir J 2004;23:93-97.
-
(2004)
Eur Respir J
, vol.23
, pp. 93-97
-
-
De Jong, P.A.1
Nakano, Y.2
Lequin, M.H.3
Mayo, J.R.4
Woods, R.5
Paré, P.D.6
Tiddens, H.A.7
-
10
-
-
49449118909
-
Structural and functional lung disease in primary ciliary dyskinesia
-
Santamaria F, Montella S, Tiddens HA, Guidi G, Casotti V, Maglione M, de Jong PA. Structural and functional lung disease in primary ciliary dyskinesia. Chest 2008;134:351-357.
-
(2008)
Chest
, vol.134
, pp. 351-357
-
-
Santamaria, F.1
Montella, S.2
Tiddens, H.A.3
Guidi, G.4
Casotti, V.5
Maglione, M.6
De Jong, P.A.7
-
11
-
-
39049105720
-
Lung clearance index is a sensitive, repeatable and practical measure of airways disease in adults with cystic fibrosis
-
Horsley AR, Gustafsson PM, Macleod KA, Saunders C, Greening AP, Porteous DJ, Davies JC, Cunningham S, Alton EW, Innes JA. Lung clearance index is a sensitive, repeatable and practical measure of airways disease in adults with cystic fibrosis. Thorax 2008;63:135-140.
-
(2008)
Thorax
, vol.63
, pp. 135-140
-
-
Horsley, A.R.1
Gustafsson, P.M.2
MacLeod, K.A.3
Saunders, C.4
Greening, A.P.5
Porteous, D.J.6
Davies, J.C.7
Cunningham, S.8
Alton, E.W.9
Innes, J.A.10
-
12
-
-
0346121620
-
Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis
-
Gustafsson PM, Aurora P, Lindblad A. Evaluation of ventilation maldistribution as an early indicator of lung disease in children with cystic fibrosis. Eur Respir J 2003;22:972-979.
-
(2003)
Eur Respir J
, vol.22
, pp. 972-979
-
-
Gustafsson, P.M.1
Aurora, P.2
Lindblad, A.3
-
13
-
-
58349084874
-
Ventilation heterogeneity in children with well controlled asthma with normal spirometry indicates residual airways disease
-
Macleod KA, Horsley AR, Bell NJ, Greening AP, Innes JA, Cunningham S. Ventilation heterogeneity in children with well controlled asthma with normal spirometry indicates residual airways disease. Thorax 2009;64: 33-37.
-
(2009)
Thorax
, vol.64
, pp. 33-37
-
-
Macleod, K.A.1
Horsley, A.R.2
Bell, N.J.3
Greening, A.P.4
Innes, J.A.5
Cunningham, S.6
-
14
-
-
79956360940
-
London cystic fibrosis collaboration Lung clearance index and hrct are complementary markers of lung abnormalities in young children with cf
-
Owens CM, Aurora P, Stanojevic S, Bush A, Wade A, Oliver C, Calder A, Price J, Carr SB, Shankar A, et al.; London Cystic Fibrosis Collaboration. Lung Clearance Index and HRCT are complementary markers of lung abnormalities in young children with CF. Thorax 2011;66:481-488.
-
(2011)
Thorax
, vol.66
, pp. 481-488
-
-
Owens, C.M.1
Aurora, P.2
Stanojevic, S.3
Bush, A.4
Wade, A.5
Oliver, C.6
Calder, A.7
Price, J.8
Carr, S.B.9
Shankar, A.10
-
15
-
-
78650016662
-
Sensitivity of lung clearance index and chest computed tomography in early cf lung disease
-
Ellemunter H, Fuchs SI, Unsinn KM, Freund MC, Waltner-Romen M, Steinkamp G, Gappa M. Sensitivity of Lung Clearance Index and chest computed tomography in early CF lung disease. Respir Med 2010;104: 1834-1842.
-
(2010)
Respir Med
, vol.104
, pp. 1834-1842
-
-
Ellemunter, H.1
Fuchs, S.I.2
Unsinn, K.M.3
Freund, M.C.4
Waltner-Romen, M.5
Steinkamp, G.6
Gappa, M.7
-
16
-
-
77951988740
-
Hypertonic saline improves the lci in paediatric patients with cf with normal lung function
-
Amin R, Subbarao P, Jabar A, Balkovec S, Jensen R, Kerrigan S, Gustafsson P, Ratjen F. Hypertonic saline improves the LCI in paediatric patients with CF with normal lung function. Thorax 2010;65:379-383.
-
(2010)
Thorax
, vol.65
, pp. 379-383
-
-
Amin, R.1
Subbarao, P.2
Jabar, A.3
Balkovec, S.4
Jensen, R.5
Kerrigan, S.6
Gustafsson, P.7
Ratjen, F.8
-
17
-
-
79953287790
-
The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis
-
Amin R, Subbarao P, Lou W, Jabar A, Balkovec S, Jensen R, Kerrigan S, Gustafsson P, Ratjen F. The effect of dornase alfa on ventilation inhomogeneity in patients with cystic fibrosis. Eur Respir J 2011;37: 806-812.
-
(2011)
Eur Respir J
, vol.37
, pp. 806-812
-
-
Amin, R.1
Subbarao, P.2
Lou, W.3
Jabar, A.4
Balkovec, S.5
Jensen, R.6
Kerrigan, S.7
Gustafsson, P.8
Ratjen, F.9
-
18
-
-
84855203126
-
Ventilation inhomogeneity in children with primary ciliary dyskinesia
-
Green K, Buchvald FF, Marthin JK, Hanel B, Gustafsson PM, Nielsen KG. Ventilation inhomogeneity in children with primary ciliary dyskinesia. Thorax 2012;67:49-53.
-
(2012)
Thorax
, vol.67
, pp. 49-53
-
-
Green, K.1
Buchvald, F.F.2
Marthin, J.K.3
Hanel, B.4
Gustafsson, P.M.5
Nielsen, K.G.6
-
19
-
-
84855186954
-
Lung clearance index and structural lung disease in cystic fibrosis: A comparison with primary ciliary dyskinesia
-
Ives A, Irving S, Hogg C, Edey A, Hansell DM, Alton EW, Davies JC, Bush A. Lung clearance index and structural lung disease in cystic fibrosis: A comparison with primary ciliary dyskinesia. Pediatr Pulmonol 2010;45:361.
-
(2010)
Pediatr Pulmonol
, vol.45
, pp. 361
-
-
Ives, A.1
Irving, S.2
Hogg, C.3
Edey, A.4
Hansell, D.M.5
Alton, E.W.6
Davies, J.C.7
Bush, A.8
-
20
-
-
36849090559
-
Primary ciliary dyskinesia: Current state of the art
-
Bush A, Chodhari R, Collins N, Copeland F, Hall P, Harcourt J, Hariri M, Hogg C, Lucas J, Mitchison HM, et al. Primary ciliary dyskinesia: current state of the art. Arch Dis Child 2007;92:1136-1140.
-
(2007)
Arch Dis Child
, vol.92
, pp. 1136-1140
-
-
Bush, A.1
Chodhari, R.2
Collins, N.3
Copeland, F.4
Hall, P.5
Harcourt, J.6
Hariri, M.7
Hogg, C.8
Lucas, J.9
Mitchison, H.M.10
-
21
-
-
0031900652
-
Cystic fibrosis foundation consensus panel, the diagnosis of cystic fibrosis: A consensus statement
-
Rosenstein BJ, Cutting GR; Cystic Fibrosis Foundation Consensus Panel. The diagnosis of cystic fibrosis: A consensus statement. J Pediatr 1998;132:589-595.
-
(1998)
J Pediatr
, vol.132
, pp. 589-595
-
-
Rosenstein, B.J.1
Cutting, G.R.2
-
22
-
-
47049115524
-
Cystic fibrosis foundation Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic fibrosis foundation consensus report
-
Farrell PM, Rosenstein BJ, White TB, Accurso FJ, Castellani C, Cutting GR, Durie PR, Legrys VA, Massie J, Parad RB, et al.; Cystic Fibrosis Foundation. Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report. J Pediatr 2008;153:S4-S14.
-
(2008)
J Pediatr
, vol.153
-
-
Farrell, P.M.1
Rosenstein, B.J.2
White, T.B.3
Accurso, F.J.4
Castellani, C.5
Cutting, G.R.6
Durie, P.R.7
Legrys, V.A.8
Massie, J.9
Parad, R.B.10
-
24
-
-
34250190592
-
American thoracic society/european respiratory society working group on infant and young children pulmonary function testing An official american thoracic society/european respiratory society statement: Pulmonary function testing in preschool children
-
Beydon N, Davis SD, Lombardi E, Allen JL, Arets HG, Aurora P, Bisgaard H, Davis GM, Ducharme FM, Eigen H, et al.; American Thoracic Society/European Respiratory Society Working Group on Infant and Young Children Pulmonary Function Testing. An official American Thoracic Society/European Respiratory Society statement: pulmonary function testing in preschool children. Am J Respir Crit Care Med 2007;175:1304-1345.
-
(2007)
Am J Respir Crit Care Med
, vol.175
, pp. 1304-1345
-
-
Beydon, N.1
Davis, S.D.2
Lombardi, E.3
Allen, J.L.4
Arets, H.G.5
Aurora, P.6
Bisgaard, H.7
Davis, G.M.8
Ducharme, F.M.9
Eigen, H.10
-
25
-
-
69949084415
-
Asthma uk spirometry collaborative group. Spirometry centile charts for young caucasian children: The asthma uk collaborative initiative
-
Stanojevic S, Wade A, Cole TJ, Lum S, Custovic A, Silverman M, Hall GL, Welsh L, Kirkby J, Nystad W, et al.; Asthma UK Spirometry Collaborative Group. Spirometry centile charts for young Caucasian children: the Asthma UK Collaborative Initiative. Am J Respir Crit Care Med 2009;180:547-552.
-
(2009)
Am J Respir Crit Care Med
, vol.180
, pp. 547-552
-
-
Stanojevic, S.1
Wade, A.2
Cole, T.J.3
Lum, S.4
Custovic, A.5
Silverman, M.6
Hall, G.L.7
Welsh, L.8
Kirkby, J.9
Nystad, W.10
-
26
-
-
38849129311
-
Reference ranges for spirometry across all ages: A new approach
-
Stanojevic S, Wade A, Stocks J, Hankinson J, Coates AL, Pan H, Rosenthal M, Corey M, Lebecque P, Cole TJ. Reference ranges for spirometry across all ages: A new approach. Am J Respir Crit Care Med 2008;177:253-260.
-
(2008)
Am J Respir Crit Care Med
, vol.177
, pp. 253-260
-
-
Stanojevic, S.1
Wade, A.2
Stocks, J.3
Hankinson, J.4
Coates, A.L.5
Pan, H.6
Rosenthal, M.7
Corey, M.8
Lebecque, P.9
Cole, T.J.10
-
27
-
-
84877593162
-
Changes in physiological, functional and structural markers of cystic fibrosis lung disease with treatment of a pulmonary exacerbation
-
Horsley AR, Davies JC, Gray RD, Macleod KA, Donovan J, Aziz ZA, Bell NJ, Rainer M, Mt-Isa S, Voase N, et al. Changes in physiological, functional and structural markers of cystic fibrosis lung disease with treatment of a pulmonary exacerbation. Thorax 2013;68:532-539.
-
(2013)
Thorax
, vol.68
, pp. 532-539
-
-
Horsley, A.R.1
Davies, J.C.2
Gray, R.D.3
MacLeod, K.A.4
Donovan, J.5
Aziz, Z.A.6
Bell, N.J.7
Rainer, M.8
Mt-Isa, S.9
Voase, N.10
-
28
-
-
33645096073
-
Reproducibility of a scoring system for computed tomography scanning in cystic fibrosis
-
Brody AS, Kosorok MR, Li Z, Broderick LS, Foster JL, Laxova A, Bandla H, Farrell PM. Reproducibility of a scoring system for computed tomography scanning in cystic fibrosis. J Thorac Imaging 2006;21:14-21.
-
(2006)
J Thorac Imaging
, vol.21
, pp. 14-21
-
-
Brody, A.S.1
Kosorok, M.R.2
Li, Z.3
Broderick, L.S.4
Foster, J.L.5
Laxova, A.6
Bandla, H.7
Farrell, P.M.8
-
29
-
-
12744277962
-
London cystic fibrosis collaboration Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis
-
Aurora P, Bush A, Gustafsson P, Oliver C, Wallis C, Price J, Stroobant J, Carr S, Stocks J; London Cystic Fibrosis Collaboration. Multiple-breath washout as a marker of lung disease in preschool children with cystic fibrosis. Am J Respir Crit Care Med 2005;171:249-256.
-
(2005)
Am J Respir Crit Care Med
, vol.171
, pp. 249-256
-
-
Aurora, P.1
Bush, A.2
Gustafsson, P.3
Oliver, C.4
Wallis, C.5
Price, J.6
Stroobant, J.7
Carr, S.8
Stocks, J.9
-
30
-
-
34247571813
-
High-resolution ct of patients with primary ciliary dyskinesia
-
Kennedy MP, Noone PG, Leigh MW, Zariwala MA, Minnix SL, Knowles MR, Molina PL. High-resolution CT of patients with primary ciliary dyskinesia. AJR Am J Roentgenol 2007;188:1232-1238.
-
(2007)
AJR Am J Roentgenol
, vol.188
, pp. 1232-1238
-
-
Kennedy, M.P.1
Noone, P.G.2
Leigh, M.W.3
Zariwala, M.A.4
Minnix, S.L.5
Knowles, M.R.6
Molina, P.L.7
-
31
-
-
67349175293
-
Lung clearance index in the assessment of airways disease
-
Horsley A. Lung clearance index in the assessment of airways disease. Respir Med 2009;103:793-799.
-
(2009)
Respir Med
, vol.103
, pp. 793-799
-
-
Horsley, A.1
-
32
-
-
32844456339
-
Mucociliary and long-term particle clearance in airways of patients with immotile cilia
-
Möller W, Häussinger K, Ziegler-Heitbrock L, Heyder J. Mucociliary and long-term particle clearance in airways of patients with immotile cilia. Respir Res 2006;7:10.
-
(2006)
Respir Res
, vol.7
, pp. 10
-
-
Möller, W.1
Häussinger, K.2
Ziegler-Heitbrock, L.3
Heyder, J.4
-
33
-
-
0028343344
-
Mucociliary clearance in patients with cystic fibrosis and in normal subjects
-
Regnis JA, Robinson M, Bailey DL, Cook P, Hooper P, Chan HK, Gonda I, Bautovich G, Bye PT. Mucociliary clearance in patients with cystic fibrosis and in normal subjects. Am J Respir Crit Care Med 1994;150:66-71.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 66-71
-
-
Regnis, J.A.1
Robinson, M.2
Bailey, D.L.3
Cook, P.4
Hooper, P.5
Chan, H.K.6
Gonda, I.7
Bautovich, G.8
Bye, P.T.9
|