Cellular stress pathways in pediatric bone marrow failure syndromes: Many roads lead to neutropenia

Pediatric Research

Volumn 75, Issue 1-2, 2014, Pages 189-195

  Glaubach, Taly ^a,b   Minella, Alex C ^a   Corey, Seth J ^a,b  

^a NORTHWESTERN UNIVERSITY   (United States)

^b CHILDREN'S MEMORIAL HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

APOPTOSIS; BONE MARROW EXAMINATION; CELL DIFFERENTIATION; CELL STRESS; CELL SURVIVAL; CSF3R GENE; ELANE GENE; ENDOPLASMIC RETICULUM STRESS; G6PC3 GENE; GENE; GENE MUTATION; GENETIC HETEROGENEITY; GENETIC VARIABILITY; GF1 GENE; HAX1 GENE; HUMAN; IN VIVO STUDY; MITOCHONDRIAL MEMBRANE POTENTIAL; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; REVIEW; SEVERE CONGENITAL NEUTROPENIA; SHWACHMAN SYNDROME; UNFOLDED PROTEIN RESPONSE; WAS GENE;

ANIMALS; APOPTOSIS; GENETIC PREDISPOSITION TO DISEASE; HEMOGLOBINURIA, PAROXYSMAL; HUMANS; MUTATION; NEUTROPENIA; NEUTROPHILS; PHENOTYPE; RISK FACTORS; SIGNAL TRANSDUCTION; STRESS, PHYSIOLOGICAL;

EID: 84900439144     PISSN: 00313998     EISSN: 15300447     Source Type: Journal    
DOI: 10.1038/pr.2013.197     Document Type: Review

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