SBDS-deficient cells undergo accelerated apoptosis through the Fas-pathway

Haematologica

Volumn 93, Issue 3, 2008, Pages 363-371

  Rujkijyanont, Piya ^a,b   Watanabe, Ken Ichiro ^a,b   Ambekar, Chhaya ^a,b   Wang, Hanming ^a,b   Schimmer, Aaron ^c   Beyene, Joseph ^a   Dror, Yigal ^a,b  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b HOSPITAL FOR SICK CHILDREN   (Canada)

^c Ontario Cancer Institute   (Canada)

Author keywords

Apoptosis; Fas; SBDS; shRNA; Shwachman Diamond syndrome

Indexed keywords

CASPASE 8; CASPASE 9; FAS ANTIGEN; PROTEIN BAX; PROTEIN BCL 2; PROTEIN BCL XL;

APOPTOSIS; ARTICLE; BONE MARROW DISEASE; CELL GROWTH; CELL VIABILITY; CONTROLLED STUDY; FLOW CYTOMETRY; GENE; GENE EXPRESSION; GENE MUTATION; HELA CELL; HUMAN; HUMAN CELL; LYMPHOBLASTOID CELL; PANCREAS DISEASE; POLYMERASE CHAIN REACTION; SBDS GENE; SHWACHMAN SYNDROME; WESTERN BLOTTING;

ANTIGENS, CD95; APOPTOSIS; BCL-2-ASSOCIATED X PROTEIN; BCL-X PROTEIN; BONE MARROW; BONE MARROW DISEASES; CASPASE 8; CASPASE 9; CELL LINE; DWARFISM; GENE EXPRESSION REGULATION; GENE TARGETING; GENES, BCL-2; HELA CELLS; HUMANS; PANCREATIC DISEASES; PROTEINS; PROTO-ONCOGENE PROTEINS C-BCL-2; RNA, SMALL INTERFERING; SIGNAL TRANSDUCTION; SYNDROME;

EID: 40849145448     PISSN: 03906078     EISSN: None     Source Type: Journal    
DOI: 10.3324/haematol.11579     Document Type: Article

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