LC3, an autophagosome marker, is expressed on oligodendrocytes in Nasu-Hakola disease brains

Orphanet Journal of Rare Diseases

Volumn 9, Issue 1, 2014, Pages

  Satoh, Jun Ichi ^a   Motohashi, Nobutaka ^b   Kino, Yoshihiro ^a   Ishida, Tsuyoshi ^c   Yagishita, Saburo ^d   Jinnai, Kenji ^e   Arai, Nobutaka ^f   Nakamagoe, Kiyotaka ^g   Tamaoka, Akira ^g   Saito, Yuko ^h   Arima, Kunimasa ^h  

^a MEIJI PHARMACEUTICAL UNIVERSITY   (Japan)

^b UNIVERSITY OF YAMANASHI   (Japan)

^c 1 7 1 Kohnodai   (Japan)

^d KANAGAWA REHABILITATION CENTER   (Japan)

^e Japan   (Japan)

^f TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

^g UNIVERSITY OF TSUKUBA   (Japan)

^h NATIONAL INSTITUTE OF MENTAL HEALTH   (Japan)

Author keywords

Autophagy; LC3; Leukoencephalopathy; Nasu Hakola disease; Oligodendrocytes

Indexed keywords

BECLIN 1; BIOLOGICAL MARKER; HISTONE DEACETYLASE 6; MICROTUBULE ASSOCIATED PROTEIN 1 LIGHT CHAIN 3; UBIQUILIN 1; UBIQUITIN; UNCLASSIFIED DRUG;

ADULT; ARTICLE; AUTOPHAGOSOME; AUTOSOMAL RECESSIVE DISORDER; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; IMMUNOREACTIVITY; LEUKOENCEPHALOPATHY; MALE; MEMBRANOUS LIPODYSTROPHY; MULTIPLE SCLEROSIS; OLIGODENDROGLIA; PROTEIN EXPRESSION; RARE DISEASE; WESTERN BLOTTING; WHITE MATTER;

ADULT; AGED; BIOLOGICAL MARKERS; BRAIN; CASE-CONTROL STUDIES; FEMALE; HUMANS; LIPODYSTROPHY; MALE; MICROTUBULE-ASSOCIATED PROTEINS; MIDDLE AGED; OLIGODENDROGLIA; OSTEOCHONDRODYSPLASIAS; PHAGOSOMES; SUBACUTE SCLEROSING PANENCEPHALITIS;

EID: 84900404767     PISSN: None     EISSN: 17501172     Source Type: Journal    
DOI: 10.1186/1750-1172-9-68     Document Type: Article

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