Cellular mechanisms of ventricular arrhythmias in a mouse model of Timothy syndrome (long QT syndrome 8)

Journal of Molecular and Cellular Cardiology

Volumn 66, Issue , 2014, Pages 63-71

  Drum, Benjamin M L ^a   Dixon, Rose E ^a   Yuan, Can ^a   Cheng, Edward P ^a   Santana, Luis F ^a  

^a UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

Author keywords

Calcium wave; Excitation contraction coupling; Timothy syndrome; Ventricular myocyte

Indexed keywords

CALCIUM CHANNEL L TYPE; CALCIUM ION;

ANIMAL CELL; ARRHYTHMOGENESIS; ARTICLE; CALCIUM CELL LEVEL; CALCIUM TRANSPORT; CHANNEL GATING; CONTROLLED STUDY; CYTOSOL; DISEASE MODEL; GAIN OF FUNCTION MUTATION; HEART DEPOLARIZATION; HEART MUSCLE CELL; HEART MUSCLE FIBER MEMBRANE; HEART MUSCLE FIBER MEMBRANE POTENTIAL; HEART MUSCLE FIBER MEMBRANE STEADY POTENTIAL; HEART VENTRICLE ARRHYTHMIA; LONG QT SYNDROME; MOUSE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; PROBABILITY; PROTEIN EXPRESSION; SARCOPLASMIC RETICULUM; TIMOTHY SYNDROME; WAVEFORM; WILD TYPE;

PHLEUM PRATENSE;

CA(V)1.2; CALCIUM WAVE; EXCITATION-CONTRACTION COUPLING; TIMOTHY SYNDROME; VENTRICULAR MYOCYTE;

ACTION POTENTIALS; ANIMALS; CALCIUM; CALCIUM CHANNELS, L-TYPE; DISEASE MODELS, ANIMAL; EXCITATION CONTRACTION COUPLING; GENE EXPRESSION; HEART VENTRICLES; LONG QT SYNDROME; MICE; MYOCYTES, CARDIAC; SARCOPLASMIC RETICULUM; SYNDACTYLY;

EID: 84889021419     PISSN: 00222828     EISSN: 10958584     Source Type: Journal    
DOI: 10.1016/j.yjmcc.2013.10.021     Document Type: Article

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