메뉴 건너뛰기




Volumn 36, Issue 6, 2013, Pages 973-981

Carnitine supplementation attenuates myocardial lipid accumulation in long-chain acyl-CoA dehydrogenase knockout mice

Author keywords

[No Author keywords available]

Indexed keywords

CARNITINE; LIPID; LONG CHAIN ACYL COENZYME A DEHYDROGENASE; TRIACYLGLYCEROL;

EID: 84888203200     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-013-9604-4     Document Type: Article
Times cited : (30)

References (29)
  • 1
    • 80555156710 scopus 로고    scopus 로고
    • Fasting-induced myocardial lipid accumulation in long-chain acyl-CoA dehydrogenase knockout mice is accompanied by impaired left ventricular function
    • 21737602 10.1161/CIRCIMAGING.111.963751
    • Bakermans AJ, Geraedts TR, van Weeghel M et al (2011) Fasting-induced myocardial lipid accumulation in long-chain acyl-CoA dehydrogenase knockout mice is accompanied by impaired left ventricular function. Circ Cardiovasc Imaging 4(5):558-565
    • (2011) Circ Cardiovasc Imaging , vol.4 , Issue.5 , pp. 558-565
    • Bakermans, A.J.1    Geraedts, T.R.2    Van Weeghel, M.3
  • 2
    • 84884356419 scopus 로고    scopus 로고
    • Clinical and biological features at diagnosis in mitochondrial fatty acid beta-oxidation defects: A French pediatric study of 187 patients
    • doi:10.1007/s10545-012-9542-6
    • Baruteau J, Sachs P, Broue P et al (2012) Clinical and biological features at diagnosis in mitochondrial fatty acid beta-oxidation defects: a French pediatric study of 187 patients. J Inherit Metab Dis doi:10.1007/s10545- 012-9542-6
    • (2012) J Inherit Metab Dis
    • Baruteau, J.1    Sachs, P.2    Broue, P.3
  • 3
    • 0032729717 scopus 로고    scopus 로고
    • Arrhythmias and conduction defects as presenting symptoms of fatty acid oxidation disorders in children
    • 10577999 10.1161/01.CIR.100.22.2248 1:STN:280:DC%2BD3c%2FkslarsQ%3D%3D
    • Bonnet D, Martin D, de Lonlay P et al (1999) Arrhythmias and conduction defects as presenting symptoms of fatty acid oxidation disorders in children. Circulation 100(22):2248-2253
    • (1999) Circulation , vol.100 , Issue.22 , pp. 2248-2253
    • Bonnet, D.1    Martin, D.2    De Lonlay, P.3
  • 4
    • 0034066578 scopus 로고    scopus 로고
    • Regulation by carnitine of myocardial fatty acid and carbohydrate metabolism under normal and pathological conditions
    • 10826498 10.1007/s003950050167 1:CAS:528:DC%2BD3cXktVOnt7g%3D
    • Calvani M, Reda E, Arrigoni-Martelli E (2000) Regulation by carnitine of myocardial fatty acid and carbohydrate metabolism under normal and pathological conditions. Basic Res Cardiol 95(2):75-83
    • (2000) Basic Res Cardiol , vol.95 , Issue.2 , pp. 75-83
    • Calvani, M.1    Reda, E.2    Arrigoni-Martelli, E.3
  • 5
    • 67650502781 scopus 로고    scopus 로고
    • Mitochondrial long chain fatty acid beta-oxidation in man and mouse
    • 19465148 10.1016/j.bbalip.2009.05.006 1:CAS:528:DC%2BD1MXoslejt7s%3D
    • Chegary M, te Brinke H, Ruiter JP et al (2009) Mitochondrial long chain fatty acid beta-oxidation in man and mouse. Biochim Biophys Acta 1791(8):806-815
    • (2009) Biochim Biophys Acta , vol.1791 , Issue.8 , pp. 806-815
    • Chegary, M.1    Te Brinke, H.2    Ruiter, J.P.3
  • 6
    • 46749092545 scopus 로고    scopus 로고
    • Role of diet and fuel overabundance in the development and progression of heart failure
    • 18343896 10.1093/cvr/cvn074 1:CAS:528:DC%2BD1cXot1Wis74%3D
    • Chess DJ, Stanley WC (2008) Role of diet and fuel overabundance in the development and progression of heart failure. Cardiovasc Res 79(2):269-278
    • (2008) Cardiovasc Res , vol.79 , Issue.2 , pp. 269-278
    • Chess, D.J.1    Stanley, W.C.2
  • 7
    • 0034782503 scopus 로고    scopus 로고
    • Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse
    • 11590124 10.1093/hmg/10.19.2069 1:CAS:528:DC%2BD3MXnsl2ktLk%3D
    • Cox KB, Hamm DA, Millington DS et al (2001) Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse. Hum Mol Genet 10(19):2069-2077
    • (2001) Hum Mol Genet , vol.10 , Issue.19 , pp. 2069-2077
    • Cox, K.B.1    Hamm, D.A.2    Millington, D.S.3
  • 8
    • 70549113382 scopus 로고    scopus 로고
    • Cardiac hypertrophy in mice with long-chain acyl-CoA dehydrogenase or very long-chain acyl-CoA dehydrogenase deficiency
    • 19736549 10.1038/labinvest.2009.86 1:CAS:528:DC%2BD1MXhsVGrtL3L
    • Cox KB, Liu J, Tian L, Barnes S, Yang Q, Wood PA (2009) Cardiac hypertrophy in mice with long-chain acyl-CoA dehydrogenase or very long-chain acyl-CoA dehydrogenase deficiency. Lab Invest 89(12):1348-1354
    • (2009) Lab Invest , vol.89 , Issue.12 , pp. 1348-1354
    • Cox, K.B.1    Liu, J.2    Tian, L.3    Barnes, S.4    Yang, Q.5    Wood, P.A.6
  • 9
    • 0026061030 scopus 로고
    • Amphipathic lipid metabolites and their relation to arrhythmogenesis in the ischemic heart
    • 2038071 10.1016/0022-2828(91)90019-I 1:CAS:528:DyaK3MXhvVeitLw%3D
    • DaTorre SD, Creer MH, Pogwizd SM, Corr PB (1991) Amphipathic lipid metabolites and their relation to arrhythmogenesis in the ischemic heart. J Mol Cell Cardiol 23(Suppl 1):11-22
    • (1991) J Mol Cell Cardiol , vol.23 , Issue.SUPPL. 1 , pp. 11-22
    • Datorre, S.D.1    Creer, M.H.2    Pogwizd, S.M.3    Corr, P.B.4
  • 10
    • 84862008999 scopus 로고    scopus 로고
    • Lipid metabolism and toxicity in the heart
    • 22682221 10.1016/j.cmet.2012.04.006 1:CAS:528:DC%2BC38Xot12gsb4%3D
    • Goldberg IJ, Trent CM, Schulze PC (2012) Lipid metabolism and toxicity in the heart. Cell Metab 15(6):805-812
    • (2012) Cell Metab , vol.15 , Issue.6 , pp. 805-812
    • Goldberg, I.J.1    Trent, C.M.2    Schulze, P.C.3
  • 11
    • 0021873302 scopus 로고
    • Long-chain acyl coenzyme A dehydrogenase deficiency: An inherited cause of nonketotic hypoglycemia
    • 4022672 10.1203/00006450-198507000-00006 1:CAS:528:DyaL2MXks12gsb8%3D
    • Hale DE, Batshaw ML, Coates PM et al (1985) Long-chain acyl coenzyme A dehydrogenase deficiency: an inherited cause of nonketotic hypoglycemia. Pediatr Res 19(7):666-671
    • (1985) Pediatr Res , vol.19 , Issue.7 , pp. 666-671
    • Hale, D.E.1    Batshaw, M.L.2    Coates, P.M.3
  • 12
    • 37849024595 scopus 로고    scopus 로고
    • Evaluation of manual and automatic segmentation of the mouse heart from CINE MR images
    • 18050352 10.1002/jmri.21236
    • Heijman E, Aben JP, Penners C et al (2008) Evaluation of manual and automatic segmentation of the mouse heart from CINE MR images. J Magn Reson Imaging 27(1):86-93
    • (2008) J Magn Reson Imaging , vol.27 , Issue.1 , pp. 86-93
    • Heijman, E.1    Aben, J.P.2    Penners, C.3
  • 13
    • 13044277575 scopus 로고    scopus 로고
    • Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation
    • 9861014 10.1073/pnas.95.26.15592 1:CAS:528:DyaK1MXhvFejtg%3D%3D
    • Kurtz DM, Rinaldo P, Rhead WJ et al (1998) Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation. Proc Natl Acad Sci U S A 95(26):15592-15597
    • (1998) Proc Natl Acad Sci U S A , vol.95 , Issue.26 , pp. 15592-15597
    • Kurtz, D.M.1    Rinaldo, P.2    Rhead, W.J.3
  • 14
    • 33745067235 scopus 로고    scopus 로고
    • Carnitine supplementation induces long-chain acylcarnitine production - Studies in the VLCAD-deficient mouse
    • 16763898 10.1007/s10545-006-0249-4 1:CAS:528:DC%2BD28XlsV2ltbg%3D
    • Liebig M, Gyenes M, Brauers G et al (2006) Carnitine supplementation induces long-chain acylcarnitine production - studies in the VLCAD-deficient mouse. J Inherit Metab Dis 29(2-3):343-344
    • (2006) J Inherit Metab Dis , vol.29 , Issue.2-3 , pp. 343-344
    • Liebig, M.1    Gyenes, M.2    Brauers, G.3
  • 15
    • 84863312655 scopus 로고    scopus 로고
    • Variability in the clinical management of fatty acid oxidation disorders: Results of a survey of Canadian metabolic physicians
    • 21630065 10.1007/s10545-011-9352-2 1:CAS:528:DC%2BC38XkslWhuw%3D%3D
    • Potter BK, Little J, Chakraborty P et al (2012) Variability in the clinical management of fatty acid oxidation disorders: results of a survey of Canadian metabolic physicians. J Inherit Metab Dis 35(1):115-123
    • (2012) J Inherit Metab Dis , vol.35 , Issue.1 , pp. 115-123
    • Potter, B.K.1    Little, J.2    Chakraborty, P.3
  • 16
    • 45849135292 scopus 로고    scopus 로고
    • Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine
    • 18317232 10.1203/PDR.0b013e31816ff6f0 1:CAS:528:DC%2BD1cXlslGqtbs%3D
    • Primassin S, ter Veld F, Mayatepek E, Spiekerkoetter U (2008) Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine. Pediatr Res 63(6):632-637
    • (2008) Pediatr Res , vol.63 , Issue.6 , pp. 632-637
    • Primassin, S.1    Ter Veld, F.2    Mayatepek, E.3    Spiekerkoetter, U.4
  • 17
    • 0036197207 scopus 로고    scopus 로고
    • Fatty acid oxidation disorders
    • 11826276 10.1146/annurev.physiol.64.082201.154705 1:CAS:528: DC%2BD38XisFGmsb4%3D
    • Rinaldo P, Matern D, Bennett MJ (2002) Fatty acid oxidation disorders. Annu Rev Physiol 64:477-502
    • (2002) Annu Rev Physiol , vol.64 , pp. 477-502
    • Rinaldo, P.1    Matern, D.2    Bennett, M.J.3
  • 19
    • 69449103722 scopus 로고    scopus 로고
    • Treatment recommendations in long-chain fatty acid oxidation defects: Consensus from a workshop
    • 19452263 10.1007/s10545-009-1126-8 1:STN:280:DC%2BD1MrkslWnug%3D%3D
    • Spiekerkoetter U, Lindner M, Santer R et al (2009) Treatment recommendations in long-chain fatty acid oxidation defects: consensus from a workshop. J Inherit Metab Dis 32(4):498-505
    • (2009) J Inherit Metab Dis , vol.32 , Issue.4 , pp. 498-505
    • Spiekerkoetter, U.1    Lindner, M.2    Santer, R.3
  • 20
    • 77957574072 scopus 로고    scopus 로고
    • Current issues regarding treatment of mitochondrial fatty acid oxidation disorders
    • 20830526 10.1007/s10545-010-9188-1 1:CAS:528:DC%2BC3cXht1WhsbzM
    • Spiekerkoetter U, Bastin J, Gillingham M, Morris A, Wijburg F, Wilcken B (2010) Current issues regarding treatment of mitochondrial fatty acid oxidation disorders. J Inherit Metab Dis 33(5):555-561
    • (2010) J Inherit Metab Dis , vol.33 , Issue.5 , pp. 555-561
    • Spiekerkoetter, U.1    Bastin, J.2    Gillingham, M.3    Morris, A.4    Wijburg, F.5    Wilcken, B.6
  • 21
    • 0021053314 scopus 로고
    • Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels
    • 6646897 10.1203/00006450-198311000-00008 1:CAS:528:DyaL2cXitFaiug%3D%3D
    • Stanley CA, Hale DE, Coates PM et al (1983) Medium-chain acyl-CoA dehydrogenase deficiency in children with non-ketotic hypoglycemia and low carnitine levels. Pediatr Res 17(11):877-884
    • (1983) Pediatr Res , vol.17 , Issue.11 , pp. 877-884
    • Stanley, C.A.1    Hale, D.E.2    Coates, P.M.3
  • 22
    • 0035175317 scopus 로고    scopus 로고
    • A severe genotype with favourable outcome in very long chain acyl-CoA dehydrogenase deficiency
    • 11124787 10.1136/adc.84.1.58 1:STN:280:DC%2BD3M3itlOrug%3D%3D
    • Touma EH, Rashed MS, Vianey-Saban C et al (2001) A severe genotype with favourable outcome in very long chain acyl-CoA dehydrogenase deficiency. Arch Dis Child 84(1):58-60
    • (2001) Arch Dis Child , vol.84 , Issue.1 , pp. 58-60
    • Touma, E.H.1    Rashed, M.S.2    Vianey-Saban, C.3
  • 23
    • 0026096951 scopus 로고
    • Hypoglycemia, hypotonia, and cardiomyopathy: The evolving clinical picture of long-chain acyl-CoA dehydrogenase deficiency
    • 2000272 1:STN:280:DyaK3M7ls1Cisw%3D%3D
    • Treem WR, Stanley CA, Hale DE, Leopold HB, Hyams JS (1991) Hypoglycemia, hypotonia, and cardiomyopathy: the evolving clinical picture of long-chain acyl-CoA dehydrogenase deficiency. Pediatrics 87(3):328-333
    • (1991) Pediatrics , vol.87 , Issue.3 , pp. 328-333
    • Treem, W.R.1    Stanley, C.A.2    Hale, D.E.3    Leopold, H.B.4    Hyams, J.S.5
  • 24
    • 17144368393 scopus 로고    scopus 로고
    • Characterization of carnitine and fatty acid metabolism in the long-chain acyl-CoA dehydrogenase-deficient mouse
    • 15535801
    • van Vlies N, Tian L, Overmars H et al (2005) Characterization of carnitine and fatty acid metabolism in the long-chain acyl-CoA dehydrogenase-deficient mouse. Biochem J 387(Pt 1):185-193
    • (2005) Biochem J , vol.387 , Issue.PART 1 , pp. 185-193
    • Van Vlies, N.1    Tian, L.2    Overmars, H.3
  • 25
    • 0346308381 scopus 로고    scopus 로고
    • Improved method for accurate and efficient quantification of MRS data with use of prior knowledge
    • 9405214 10.1006/jmre.1997.1244 1:CAS:528:DyaK2sXnvFWnu7o%3D
    • Vanhamme L, van den Boogaart A, van Huffel S (1997) Improved method for accurate and efficient quantification of MRS data with use of prior knowledge. J Magn Reson 129(1):35-43
    • (1997) J Magn Reson , vol.129 , Issue.1 , pp. 35-43
    • Vanhamme, L.1    Van Den Boogaart, A.2    Van Huffel, S.3
  • 26
    • 15644369240 scopus 로고    scopus 로고
    • Carnitine palmitoyltransferase II specificity towards beta-oxidation intermediates - Evidence for a reverse carnitine cycle in mitochondria
    • 9654057 10.1046/j.1432-1327.1998.2530614.x 1:CAS:528:DyaK1cXkt1Sqt7Y%3D
    • Ventura FV, Ijlst L, Ruiter J et al (1998) Carnitine palmitoyltransferase II specificity towards beta-oxidation intermediates - evidence for a reverse carnitine cycle in mitochondria. Eur J Biochem 253(3):614-618
    • (1998) Eur J Biochem , vol.253 , Issue.3 , pp. 614-618
    • Ventura, F.V.1    Ijlst, L.2    Ruiter, J.3
  • 27
    • 0033037321 scopus 로고    scopus 로고
    • 13C] palmitic acid: An improved tool for the diagnosis of fatty acid oxidation defects
    • 10217622 10.1016/S0009-8981(98)00188-0 1:CAS:528:DyaK1MXhvVCmsrs%3D
    • 13C] palmitic acid: an improved tool for the diagnosis of fatty acid oxidation defects. Clin Chim Acta 281(1-2):1-17
    • (1999) Clin Chim Acta , vol.281 , Issue.1-2 , pp. 1-17
    • Ventura, F.V.1    Costa, C.G.2    Struys, E.A.3
  • 29
    • 0038042472 scopus 로고    scopus 로고
    • Treatment of carnitine deficiency
    • 12889658 10.1023/A:1024433100257 1:CAS:528:DC%2BD3sXkvVCku7s%3D
    • Winter SC (2003) Treatment of carnitine deficiency. J Inherit Metab Dis 26(2-3):171-180
    • (2003) J Inherit Metab Dis , vol.26 , Issue.2-3 , pp. 171-180
    • Winter, S.C.1


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.