-
1
-
-
84861559058
-
Transmissible proteins: expanding the prion heresy
-
Soto C, (2012) Transmissible proteins: expanding the prion heresy. Cell 149: 968-977.
-
(2012)
Cell
, vol.149
, pp. 968-977
-
-
Soto, C.1
-
2
-
-
84879751760
-
p53 Aggregates Penetrate Cells and Induce the Co-Aggregation of Intracellular p53
-
Forget KJ, Tremblay G, Roucou X, (2013) p53 Aggregates Penetrate Cells and Induce the Co-Aggregation of Intracellular p53. PLoS One 8: e69242.
-
(2013)
PLoS One
, vol.8
-
-
Forget, K.J.1
Tremblay, G.2
Roucou, X.3
-
3
-
-
84862620376
-
Cell biology. A unifying role for prions in neurodegenerative diseases
-
Prusiner SB, (2012) Cell biology. A unifying role for prions in neurodegenerative diseases. Science 336: 1511-1513.
-
(2012)
Science
, vol.336
, pp. 1511-1513
-
-
Prusiner, S.B.1
-
4
-
-
84875057980
-
The importance of prions
-
Telling GC, (2013) The importance of prions. PLoS Pathog 9: e1003090.
-
(2013)
PLoS Pathog
, vol.9
-
-
Telling, G.C.1
-
5
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
Will RG, Ironside JW, Zeidler M, Cousens SN, Estibeiro K, et al. (1996) A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 347: 921-925.
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.G.1
Ironside, J.W.2
Zeidler, M.3
Cousens, S.N.4
Estibeiro, K.5
-
6
-
-
84872473797
-
Advances in veterinary research
-
Gordon WS, (1946) Advances in veterinary research. Vet Res 58: 516-520.
-
(1946)
Vet Res
, vol.58
, pp. 516-520
-
-
Gordon, W.S.1
-
7
-
-
0032992340
-
Epidemic of transmissible spongiform encephalopathy in sheep and goats in Italy
-
Agrimi U, Ru G, Cardone F, Pocchiari M, Caramelli M, (1999) Epidemic of transmissible spongiform encephalopathy in sheep and goats in Italy. Lancet 353: 560-561.
-
(1999)
Lancet
, vol.353
, pp. 560-561
-
-
Agrimi, U.1
Ru, G.2
Cardone, F.3
Pocchiari, M.4
Caramelli, M.5
-
8
-
-
0025244011
-
Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication
-
Prusiner SB, Scott M, Foster D, Pan K-M, Groth D, et al. (1990) Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication. Cell 63: 673-686.
-
(1990)
Cell
, vol.63
, pp. 673-686
-
-
Prusiner, S.B.1
Scott, M.2
Foster, D.3
Pan, K.-M.4
Groth, D.5
-
9
-
-
0027229676
-
Propagation of prions with artificial properties in transgenic mice expressing chimeric PrP genes
-
Scott M, Groth D, Foster D, Torchia M, Yang S-L, et al. (1993) Propagation of prions with artificial properties in transgenic mice expressing chimeric PrP genes. Cell 73: 979-988.
-
(1993)
Cell
, vol.73
, pp. 979-988
-
-
Scott, M.1
Groth, D.2
Foster, D.3
Torchia, M.4
Yang, S.-L.5
-
10
-
-
0027956109
-
Cell-free formation of protease-resistant prion protein
-
Kocisko DA, Come JH, Priola SA, Chesebro B, Raymond GJ, et al. (1994) Cell-free formation of protease-resistant prion protein. Nature 370: 471-474.
-
(1994)
Nature
, vol.370
, pp. 471-474
-
-
Kocisko, D.A.1
Come, J.H.2
Priola, S.A.3
Chesebro, B.4
Raymond, G.J.5
-
11
-
-
0029161777
-
Different allelic effects of the codons 136 and 171 of the prion protein gene in sheep with natural scrapie
-
Clouscard C, Beaudry P, Elsen JM, Milan D, Dussaucy M, et al. (1995) Different allelic effects of the codons 136 and 171 of the prion protein gene in sheep with natural scrapie. J Gen Virol 76 (Pt 8) (): 2097-2101.
-
(1995)
J Gen Virol
, vol.76
, Issue.Pt 8
, pp. 2097-2101
-
-
Clouscard, C.1
Beaudry, P.2
Elsen, J.M.3
Milan, D.4
Dussaucy, M.5
-
12
-
-
0028043661
-
Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy
-
Bessen RA, Marsh RF, (1994) Distinct PrP properties suggest the molecular basis of strain variation in transmissible mink encephalopathy. J Virol 68: 7859-7868.
-
(1994)
J Virol
, vol.68
, pp. 7859-7868
-
-
Bessen, R.A.1
Marsh, R.F.2
-
13
-
-
12644272790
-
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity
-
Telling GC, Parchi P, DeArmond SJ, Cortelli P, Montagna P, et al. (1996) Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science 274: 2079-2082.
-
(1996)
Science
, vol.274
, pp. 2079-2082
-
-
Telling, G.C.1
Parchi, P.2
DeArmond, S.J.3
Cortelli, P.4
Montagna, P.5
-
14
-
-
84868253461
-
Characterization of Conformation-Dependent Prion Protein Epitopes
-
Kang HE, Weng CC, Saijo E, Saylor V, Bian J, et al. (2012) Characterization of Conformation-Dependent Prion Protein Epitopes. J Biol Chem 287 (44) ():: 37219-32.
-
(2012)
J Biol Chem
, vol.287
, Issue.44
, pp. 37219-37232
-
-
Kang, H.E.1
Weng, C.C.2
Saijo, E.3
Saylor, V.4
Bian, J.5
-
15
-
-
0036246734
-
New Zealand sheep with scrapie-susceptible PrP genotypes succumb to experimental challenge with a sheep-passaged scrapie isolate (SSBP/1)
-
Houston EF, Halliday SI, Jeffrey M, Goldmann W, Hunter N, (2002) New Zealand sheep with scrapie-susceptible PrP genotypes succumb to experimental challenge with a sheep-passaged scrapie isolate (SSBP/1). J Gen Virol 83: 1247-1250.
-
(2002)
J Gen Virol
, vol.83
, pp. 1247-1250
-
-
Houston, E.F.1
Halliday, S.I.2
Jeffrey, M.3
Goldmann, W.4
Hunter, N.5
-
16
-
-
0000332228
-
Further evidence that scrapie agent has an independent genome
-
In: Court LA, Dormont D, Brown P, Kingsbury DT, editors. Candé, France: L'Imprimerie Lefrancq et Cie
-
Dickinson AG, Outram GW, Taylor DM, Foster JD (1989) Further evidence that scrapie agent has an independent genome. In: Court LA, Dormont D, Brown P, Kingsbury DT, editors. Unconventional Virus Diseases of the Central Nervous System. Candé, France: L'Imprimerie Lefrancq et Cie. pp. 446-460.
-
(1989)
Unconventional Virus Diseases of the Central Nervous System
, pp. 446-460
-
-
Dickinson, A.G.1
Outram, G.W.2
Taylor, D.M.3
Foster, J.D.4
-
17
-
-
0024276258
-
The unusual properties of CH 1641, a sheep-passaged isolate of scrapie
-
Foster JD, Dickinson AG, (1988) The unusual properties of CH 1641, a sheep-passaged isolate of scrapie. Vet Rec 123: 5-8.
-
(1988)
Vet Rec
, vol.123
, pp. 5-8
-
-
Foster, J.D.1
Dickinson, A.G.2
-
18
-
-
0032892688
-
Molecular analysis of ovine prion protein identifies similarities between BSE and an experimental isolate of natural scrapie, CH1641
-
Hope J, Wood SC, Birkett CR, Chong A, Bruce ME, et al. (1999) Molecular analysis of ovine prion protein identifies similarities between BSE and an experimental isolate of natural scrapie, CH1641. J Gen Virol 80 (Pt 1) (): 1-4.
-
(1999)
J Gen Virol
, vol.80
, Issue.Pt 1
, pp. 1-4
-
-
Hope, J.1
Wood, S.C.2
Birkett, C.R.3
Chong, A.4
Bruce, M.E.5
-
19
-
-
34447639732
-
Continuum of prion protein structures enciphers a multitude of prion isolate-specified phenotypes
-
Legname G, Nguyen HO, Peretz D, Cohen FE, DeArmond SJ, et al. (2006) Continuum of prion protein structures enciphers a multitude of prion isolate-specified phenotypes. Proc Natl Acad Sci U S A 103: 19105-19110.
-
(2006)
Proc Natl Acad Sci U S A
, vol.103
, pp. 19105-19110
-
-
Legname, G.1
Nguyen, H.O.2
Peretz, D.3
Cohen, F.E.4
DeArmond, S.J.5
-
20
-
-
50849116428
-
Accelerated high fidelity prion amplification within and across prion species barriers
-
Green KM, Castilla J, Seward TS, Napier DL, Jewell JE, et al. (2008) Accelerated high fidelity prion amplification within and across prion species barriers. PLoS Pathog 4: e1000139.
-
(2008)
PLoS Pathog
, vol.4
-
-
Green, K.M.1
Castilla, J.2
Seward, T.S.3
Napier, D.L.4
Jewell, J.E.5
-
21
-
-
79953286302
-
The strain-encoded relationship between PrP replication, stability and processing in neurons is predictive of the incubation period of disease
-
Ayers JI, Schutt CR, Shikiya RA, Aguzzi A, Kincaid AE, et al. (2011) The strain-encoded relationship between PrP replication, stability and processing in neurons is predictive of the incubation period of disease. PLoS Pathog 7: e1001317.
-
(2011)
PLoS Pathog
, vol.7
-
-
Ayers, J.I.1
Schutt, C.R.2
Shikiya, R.A.3
Aguzzi, A.4
Kincaid, A.E.5
-
22
-
-
84863913395
-
Cofactor molecules maintain infectious conformation and restrict strain properties in purified prions
-
Deleault NR, Walsh DJ, Piro JR, Wang F, Wang X, et al. (2012) Cofactor molecules maintain infectious conformation and restrict strain properties in purified prions. Proc Natl Acad Sci U S A 109: E1938-1946.
-
(2012)
Proc Natl Acad Sci U S A
, vol.109
-
-
Deleault, N.R.1
Walsh, D.J.2
Piro, J.R.3
Wang, F.4
Wang, X.5
-
23
-
-
0026644090
-
Regional mapping of prion proteins in brains
-
Taraboulos A, Jendroska K, Serban D, Yang S-L, DeArmond SJ, et al. (1992) Regional mapping of prion proteins in brains. Proc Natl Acad Sci USA 89: 7620-7624.
-
(1992)
Proc Natl Acad Sci USA
, vol.89
, pp. 7620-7624
-
-
Taraboulos, A.1
Jendroska, K.2
Serban, D.3
Yang, S.-L.4
DeArmond, S.J.5
-
24
-
-
77952964383
-
Prion strain mutation determined by prion protein conformational compatibility and primary structure
-
Angers RC, Kang HE, Napier D, Browning S, Seward T, et al. (2010) Prion strain mutation determined by prion protein conformational compatibility and primary structure. Science 328: 1154-1158.
-
(2010)
Science
, vol.328
, pp. 1154-1158
-
-
Angers, R.C.1
Kang, H.E.2
Napier, D.3
Browning, S.4
Seward, T.5
-
25
-
-
0035859102
-
Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding
-
Saborio GP, Permanne B, Soto C, (2001) Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding. Nature 411: 810-813.
-
(2001)
Nature
, vol.411
, pp. 810-813
-
-
Saborio, G.P.1
Permanne, B.2
Soto, C.3
-
26
-
-
17444413067
-
In vitro generation of infectious scrapie prions
-
Castilla J, Saa P, Hetz C, Soto C, (2005) In vitro generation of infectious scrapie prions. Cell 121: 195-206.
-
(2005)
Cell
, vol.121
, pp. 195-206
-
-
Castilla, J.1
Saa, P.2
Hetz, C.3
Soto, C.4
-
27
-
-
0028052363
-
Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins
-
Westaway D, DeArmond SJ, Cayetano-Canlas J, Groth D, Foster D, et al. (1994) Degeneration of skeletal muscle, peripheral nerves, and the central nervous system in transgenic mice overexpressing wild-type prion proteins. Cell 76: 117-129.
-
(1994)
Cell
, vol.76
, pp. 117-129
-
-
Westaway, D.1
DeArmond, S.J.2
Cayetano-Canlas, J.3
Groth, D.4
Foster, D.5
-
28
-
-
84861172372
-
PrP(Sc) detection and infectivity in semen from scrapie-infected sheep
-
Rubenstein R, Bulgin MS, Chang B, Sorensen-Melson S, Petersen RB, et al. (2012) PrP(Sc) detection and infectivity in semen from scrapie-infected sheep. J Gen Virol 93: 1375-1383.
-
(2012)
J Gen Virol
, vol.93
, pp. 1375-1383
-
-
Rubenstein, R.1
Bulgin, M.S.2
Chang, B.3
Sorensen-Melson, S.4
Petersen, R.B.5
-
29
-
-
0035025625
-
Efficient transmission of two different sheep scrapie isolates in transgenic mice expressing the ovine PrP gene
-
Crozet C, Flamant F, Bencsik A, Aubert D, Samarut J, et al. (2001) Efficient transmission of two different sheep scrapie isolates in transgenic mice expressing the ovine PrP gene. J Virol 75: 5328-5334.
-
(2001)
J Virol
, vol.75
, pp. 5328-5334
-
-
Crozet, C.1
Flamant, F.2
Bencsik, A.3
Aubert, D.4
Samarut, J.5
-
30
-
-
0034761946
-
Florid plaques in ovine PrP transgenic mice infected with an experimental ovine BSE
-
Crozet C, Bencsik A, Flamant F, Lezmi S, Samarut J, et al. (2001) Florid plaques in ovine PrP transgenic mice infected with an experimental ovine BSE. EMBO Rep 2: 952-956.
-
(2001)
EMBO Rep
, vol.2
, pp. 952-956
-
-
Crozet, C.1
Bencsik, A.2
Flamant, F.3
Lezmi, S.4
Samarut, J.5
-
31
-
-
0034973230
-
Markedly increased susceptibility to natural sheep scrapie of transgenic mice expressing ovine prp
-
Vilotte JL, Soulier S, Essalmani R, Stinnakre MG, Vaiman D, et al. (2001) Markedly increased susceptibility to natural sheep scrapie of transgenic mice expressing ovine prp. J Virol 75: 5977-5984.
-
(2001)
J Virol
, vol.75
, pp. 5977-5984
-
-
Vilotte, J.L.1
Soulier, S.2
Essalmani, R.3
Stinnakre, M.G.4
Vaiman, D.5
-
32
-
-
65549138821
-
Transmission of scrapie and sheep-passaged bovine spongiform encephalopathy prions to transgenic mice expressing elk prion protein
-
Tamguney G, Miller MW, Giles K, Lemus A, Glidden DV, et al. (2009) Transmission of scrapie and sheep-passaged bovine spongiform encephalopathy prions to transgenic mice expressing elk prion protein. J Gen Virol 90: 1035-1047.
-
(2009)
J Gen Virol
, vol.90
, pp. 1035-1047
-
-
Tamguney, G.1
Miller, M.W.2
Giles, K.3
Lemus, A.4
Glidden, D.V.5
-
33
-
-
33751399001
-
Transmission and characterization of bovine spongiform encephalopathy sources in two ovine transgenic mouse lines (TgOvPrP4 and TgOvPrP59)
-
Cordier C, Bencsik A, Philippe S, Betemps D, Ronzon F, et al. (2006) Transmission and characterization of bovine spongiform encephalopathy sources in two ovine transgenic mouse lines (TgOvPrP4 and TgOvPrP59). J Gen Virol 87: 3763-3771.
-
(2006)
J Gen Virol
, vol.87
, pp. 3763-3771
-
-
Cordier, C.1
Bencsik, A.2
Philippe, S.3
Betemps, D.4
Ronzon, F.5
-
34
-
-
0027086835
-
Chimeric prion protein expression in cultured cells and transgenic mice
-
Scott MR, Köhler R, Foster D, Prusiner SB, (1992) Chimeric prion protein expression in cultured cells and transgenic mice. Protein Sci 1: 986-997.
-
(1992)
Protein Sci
, vol.1
, pp. 986-997
-
-
Scott, M.R.1
Köhler, R.2
Foster, D.3
Prusiner, S.B.4
-
35
-
-
0028349264
-
PrP genotype and agent effects in scrapie: change in allelic interaction with different isolates of agent in sheep, a natural host of scrapie
-
Goldmann W, Hunter N, Smith G, Foster J, Hope J, (1994) PrP genotype and agent effects in scrapie: change in allelic interaction with different isolates of agent in sheep, a natural host of scrapie. J Gen Virol 75: 989-995.
-
(1994)
J Gen Virol
, vol.75
, pp. 989-995
-
-
Goldmann, W.1
Hunter, N.2
Smith, G.3
Foster, J.4
Hope, J.5
-
36
-
-
34250904061
-
Molecular behaviors of "CH1641-like" sheep scrapie isolates in ovine transgenic mice (TgOvPrP4)
-
Baron T, Biacabe AG, (2007) Molecular behaviors of "CH1641-like" sheep scrapie isolates in ovine transgenic mice (TgOvPrP4). J Virol 81: 7230-7237.
-
(2007)
J Virol
, vol.81
, pp. 7230-7237
-
-
Baron, T.1
Biacabe, A.G.2
-
37
-
-
0029692399
-
Natural scrapie in a closed flock of Cheviot sheep occurs only in specific PrP genotypes
-
Hunter N, Foster JD, Goldmann W, Stear MJ, Hope J, et al. (1996) Natural scrapie in a closed flock of Cheviot sheep occurs only in specific PrP genotypes. Archives of virology 141: 809-824.
-
(1996)
Archives of Virology
, vol.141
, pp. 809-824
-
-
Hunter, N.1
Foster, J.D.2
Goldmann, W.3
Stear, M.J.4
Hope, J.5
-
38
-
-
84867031503
-
Susceptibility to scrapie and disease phenotype in sheep: cross-PRNP genotype experimental transmissions with natural sources
-
Gonzalez L, Jeffrey M, Dagleish MP, Goldmann W, Siso S, et al. (2012) Susceptibility to scrapie and disease phenotype in sheep: cross-PRNP genotype experimental transmissions with natural sources. Vet Res 43: 55.
-
(2012)
Vet Res
, vol.43
, pp. 55
-
-
Gonzalez, L.1
Jeffrey, M.2
Dagleish, M.P.3
Goldmann, W.4
Siso, S.5
-
39
-
-
41649087845
-
The elk PRNP codon 132 polymorphism controls cervid and scrapie prion propagation
-
Green KM, Browning SR, Seward TS, Jewell JE, Ross DL, et al. (2008) The elk PRNP codon 132 polymorphism controls cervid and scrapie prion propagation. J Gen Virol 89: 598-608.
-
(2008)
J Gen Virol
, vol.89
, pp. 598-608
-
-
Green, K.M.1
Browning, S.R.2
Seward, T.S.3
Jewell, J.E.4
Ross, D.L.5
-
40
-
-
10044224475
-
Human prion protein with valine 129 prevents expression of variant CJD phenotype
-
Wadsworth JD, Asante EA, Desbruslais M, Linehan JM, Joiner S, et al. (2004) Human prion protein with valine 129 prevents expression of variant CJD phenotype. Science 306: 1793-1796.
-
(2004)
Science
, vol.306
, pp. 1793-1796
-
-
Wadsworth, J.D.1
Asante, E.A.2
Desbruslais, M.3
Linehan, J.M.4
Joiner, S.5
-
41
-
-
36049020231
-
A general model of prion strains and their pathogenicity
-
Collinge J, Clarke AR, (2007) A general model of prion strains and their pathogenicity. Science 318: 930-936.
-
(2007)
Science
, vol.318
, pp. 930-936
-
-
Collinge, J.1
Clarke, A.R.2
-
42
-
-
0002358531
-
The scrapie replication-site hypothesis and its implications for pathogenesis
-
In: Prusiner SB, Hadlow WJ, editors. New York: Academic Press
-
Dickinson AG, Outram GW (1979) The scrapie replication-site hypothesis and its implications for pathogenesis. In: Prusiner SB, Hadlow WJ, editors. Slow Transmissible Diseases of the Nervous System, Vol 2. New York: Academic Press. pp. 13-31.
-
(1979)
Slow Transmissible Diseases of the Nervous System
, vol.2
, pp. 13-31
-
-
Dickinson, A.G.1
Outram, G.W.2
-
43
-
-
0026099887
-
The disease characteristics of different strains of scrapie in Sinc congenic mouse lines: implications for the nature of the agent and host control of pathogenesis
-
Bruce ME, McConnell I, Fraser H, Dickinson AG, (1991) The disease characteristics of different strains of scrapie in Sinc congenic mouse lines: implications for the nature of the agent and host control of pathogenesis. J Gen Virol 72: 595-603.
-
(1991)
J Gen Virol
, vol.72
, pp. 595-603
-
-
Bruce, M.E.1
McConnell, I.2
Fraser, H.3
Dickinson, A.G.4
-
44
-
-
0016431525
-
Extraneural competition between different scrapie agents leading to loss of infectivity
-
Dickinson AG, Fraser H, McConnell I, Outram GW, Sales DI, et al. (1975) Extraneural competition between different scrapie agents leading to loss of infectivity. Nature 253: 556.
-
(1975)
Nature
, vol.253
, pp. 556
-
-
Dickinson, A.G.1
Fraser, H.2
McConnell, I.3
Outram, G.W.4
Sales, D.I.5
-
45
-
-
77951996350
-
Coinfecting prion strains compete for a limiting cellular resource
-
Shikiya RA, Ayers JI, Schutt CR, Kincaid AE, Bartz JC, (2010) Coinfecting prion strains compete for a limiting cellular resource. J Virol 84: 5706-5714.
-
(2010)
J Virol
, vol.84
, pp. 5706-5714
-
-
Shikiya, R.A.1
Ayers, J.I.2
Schutt, C.R.3
Kincaid, A.E.4
Bartz, J.C.5
-
46
-
-
0028420937
-
129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal
-
Manson JC, Clarke AR, Hooper ML, Aitchison L, McConnell I, et al. (1994) 129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal. Mol Neurobiol 8: 121-127.
-
(1994)
Mol Neurobiol
, vol.8
, pp. 121-127
-
-
Manson, J.C.1
Clarke, A.R.2
Hooper, M.L.3
Aitchison, L.4
McConnell, I.5
-
47
-
-
53549095695
-
Cell-free propagation of prion strains
-
Castilla J, Morales R, Saa P, Barria M, Gambetti P, et al. (2008) Cell-free propagation of prion strains. EMBO J 27: 2557-2566.
-
(2008)
EMBO J
, vol.27
, pp. 2557-2566
-
-
Castilla, J.1
Morales, R.2
Saa, P.3
Barria, M.4
Gambetti, P.5
|