Complement activation in diseases presenting with thrombotic microangiopathy

European Journal of Internal Medicine

Volumn 24, Issue 6, 2013, Pages 496-502

  Meri, Seppo ^a  

^a UNIVERSITY OF HELSINKI   (Finland)

Author keywords

Complement factor; Complement regulation; H CD46; Hemolytic uremic syndrome; Microangiopathy; Thrombosis

Indexed keywords

CLASSICAL COMPLEMENT PATHWAY C3 C5 CONVERTASE; COMPLEMENT COMPONENT C3B; COMPLEMENT COMPONENT C4B; COMPLEMENT COMPONENT C5A; COMPLEMENT COMPONENT C5B; COMPLEMENT FACTOR H; MEMBRANE COFACTOR PROTEIN;

CELL SURFACE; COMPLEMENT ACTIVATION; DISEASE ASSOCIATION; GENE MUTATION; HUMAN; IMMUNOPATHOGENESIS; INFLAMMATION; MOLECULAR PATHOLOGY; PAROXYSMAL NOCTURNAL HEMOGLOBINURIA; PROGNOSIS; PROTEIN CLEAVAGE; PROTEIN FUNCTION; PROTEIN TARGETING; REVIEW; THROMBOSIS; THROMBOTIC THROMBOCYTOPENIC PURPURA;

A DISINTEGRIN AND METALLOPROTEINASE WITH A THROMBOSPONDIN TYPE 1 MOTIF, MEMBER 13; ADAMTS13; AHUS; ALTERNATIVE PATHWAY; AP; ATYPICAL HEMOLYTIC SYNDROME; CCP; CD46; COMPLEMENT CONTROL PROTEIN DOMAIN; COMPLEMENT FACTOR H; COMPLEMENT REGULATION; DDD; DENSE DEPOSIT DISEASE; DGKE; DIACYLGLYCEROL KINASE Ε; FACTOR H; FH; HEMOLYTIC UREMIC SYNDROME; MICROANGIOPATHY; PAROXYSMAL NOCTURNAL HEMOGLOBINURIA; PNH; SHIGA-TOXIN PRODUCING E. COLI; STEC; THROMBOSIS; THROMBOTIC MICROANGIOPATHY; THROMBOTIC THROMBOCYTOPENIC PURPURA; TMA; TTP;

ANTIGENS, CD46; AUTOANTIBODIES; COMPLEMENT ACTIVATION; COMPLEMENT C3; COMPLEMENT FACTOR B; COMPLEMENT FACTOR H; COMPLEMENT FACTOR I; COMPLEMENT PATHWAY, ALTERNATIVE; GENETIC PREDISPOSITION TO DISEASE; HEMOLYTIC-UREMIC SYNDROME; HUMANS; PURPURA, THROMBOTIC THROMBOCYTOPENIC; THROMBOMODULIN; THROMBOTIC MICROANGIOPATHIES;

EID: 84883561031     PISSN: 09536205     EISSN: 18790828     Source Type: Journal    
DOI: 10.1016/j.ejim.2013.05.009     Document Type: Review

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