Heparan sulfate in skeletal development, growth, and pathology: The case of hereditary multiple exostoses

Developmental Dynamics

Volumn 242, Issue 9, 2013, Pages 1021-1032

  Huegel, Julianne ^a   Sgariglia, Federica ^a   Enomoto Iwamoto, Motomi ^a   Koyama, Eiki ^a   Dormans, John P ^a   Pacifici, Maurizio ^a  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

Author keywords

Cell surface proteoglycans; Ectopic cartilage; Growth plate; Heparan sulfate; Hereditary multiple exostoses; Signaling proteins

Indexed keywords

COLLAGEN TYPE 10; COLLAGEN TYPE 2; EXT1 PROTEIN; EXT2 PROTEIN; GLUCURONIC ACID; HEPARAN SULFATE; N ACETYLGLUCOSAMINE; PROTEIN; SONIC HEDGEHOG PROTEIN; TRANSCRIPTION FACTOR SOX9; UNCLASSIFIED DRUG; EXOSTOSIN-1; EXOSTOSIN-2; N ACETYLGLUCOSAMINYLTRANSFERASE;

ARTICLE; BONE DEVELOPMENT; BONE GROWTH; CARBOHYDRATE SYNTHESIS; CHEMICAL MODIFICATION; CHRONIC PAIN; DISEASE COURSE; EXPERIMENTAL MODEL; GROWTH PLATE; GROWTH RETARDATION; HEREDITARY MULTIPLE EXOSTOSIS; HETEROZYGOSITY LOSS; HUMAN; MOLECULAR GENETICS; MOLECULAR INTERACTION; NONHUMAN; PATHOGENESIS; PATHOLOGY; POPULATION RESEARCH; PRIORITY JOURNAL; SIGNAL TRANSDUCTION; TARGET CELL; WILD TYPE; ANIMAL; BONE; ENZYMOLOGY; GENETICS; METABOLISM; MUSCULOSKELETAL DEVELOPMENT;

ANIMALS; BONE AND BONES; EXOSTOSES, MULTIPLE HEREDITARY; HEPARITIN SULFATE; HUMANS; MUSCULOSKELETAL DEVELOPMENT; N-ACETYLGLUCOSAMINYLTRANSFERASES;

EID: 84882653174     PISSN: 10588388     EISSN: 10970177     Source Type: Journal    
DOI: 10.1002/dvdy.24010     Document Type: Article

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