Treatment with the cysteine precursor L-2-oxothiazolidine-4-carboxylate (OTC) implicates taurine deficiency in severity of dystropathology in mdx mice

International Journal of Biochemistry and Cell Biology

Volumn 45, Issue 9, 2013, Pages 2097-2108

  Terrill, Jessica R ^a   Boyatzis, Amber ^a   Grounds, Miranda D ^a   Arthur, Peter G ^a  

^a UNIVERSITY OF WESTERN AUSTRALIA   (Australia)

Author keywords

Duchenne muscular dystrophy; L 2 Oxothiazolidine 4 carboxylate; Mdx mice; Oxidative stress; Taurine

Indexed keywords

2 OXO 4 THIAZOLIDINECARBOXYLIC ACID; CYSTEINE; GLUTATHIONE; TAURINE;

AMINO ACID DEFICIENCY; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DUCHENNE MUSCULAR DYSTROPHY; EX VIVO STUDY; MALE; MOUSE; MUSCLE DISEASE; NONHUMAN; OXIDATION; OXIDATIVE STRESS; TAURINE DEFICIENCY;

MUS;

-2-OXOTHIAZOLIDINE-4-CARBOXYLATE; 2-MERCAPTOETHANOL; 2-[6-(4-AMINOPHENOXY)-3-OXO-3H-XANTHEN-9-YL]BENZOIC ACID; 2ME; 4-(2-HYDROXYETHYL)-1-PIPERAZINEETHANESULFONIC ACID; 5,5′-DITHIOBIS-(2-NITROBENZOIC ACID); ACETONITRILE; ACN; APF; BODIPY FL-N-(2-AMINOETHYL) MALEIMIDE; CITRATE SYNTHASE; CK; CREATINE KINASE; CS; CTAB; DMD; DTNB; DUCHENNE MUSCULAR DYSTROPHY; EGTA; ETHYLENE GLYCOL TETRAACETIC ACID; FLM; GLUTATHIONE; GSH; GSSG; HEPES; HEXADECYLTRIMETHYLAMMONIUM BROMIDE; L-2-OXOTHIAZOLIDINE-4-CARBOXYLATE; MDX MICE; MPO; MYELOPEROXIDASE, N-ACETYLCYSTEINE; N-ETHYLMALEIMIDE; NEM; O-PHTHALALDEHYDE; OPA; OTCL; OXIDATIVE STRESS; OXIDIZED GLUTATHIONE; PBS; PHOSPHATE BUFFERED SALINE; REACTIVE OXYGEN SPECIES; ROS; SDS; SDS-PAGE; SODIUM DODECYL SULPHATE; SODIUM DODECYL SULPHATE POLYACRYLAMIDE GEL ELECTROPHORESIS; TAURINE; TCA; TCEP; TEXAS RED; TEXAS RED C2-MALEIMIDE; TNF; TRICHLOROACETIC ACID; TRIS(2-CARBOXYETHYL)PHOSPHINE; TUMOR NECROSIS FACTOR;

ACETYLCYSTEINE; ANIMALS; DISEASE MODELS, ANIMAL; MALE; MICE; MICE, INBRED C57BL; MUSCULAR DYSTROPHY, DUCHENNE; OXIDATIVE STRESS; PYRROLIDONECARBOXYLIC ACID; TAURINE; THIAZOLIDINES;

EID: 84881160375     PISSN: 13572725     EISSN: 18785875     Source Type: Journal    
DOI: 10.1016/j.biocel.2013.07.009     Document Type: Article

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