Axonal Transport Defects in a Mitofusin 2 Loss of Function Model of Charcot-Marie-Tooth Disease in Zebrafish

PLoS ONE

Volumn 8, Issue 6, 2013, Pages

  Chapman, Anna L ^a,b   Bennett, Ellen J ^a   Ramesh, Tennore M ^a   De Vos, Kurt J ^a   Grierson, Andrew J ^a,c  

^a UNIVERSITY OF SHEFFIELD   (United Kingdom)

^b UNIVERSITY OF MANCHESTER   (United Kingdom)

^c UNIVERSITY OF SHEFFIELD   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

MITOFUSIN 2; GUANOSINE TRIPHOSPHATASE; MITOFUSIN 2 PROTEIN, ZEBRAFISH; ZEBRAFISH PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL TRANSPORT; CONTROLLED STUDY; DISEASE COURSE; HEREDITARY MOTOR SENSORY NEUROPATHY; LOSS OF FUNCTION MUTATION; MITOCHONDRION; MOTOR DYSFUNCTION; NERVE FIBER TRANSPORT; NEUROMUSCULAR FUNCTION; NONHUMAN; NONSENSE MUTATION; ONSET AGE; PHENOTYPE; RECESSIVE INHERITANCE; SWIMMING; ZEBRA FISH; AMINO ACID SEQUENCE; ANIMAL; CHEMISTRY; DISEASE MODEL; GENETICS; HOMOZYGOTE; HUMAN; METABOLISM; MOTOR ACTIVITY; MUTATION; NERVE CELL; PATHOLOGY; PATHOPHYSIOLOGY;

DANIO RERIO; MUS;

AMINO ACID SEQUENCE; ANIMALS; AXONAL TRANSPORT; CHARCOT-MARIE-TOOTH DISEASE; DISEASE MODELS, ANIMAL; GTP PHOSPHOHYDROLASES; HOMOZYGOTE; HUMANS; MITOCHONDRIA; MOTOR ACTIVITY; MUTATION; NEURONS; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 84879478992     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0067276     Document Type: Article

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