Developmental defects and neuromuscular alterations due to mitofusin 2 gene (MFN2) silencing in zebrafish: A new model for Charcot-Marie-Tooth type 2A neuropathy

Neuromuscular Disorders

Volumn 21, Issue 1, 2011, Pages 58-67

  Vettori, Andrea ^a   Bergamin, Giorgia ^a   Moro, Enrico ^a   Vazza, Giovanni ^a   Polo, Giulia ^a   Tiso, Natascia ^a   Argenton, Francesco ^a   Mostacciuolo, Maria Luisa ^a  

^a UNIVERSITY OF PADOVA   (Italy)

Author keywords

Axonal degeneration; CMT2A; MFN2; Peripheral neuropathy; Zebrafish

Indexed keywords

CHOLINERGIC RECEPTOR; MITOFUSIN 2;

ADULT ANIMAL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHARCOT MARIE TOOTH DISEASE TYPE 2A; CONTROLLED STUDY; DEVELOPMENTAL DISORDER; DOWN REGULATION; EMBRYO; EMBRYO DEVELOPMENT; GENE; GENE FUNCTION; GENE MUTATION; GENE SILENCING; HEREDITARY MOTOR SENSORY NEUROPATHY; MFN2 GENE; MOTONEURON; MUSCLE CELL; NERVE FIBER GROWTH; NEUROMUSCULAR DISEASE; NONHUMAN; PATHOGENESIS; PRIORITY JOURNAL; ZEBRA FISH;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BODY PATTERNING; CHARCOT-MARIE-TOOTH DISEASE; COMPUTATIONAL BIOLOGY; DEVELOPMENTAL DISABILITIES; DISEASE MODELS, ANIMAL; DOWN-REGULATION; EMBRYO, NONMAMMALIAN; HUMANS; MEMBRANE PROTEINS; MITOCHONDRIAL PROTEINS; MOTOR ACTIVITY; NEUROMUSCULAR DISEASES; OLIGODEOXYRIBONUCLEOTIDES, ANTISENSE; RECEPTORS, CHOLINERGIC; RNA, MESSENGER; TOLLOID-LIKE METALLOPROTEINASES; TUBULIN; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 78650309622     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.nmd.2010.09.002     Document Type: Article

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