Abnormal accumulation and recycling of glycoproteins visualized in Niemann-Pick type C cells using the chemical reporter strategy

Proceedings of the National Academy of Sciences of the United States of America

Volumn 110, Issue 25, 2013, Pages 10207-10212

  Mbu, Ngalle Eric ^a   Flanagan Steet, Heather ^a   Johnson, Steven ^a   Wolfert, Margreet A ^a   Boons, Geert Jan ^a   Steet, Richard ^a,b  

^a UNIVERSITY OF GEORGIA   (United States)

^b NONE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHOLESTEROL; CYCLODEXTRIN; GLYCOLIPID; GLYCOPROTEIN;

ARTICLE; CELL MIGRATION; CHEMICAL ANALYSIS; CONTROLLED STUDY; ENDOSOME; FIBROBLAST; HUMAN; HUMAN CELL; LYSOSOME; NIEMANN PICK DISEASE; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

AZIDES; BETA-CYCLODEXTRINS; CARRIER PROTEINS; CELL LINE; CHOLESTEROL; DEXTRANS; ENDOSOMES; FIBROBLASTS; GALACTOSAMINE; GLYCOCONJUGATES; GLYCOPROTEINS; HUMANS; LYSOSOMES; MEMBRANE GLYCOPROTEINS; NIEMANN-PICK DISEASE, TYPE C; PROTEIN TRANSPORT; SIALOGLYCOPROTEINS;

EID: 84879322602     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1221105110     Document Type: Article

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