Functional and histopathological identification of the respiratory failure in a DMSXL transgenic mouse model of myotonic dystrophy

DMM Disease Models and Mechanisms

Volumn 6, Issue 3, 2013, Pages 622-631

  Panaite, Petrica Adrian ^a   Kuntzer, Thierry ^a   Gourdon, Geneviève ^c   Lobrinus, Johannes Alexander ^d   Barakat Walter, Ibtissam ^a,b  

^a LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

^b UNIVERSITY OF LAUSANNE   (Switzerland)

^c IMAGINE INSTITUTE   (France)

^d University Hospital   (Switzerland)

Author keywords

[No Author keywords available]

Indexed keywords

CHOLINERGIC RECEPTOR; MYOTONIC DYSTROPHY PROTEIN KINASE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN STEM; BREATHING; BREATHING MUSCLE; BREATHING PATTERN; CONTROLLED STUDY; DENERVATION; DIAPHRAGM MUSCLE; HISTOPATHOLOGY; MOTONEURON; MOTOR PERFORMANCE; MOUSE; MUSCLE ACTION POTENTIAL; MUSCLE BIOPSY; MUSCLE CELL; MYOTONIC DYSTROPHY; NERVE ENDING; NEUROMUSCULAR SYNAPSE; NONHUMAN; NONMYELINATED NERVE; PHRENIC NERVE; PLETHYSMOGRAPHY; POSTSYNAPTIC MEMBRANE; PRIORITY JOURNAL; RESPIRATORY FAILURE; RESPIRATORY FUNCTION; RESPIRATORY NERVE CELL; TRANSGENIC MOUSE;

ANIMALS; AXONS; BRAIN STEM; DIAPHRAGM; DISEASE MODELS, ANIMAL; HUMANS; IN SITU HYBRIDIZATION, FLUORESCENCE; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUSCLES; MYELIN SHEATH; MYOTONIC DYSTROPHY; NEUROMUSCULAR JUNCTION; PHRENIC NERVE; RESPIRATION; RESPIRATORY FUNCTION TESTS;

EID: 84877806741     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.010512     Document Type: Article

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