The expansion of 300 CTG repeats in myotonic dystrophy transgenic mice does not induce sensory or motor neuropathy

Acta Neuropathologica

Volumn 114, Issue 2, 2007, Pages 175-185

  Gantelet, E ^b   Kraftsik, R ^b   Delaloye, S ^b   Gourdon, G ^c   Kuntzer, T ^a   Barakat Walter, Ibtissam ^a,b  

^a UNIVERSITY OF LAUSANNE   (Switzerland)

^b LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

DM1 transgenic mice; Morphometric analysis; Myotonic dystrophy; Sensory neuropathy

Indexed keywords

ALPHA BUNGAROTOXIN; CHOLINERGIC RECEPTOR; CYTOSINE; GUANINE; MONOCLONAL ANTIBODY; MYOTONIC DYSTROPHY PROTEIN KINASE; THYMIDINE;

3' UNTRANSLATED REGION; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL COUNT; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; DEMYELINATION; DISEASE MODEL; ELECTRON MICROSCOPY; HINDLIMB; INCIDENCE; LUMBAR SPINAL CORD; MORPHOLOGY; MORPHOMETRICS; MOTONEURON; MOTOR NEUROPATHY; MOUSE; MYELINATION; MYOTONIC DYSTROPHY; NERVE CELL; NERVE ENDING; NERVE FIBER; NEUROFILAMENT; NEUROPATHY; NONHUMAN; PATHOGENESIS; PERIPHERAL NERVOUS SYSTEM; PHENOTYPE; PRIORITY JOURNAL; SCIATIC NERVE; SENSORY NERVE CELL; SENSORY NEUROPATHY; SPINAL GANGLION; STATISTICAL ANALYSIS; SURAL NERVE; TISSUE SECTION; TRANSGENIC MOUSE; TRINUCLEOTIDE REPEAT; WILD TYPE;

ANIMALS; AXONS; DEMYELINATING DISEASES; GANGLIA, SPINAL; HUMANS; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON, TRANSMISSION; MOTOR NEURONS; MYOTONIC DYSTROPHY; NEUROMUSCULAR JUNCTION; NEURONS, AFFERENT; PERIPHERAL NERVOUS SYSTEM DISEASES; SCIATIC NERVE; SPINAL CORD; SURAL NERVE; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 34547096527     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0205-x     Document Type: Article

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