메뉴 건너뛰기




Volumn 43, Issue 2, 2011, Pages 263-267

Impaired respiratory function in mdx and mdx/utrn+/- mice

Author keywords

Diaphragm fibrosis; Duchenne muscular dystrophy; mdx mice; Respiratory function; Whole body non invasive plethysmography

Indexed keywords

UTROPHIN;

EID: 78751670433     PISSN: 0148639X     EISSN: 10974598     Source Type: Journal    
DOI: 10.1002/mus.21848     Document Type: Article
Times cited : (60)

References (14)
  • 1
    • 0025998134 scopus 로고
    • Population frequencies of inherited neuromuscular diseases - A world survey
    • Emery AE. Population frequencies of inherited neuromuscular diseases - a world survey. Neuromuscul Disord 1991;1:19-29.
    • (1991) Neuromuscul Disord , vol.1 , pp. 19-29
    • Emery, A.E.1
  • 3
    • 0026782972 scopus 로고
    • Differential expression of muscular dystrophy in diaphragm versus hindlimb muscles of mdxmice
    • Dupont-Versteegden EE, McCarter RJ. Differential expression of muscular dystrophy in diaphragm versus hindlimb muscles of mdxmice. Muscle Nerve 1992;15:1105-1110.
    • (1992) Muscle Nerve , vol.15 , pp. 1105-1110
    • Dupont-Versteegden, E.E.1    McCarter, R.J.2
  • 4
  • 5
    • 30644470664 scopus 로고    scopus 로고
    • Temporal and spatial mRNA expression patterns of TGF-beta1, 2, 3 and TbetaRI, II, III in skeletal muscles of mdx mice
    • Zhou L, Porter JD, Cheng G, Gong B, Hatala DA, Merriam AP, et al. Temporal and spatial mRNA expression patterns of TGF-beta1, 2, 3 and TbetaRI, II, III in skeletal muscles of mdx mice. Neuromuscul Disord 2006;16:32-38.
    • (2006) Neuromuscul Disord , vol.16 , pp. 32-38
    • Zhou, L.1    Porter, J.D.2    Cheng, G.3    Gong, B.4    Hatala, D.A.5    Merriam, A.P.6
  • 7
    • 0035096268 scopus 로고    scopus 로고
    • Force and power output of diaphragm muscle strips from mdx and control mice after clenbuterol treatment
    • Lynch GS, Hinkle RT, Faulkner JA. Force and power output of diaphragm muscle strips from mdx and control mice after clenbuterol treatment. Neuromuscul Disord 2001;11:192-196.
    • (2001) Neuromuscul Disord , vol.11 , pp. 192-196
    • Lynch, G.S.1    Hinkle, R.T.2    Faulkner, J.A.3
  • 9
    • 0030848338 scopus 로고    scopus 로고
    • Skeletal and cardiac myopathies in mice lacking utrophin and dystrophin: A model for Duchenne muscular dystrophy
    • DOI 10.1016/S0092-8674(00)80533-4
    • Grady RM, Teng H, Nichol MC, Cunningham JC, Wilkinson RS, Sanes JR. Skeletal and cardiac myopathies in mice lacking utrophin and dystrophin: a model for Duchenne muscular dystrophy. Cell 1997;90:729-738. (Pubitemid 27357964)
    • (1997) Cell , vol.90 , Issue.4 , pp. 729-738
    • Grady, R.M.1    Teng, H.2    Nichol, M.C.3    Cunningham, J.C.4    Wilkinson, R.S.5    Sanest, J.R.6
  • 11
    • 33846946114 scopus 로고    scopus 로고
    • Angiotensin II type 1 receptor blockade attenuates TGF-betainduced failure of muscle regeneration in multiple myopathic states
    • Cohn RD, van Erp C, Habashi JP, Soleimani AA, Klein EC, Lisi MT, et al. Angiotensin II type 1 receptor blockade attenuates TGF-betainduced failure of muscle regeneration in multiple myopathic states. Nat Med 2007;13:204-210.
    • (2007) Nat Med , vol.13 , pp. 204-210
    • Cohn, R.D.1    Van Erp, C.2    Habashi, J.P.3    Soleimani, A.A.4    Klein, E.C.5    Lisi, M.T.6
  • 12
    • 68849130956 scopus 로고    scopus 로고
    • Imatinib attenuates skeletal muscle dystrophy in mdx mice
    • Huang P, Zhao XS, Fields M, Ransohoff RM, Zhou L. Imatinib attenuates skeletal muscle dystrophy in mdx mice. FASEB J 2009;23:2539-2548.
    • (2009) FASEB J , vol.23 , pp. 2539-2548
    • Huang, P.1    Zhao, X.S.2    Fields, M.3    Ransohoff, R.M.4    Zhou, L.5


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.