Myotonic dystrophy transgenic mice exhibit pathologic abnormalities in diaphragm neuromuscular junctions and phrenic nerves

Journal of Neuropathology and Experimental Neurology

Volumn 67, Issue 8, 2008, Pages 763-772

  Panaite, Petrica Adrian ^a   Gantelet, Emilien ^a   Kraftsik, Rudolf ^b   Gourdon, Geneviève ^c   Kuntzer, Thierry ^a   Barakat Walter, Ibtissam ^a,b  

^a LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

^b UNIVERSITY OF LAUSANNE   (Switzerland)

^c INSERM   (France)

Author keywords

Cervical motor neurons; Diaphragm neuromuscular junctions; Medullary respiratory neurons; Morphometric analysis; Myotonic dystrophy; Phrenic nerves; Respiratory failure

Indexed keywords

CHOLINERGIC RECEPTOR; REPETITIVE DNA; BUNGAROTOXIN; NEUROFILAMENT PROTEIN;

ACTION POTENTIAL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN STEM; BREATHING; CELL LOSS; CERVICAL SPINAL CORD; CONTROLLED STUDY; DENERVATION; DIAPHRAGM MUSCLE; GENOMICS; MORPHOLOGY; MORPHOMETRICS; MOTONEURON; MOUSE; MYELINATED NERVE; MYOTONIC DYSTROPHY; MYOTONIC DYSTROPHY TYPE 1; NERVE CELL NETWORK; NERVE ENDING; NEUROMUSCULAR JUNCTION DISORDER; NEUROPATHY; NEUROTRANSMISSION; NONHUMAN; NONMYELINATED NERVE; PHRENIC NERVE; POSTSYNAPTIC MEMBRANE; PRIORITY JOURNAL; RESPIRATORY FAILURE; SENSORY NERVE; TRANSGENIC MOUSE; ANIMAL; DIAPHRAGM; GENETICS; HUMAN; METABOLISM; NERVE FIBER; NEUROMUSCULAR SYNAPSE; PATHOLOGY; TRINUCLEOTIDE REPEAT;

ANIMALS; AXONS; BUNGAROTOXINS; DIAPHRAGM; HUMANS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MYOTONIC DYSTROPHY; NEUROFILAMENT PROTEINS; NEUROMUSCULAR JUNCTION; PHRENIC NERVE; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 52249113545     PISSN: 00223069     EISSN: None     Source Type: Journal    
DOI: 10.1097/NEN.0b013e318180ec64     Document Type: Article

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