Peripheral neuropathy is linked to a severe form of myotonic dystrophy in transgenic mice

Journal of Neuropathology and Experimental Neurology

Volumn 70, Issue 8, 2011, Pages 678-685

  Panaite, Petrica Adrian ^a   Kielar, Marie ^a   Kraftsik, Rudolf ^b   Gourdon, Geneviève ^c   Kuntzer, Thierry ^a   Barakat Walter, Ibtissam ^a,b  

^a LAUSANNE UNIVERSITY HOSPITAL   (Switzerland)

^b UNIVERSITY OF LAUSANNE   (Switzerland)

^c INSERM   (France)

Author keywords

Compound muscle action potential; DMSXL transgenic mice; Motor neuropathy; Myotonic dystrophy; Neuromuscular junctions; Physical disector method

Indexed keywords

CYTOSINE; GUANINE; THYMINE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ELECTROPHYSIOLOGY; HINDLIMB; HISTOPATHOLOGY; LUMBAR SPINAL CORD; MORPHOMETRICS; MOTONEURON; MOUSE; MUSCLE ACTION POTENTIAL; MYOTONIC DYSTROPHY; NERVE CONDUCTION; NERVE FUNCTION; NEUROMUSCULAR SYNAPSE; NEUROPATHY; NONHUMAN; NONMYELINATED NERVE; PERIPHERAL NERVE; PERIPHERAL NEUROPATHY; PRIORITY JOURNAL; SCIATIC NERVE; TRINUCLEOTIDE REPEAT;

ANIMALS; BUNGAROTOXINS; DISEASE MODELS, ANIMAL; ELECTROMYOGRAPHY; EVOKED POTENTIALS, MOTOR; HINDLIMB; HUMANS; MICE; MICE, TRANSGENIC; MOTOR NEURONS; MUSCLE, SKELETAL; MYOTONIC DYSTROPHY; NERVE FIBERS, MYELINATED; NEURAL CONDUCTION; NEUROFILAMENT PROTEINS; NEUROMUSCULAR JUNCTION; PROTEIN-SERINE-THREONINE KINASES; SCIATIC NEUROPATHY; SPINAL CORD; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 79961024150     PISSN: 00223069     EISSN: 15546578     Source Type: Journal    
DOI: 10.1097/NEN.0b013e3182260939     Document Type: Article

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