Transcomplementation by a truncation mutant of cystic fibrosis transmembrane conductance regulator (CFTR) EnhancesδF508 processing through a biomolecular interaction

Journal of Biological Chemistry

Volumn 288, Issue 15, 2013, Pages 10505-10512

  Cebotaru, Liudmila ^a,b   Woodward, Owen ^b   Cebotaru, Valeriu ^b   Guggino, William B ^b  

^a JOHNS HOPKINS UNIVERSITY   (United States)

^b JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIMOLECULAR INTERACTIONS; BIOMOLECULAR INTERACTIONS; CHANNEL FUNCTIONS; CHLORIDE CHANNELS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATORS; IMMUNOPRECIPITATIONS; TRANSMEMBRANE SEGMENTS; TRUNCATION MUTANTS;

CHLORINE COMPOUNDS; ELECTROPHYSIOLOGY; EXPERIMENTS; PROTEINS;

BIOLOGICAL MEMBRANES;

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; PARVOVIRUS VECTOR;

ANIMAL CELL; ARTICLE; CHLORIDE CURRENT; CONTROLLED STUDY; DRUG EFFECT; GENETIC COMPLEMENTATION; HUMAN; HUMAN CELL; MOLECULAR INTERACTION; MUTANT; NONHUMAN; PRIORITY JOURNAL; PROTEIN PROCESSING; VIRAL GENE DELIVERY SYSTEM; VIRAL GENE THERAPY;

AMINO ACID SEQUENCE; ANIMALS; CERCOPITHECUS AETHIOPS; CHO CELLS; COS CELLS; CRICETINAE; CRICETULUS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DEPENDOVIRUS; GENETIC COMPLEMENTATION TEST; GENETIC THERAPY; GENETIC VECTORS; HUMANS; MUTATION, MISSENSE; SEQUENCE DELETION;

EID: 84876239115     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M112.420489     Document Type: Article

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