A truncated CFTR protein rescues endogenous ΔF508-CFTR and corrects chloride transport in mice

FASEB Journal

Volumn 23, Issue 11, 2009, Pages 3743-3751

  Cormet Boyaka, Estelle ^a   Hong, Jeong S ^b   Berdiev, Bakhram K ^b   Fortenberry, James A ^c   Rennolds, Jessica ^a   Clancy, J P ^d   Benos, Dale J ^b   Boyaka, Prosper N ^a   Sorscher, Eric J ^c  

^a OHIO STATE UNIVERSITY   (United States)

^b UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^c University of Alabama at Birmingham   (United States)

^d University of Alabama at Birmingham   (United States)

Author keywords

Cystic fibrosis; In vivo rescue; Processing; Transcomplementation

Indexed keywords

ADENOVIRUS VECTOR; CHLORIDE CHANNEL; COMPLEMENTARY DNA; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELLULAR DISTRIBUTION; CHLORIDE TRANSPORT; CONTROLLED STUDY; CYSTIC FIBROSIS; ENDOPLASMIC RETICULUM; EPITHELIUM CELL; HUMAN; HUMAN CELL; MOLECULAR INTERACTION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN PROCESSING;

ADENOVIRIDAE; MUS;

ANIMALS; CELLS, CULTURED; CHLORIDES; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL CELLS; HUMANS; ION TRANSPORT; MICE; PEPTIDE FRAGMENTS;

EID: 70350550448     PISSN: 08926638     EISSN: 15306860     Source Type: Journal    
DOI: 10.1096/fj.08-127878     Document Type: Article

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