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Volumn 21, Issue 126, 2012, Pages 328-337

Pulmonary arterial hypertension associated with congenital heart disease

Author keywords

Congenital heart disease; Down's syndrome; Eisenmenger's syndrome; Pulmonary arterial hypertension

Indexed keywords

AMBRISENTAN; ANTICOAGULANT AGENT; BOSENTAN; CALCIUM CHANNEL BLOCKING AGENT; ENDOTHELIN RECEPTOR ANTAGONIST; IRON; OXYGEN; PHOSPHODIESTERASE V INHIBITOR; PLACEBO; PROSTACYCLIN; PROSTANOID; SILDENAFIL;

EID: 84870744536     PISSN: 09059180     EISSN: 16000617     Source Type: Journal    
DOI: 10.1183/09059180.00004712     Document Type: Article
Times cited : (146)

References (77)
  • 1
    • 0002569461 scopus 로고
    • Die angeborenen Defecte der Kammerscheidewand des Herzens
    • Eisenmenger V. Die angeborenen Defecte der Kammerscheidewand des Herzens. Z Klin Med 1897; 32: 1-28.
    • (1897) Z Klin Med , vol.32 , pp. 1-28
    • Eisenmenger, V.1
  • 2
    • 70449220431 scopus 로고
    • The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. I
    • Wood P. The Eisenmenger syndrome or pulmonary hypertension with reversed central shunt. I. Br Med J 1958; 2: 701-709.
    • (1958) Br Med J , vol.2 , pp. 701-709
    • Wood, P.1
  • 3
    • 70049112901 scopus 로고    scopus 로고
    • Guidelines for the diagnosis and treatment of pulmonary hypertension: The Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS), endorsed by the International Society of Heart and Lung Transplantation (ISHLT)
    • Galie' N, Hoeper MM, Humbert M, et al. Guidelines for the diagnosis and treatment of pulmonary hypertension: the Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS), endorsed by the International Society of Heart and Lung Transplantation (ISHLT). Eur Heart J 2009; 30: 2493-2537.
    • (2009) Eur Heart J , vol.30 , pp. 2493-2537
    • Galie', N.1    Hoeper, M.M.2    Humbert, M.3
  • 4
    • 43749107536 scopus 로고    scopus 로고
    • Management of pulmonary arterial hypertension associated with congenital systemic-topulmonary shunts and Eisenmenger's syndrome
    • Galie' N, Manes A, Palazzini M, et al. Management of pulmonary arterial hypertension associated with congenital systemic-topulmonary shunts and Eisenmenger's syndrome. Drugs 2008; 68: 1049-1066.
    • (2008) Drugs , vol.68 , pp. 1049-1066
    • Galie', N.1    Manes, A.2    Palazzini, M.3
  • 5
    • 79959742137 scopus 로고    scopus 로고
    • Outcomes of hospitalization in adults in the United States with atrial septal defect, ventricular septal defect, and atrioventricular septal defect
    • Rodriguez FH 3rd, Moodie DS, Parekh DR, et al. Outcomes of hospitalization in adults in the United States with atrial septal defect, ventricular septal defect, and atrioventricular septal defect. Am J Cardiol 2011; 108: 290-293.
    • (2011) Am J Cardiol , vol.108 , pp. 290-293
    • Rodriguez III, F.H.1    Moodie, D.S.2    Parekh, D.R.3
  • 6
    • 79960585821 scopus 로고    scopus 로고
    • Diagnosis of pulmonary hypertension in the congenital heart disease adult population impact on outcomes
    • Lowe BS, Therrien J, Ionescu-Ittu R, et al. Diagnosis of pulmonary hypertension in the congenital heart disease adult population impact on outcomes. J Am Coll Cardiol 2011; 58: 538-546.
    • (2011) J Am Coll Cardiol , vol.58 , pp. 538-546
    • Lowe, B.S.1    Therrien, J.2    Ionescu-Ittu, R.3
  • 7
    • 0036720702 scopus 로고    scopus 로고
    • Grown-up congenital heart (GUCH) disease: Current needs and provision of service for adolescents and adults with congenital heart disease in the UK
    • Report of the British Cardiac Society Working Party
    • Report of the British Cardiac Society Working Party. Grown-up congenital heart (GUCH) disease: current needs and provision of service for adolescents and adults with congenital heart disease in the UK. Heart 2002; 88: Suppl. 1, i1-i14.
    • (2002) Heart , vol.88 , Issue.SUPPL. 1
  • 8
    • 33847287734 scopus 로고    scopus 로고
    • Pulmonary vascular disease in adults with congenital heart disease
    • Diller GP, Gatzoulis MA. Pulmonary vascular disease in adults with congenital heart disease. Circulation 2007; 115: 1039-1050.
    • (2007) Circulation , vol.115 , pp. 1039-1050
    • Diller, G.P.1    Gatzoulis, M.A.2
  • 9
    • 69249154305 scopus 로고    scopus 로고
    • The Belgian Eisenmenger syndrome registry: Implications for treatment strategies
    • Van de Bruaene A, Delcroix M, Pasquet A, et al. The Belgian Eisenmenger syndrome registry: implications for treatment strategies? Acta Cardiol 2009; 64: 447-453.
    • (2009) Acta Cardiol , vol.64 , pp. 447-453
    • van de Bruaene, A.1    Delcroix, M.2    Pasquet, A.3
  • 10
    • 0034719427 scopus 로고    scopus 로고
    • Congenital heart disease in adults: First of two parts
    • Brickner ME, Hillis LD, Lange RA. Congenital heart disease in adults: first of two parts. N Engl J Med 2000; 342: 256-263.
    • (2000) N Engl J Med , vol.342 , pp. 256-263
    • Brickner, M.E.1    Hillis, L.D.2    Lange, R.A.3
  • 11
    • 79960054631 scopus 로고    scopus 로고
    • Recommendations for improving the quality of the interdisciplinary medical care of grown-ups with congenital heart disease (GUCH)
    • Kaemmerer H, Bauer U, de Haan F, et al. Recommendations for improving the quality of the interdisciplinary medical care of grown-ups with congenital heart disease (GUCH). Int J Cardiol 2011; 150: 59-64.
    • (2011) Int J Cardiol , vol.150 , pp. 59-64
    • Kaemmerer, H.1    Bauer, U.2    de Haan, F.3
  • 12
    • 33846220206 scopus 로고    scopus 로고
    • Congenital heart disease in the general population: Changing prevalence and age distribution
    • Marelli AJ, Mackie AS, Ionescu-Ittu R, et al. Congenital heart disease in the general population: changing prevalence and age distribution. Circulation 2007; 115: 163-172.
    • (2007) Circulation , vol.115 , pp. 163-172
    • Marelli, A.J.1    Mackie, A.S.2    Ionescu-Ittu, R.3
  • 13
    • 77953302009 scopus 로고    scopus 로고
    • Pulmonary hypertension associated with congenital heart disease: Pulmonary vascular disease: The global perspective
    • Adatia I, Kothari SS, Feinstein JA. Pulmonary hypertension associated with congenital heart disease: pulmonary vascular disease: the global perspective. Chest 2010; 137: Suppl. 6, 52S-61S.
    • (2010) Chest , vol.137 , Issue.SUPPL. 6
    • Adatia, I.1    Kothari, S.S.2    Feinstein, J.A.3
  • 14
    • 34447249704 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in congenital heart disease: An epidemiologic perspective from a Dutch registry
    • Duffels MG, Engelfriet PM, Berger RM, et al. Pulmonary arterial hypertension in congenital heart disease: an epidemiologic perspective from a Dutch registry. Int J Cardiol 2007; 120: 198-204.
    • (2007) Int J Cardiol , vol.120 , pp. 198-204
    • Duffels, M.G.1    Engelfriet, P.M.2    Berger, R.M.3
  • 15
    • 33646269035 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in France: Results from a national registry
    • Humbert M, Sitbon O, Chaouat A, et al. Pulmonary arterial hypertension in France: results from a national registry. Am J Respir Crit Care Med 2006; 173: 1023-1030.
    • (2006) Am J Respir Crit Care Med , vol.173 , pp. 1023-1030
    • Humbert, M.1    Sitbon, O.2    Chaouat, A.3
  • 16
    • 34249316235 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in adults born with a heart septal defect: The Euro Heart Survey on adult congenital heart disease
    • Engelfriet PM, Duffels MG, Mö ller T, et al. Pulmonary arterial hypertension in adults born with a heart septal defect: the Euro Heart Survey on adult congenital heart disease. Heart 2007; 93: 682-687.
    • (2007) Heart , vol.93 , pp. 682-687
    • Engelfriet, P.M.1    Duffels, M.G.2    Mö ller, T.3
  • 17
    • 60449104617 scopus 로고    scopus 로고
    • Eisenmenger syndrome a clinical perspective in a new therapeutic era of pulmonary arterial hypertension
    • Beghetti M, Galie' N. Eisenmenger syndrome a clinical perspective in a new therapeutic era of pulmonary arterial hypertension. J Am Coll Cardiol 2009; 53: 733-740.
    • (2009) J Am Coll Cardiol , vol.53 , pp. 733-740
    • Beghetti, M.1    Galie', N.2
  • 18
  • 20
    • 33745792342 scopus 로고    scopus 로고
    • Presentation, survival prospects and predictors of death in Eisenmenger's syndrome: A combined retrospective and case-control study
    • Diller GP, Dimopoulos K, Broberg CS, et al. Presentation, survival prospects and predictors of death in Eisenmenger's syndrome: a combined retrospective and case-control study. Eur Heart J 2006; 27: 1737-1742.
    • (2006) Eur Heart J , vol.27 , pp. 1737-1742
    • Diller, G.P.1    Dimopoulos, K.2    Broberg, C.S.3
  • 21
    • 80054901197 scopus 로고    scopus 로고
    • Pediatric pulmonary hypertension in the Netherlands: Epidemiology and characterization during the period 1991 to 2005
    • van Loon RL, Roofthooft MT, Hillege HL, et al. Pediatric pulmonary hypertension in the Netherlands: epidemiology and characterization during the period 1991 to 2005. Circulation 2011; 124: 1755-1764.
    • (2011) Circulation , vol.124 , pp. 1755-1764
    • van Loon, R.L.1    Roofthooft, M.T.2    Hillege, H.L.3
  • 22
    • 4644290657 scopus 로고    scopus 로고
    • Treatment of pulmonary arterial hypertension
    • Humbert M, Sitbon O, Simonneau G. Treatment of pulmonary arterial hypertension. N Engl J Med 2004; 351: 1425-1436.
    • (2004) N Engl J Med , vol.351 , pp. 1425-1436
    • Humbert, M.1    Sitbon, O.2    Simonneau, G.3
  • 23
    • 0036899034 scopus 로고    scopus 로고
    • Pulmonary hypertension in the young
    • Haworth SG. Pulmonary hypertension in the young. Heart 2002; 88: 658-664.
    • (2002) Heart , vol.88 , pp. 658-664
    • Haworth, S.G.1
  • 24
    • 50249179722 scopus 로고    scopus 로고
    • Outcomes in patients with pulmonary hypertension undergoing percutaneous atrial septal defect closure
    • Balint OH, Samman A, Haberer K, et al. Outcomes in patients with pulmonary hypertension undergoing percutaneous atrial septal defect closure. Heart 2008; 94: 1189-1193.
    • (2008) Heart , vol.94 , pp. 1189-1193
    • Balint, O.H.1    Samman, A.2    Haberer, K.3
  • 25
    • 14044255902 scopus 로고    scopus 로고
    • The remarkable right ventricle of patients with Eisenmenger syndrome
    • Hopkins WE. The remarkable right ventricle of patients with Eisenmenger syndrome. Coron Artery Dis 2005; 16: 19-25.
    • (2005) Coron Artery Dis , vol.16 , pp. 19-25
    • Hopkins, W.E.1
  • 26
    • 0036149441 scopus 로고    scopus 로고
    • Severe pulmonary hypertension without right ventricular failure: The unique hearts of patients with Eisenmenger syndrome
    • Hopkins WE, Waggoner AD. Severe pulmonary hypertension without right ventricular failure: the unique hearts of patients with Eisenmenger syndrome. Am J Cardiol 2002; 89: 34-38.
    • (2002) Am J Cardiol , vol.89 , pp. 34-38
    • Hopkins, W.E.1    Waggoner, A.D.2
  • 27
    • 84857790009 scopus 로고    scopus 로고
    • Bosentan-sildenafil association in patients with congenital heart disease-related pulmonary arterial hypertension and Eisenmenger physiology
    • D'Alto M, Romeo E, Argiento P, et al. Bosentan-sildenafil association in patients with congenital heart disease-related pulmonary arterial hypertension and Eisenmenger physiology. Int J Cardiol 2012; 155: 378-382.
    • (2012) Int J Cardiol , vol.155 , pp. 378-382
    • D'Alto, M.1    Romeo, E.2    Argiento, P.3
  • 28
    • 80051815262 scopus 로고    scopus 로고
    • Identifying high risk in adults with congenital heart disease and atrial arrhythmias
    • Yap SC, Harris L, Chauhan VS, et al. Identifying high risk in adults with congenital heart disease and atrial arrhythmias. Am J Cardiol 2011; 108: 723-728.
    • (2011) Am J Cardiol , vol.108 , pp. 723-728
    • Yap, S.C.1    Harris, L.2    Chauhan, V.S.3
  • 29
    • 33845804255 scopus 로고    scopus 로고
    • Blood is thicker than water: The management of hyperviscosity in adults with cyanotic heart disease
    • DeFilippis AP, Law K, Curtin S, et al. Blood is thicker than water: the management of hyperviscosity in adults with cyanotic heart disease. Cardiol Rev 2007; 15: 31-34.
    • (2007) Cardiol Rev , vol.15 , pp. 31-34
    • DeFilippis, A.P.1    Law, K.2    Curtin, S.3
  • 30
    • 23844535863 scopus 로고    scopus 로고
    • Exercise intolerance in adult congenital heart disease: Comparative severity, correlates, and prognostic implication
    • Diller GP, Dimopoulos K, Okonko D, et al. Exercise intolerance in adult congenital heart disease: comparative severity, correlates, and prognostic implication. Circulation 2005; 112: 828-835.
    • (2005) Circulation , vol.112 , pp. 828-835
    • Diller, G.P.1    Dimopoulos, K.2    Okonko, D.3
  • 31
    • 0032484655 scopus 로고    scopus 로고
    • How to manage the Eisenmenger syndrome
    • Somerville J. How to manage the Eisenmenger syndrome. Int J Cardiol 1998; 63: 1-8.
    • (1998) Int J Cardiol , vol.63 , pp. 1-8
    • Somerville, J.1
  • 32
    • 0032402278 scopus 로고    scopus 로고
    • Eisenmenger syndrome. Factors relating to deterioration and death
    • Daliento L, Somerville J, Presbitero P, et al. Eisenmenger syndrome. Factors relating to deterioration and death. Eur Heart J 1998; 19: 1845-1855.
    • (1998) Eur Heart J , vol.19 , pp. 1845-1855
    • Daliento, L.1    Somerville, J.2    Presbitero, P.3
  • 33
    • 84861814180 scopus 로고    scopus 로고
    • Reference values for exercise limitations among adults with congenital heart disease. Relation to activities of daily life-single centre experience and review of published data
    • Kempny A, Dimopoulos K, Uebing A, et al. Reference values for exercise limitations among adults with congenital heart disease. Relation to activities of daily life-single centre experience and review of published data. Eur Heart J 2012; 33: 1386-1396.
    • (2012) Eur Heart J , vol.33 , pp. 1386-1396
    • Kempny, A.1    Dimopoulos, K.2    Uebing, A.3
  • 34
    • 55149086987 scopus 로고    scopus 로고
    • Pulmonary arterial hypertension in adults with congenital heart disease: Distinct differences from other causes of pulmonary arterial hypertension and management implications
    • Dimopoulos K, Giannakoulas G, Wort SJ, et al. Pulmonary arterial hypertension in adults with congenital heart disease: distinct differences from other causes of pulmonary arterial hypertension and management implications. Curr Opin Cardiol 2008; 23: 545-554.
    • (2008) Curr Opin Cardiol , vol.23 , pp. 545-554
    • Dimopoulos, K.1    Giannakoulas, G.2    Wort, S.J.3
  • 35
    • 34247364400 scopus 로고    scopus 로고
    • Limitations of the New York Heart Association functional classification system and selfreported walking distances in chronic heart failure
    • Raphael C, Briscoe C, Davies J, et al. Limitations of the New York Heart Association functional classification system and selfreported walking distances in chronic heart failure. Heart 2007; 93: 476-482.
    • (2007) Heart , vol.93 , pp. 476-482
    • Raphael, C.1    Briscoe, C.2    Davies, J.3
  • 36
    • 0035508410 scopus 로고    scopus 로고
    • Nocturnal oxygen therapy in patients with the Eisenmenger syndrome
    • Sandoval J, Aguirre JS, Pulido T, et al. Nocturnal oxygen therapy in patients with the Eisenmenger syndrome. Am J Respir Crit Care Med 2001; 164: 1682-1687.
    • (2001) Am J Respir Crit Care Med , vol.164 , pp. 1682-1687
    • Sandoval, J.1    Aguirre, J.S.2    Pulido, T.3
  • 37
    • 34547577592 scopus 로고    scopus 로고
    • Pulmonary arterial thrombosis in Eisenmenger syndrome is associated with biventricular dysfunction and decreased pulmonary flow velocity
    • Broberg CS, Ujita M, Prasad S, et al. Pulmonary arterial thrombosis in Eisenmenger syndrome is associated with biventricular dysfunction and decreased pulmonary flow velocity. J Am Coll Cardiol 2007; 50: 634-642.
    • (2007) J Am Coll Cardiol , vol.50 , pp. 634-642
    • Broberg, C.S.1    Ujita, M.2    Prasad, S.3
  • 38
    • 78649813429 scopus 로고    scopus 로고
    • ESC guidelines for the management of grown-up congenital heart disease (new version 2010)
    • Baumgartner H, Bonhoeffer P, De Groot N, et al. ESC guidelines for the management of grown-up congenital heart disease (new version 2010). Eur Heart J 2010; 31: 2915-2957.
    • (2010) Eur Heart J , vol.31 , pp. 2915-2957
    • Baumgartner, H.1    Bonhoeffer, P.2    de Groot, N.3
  • 39
    • 81855190691 scopus 로고    scopus 로고
    • Iron deficiency is associated with adverse outcome in Eisenmenger patients
    • Van De Bruaene A, Delcroix M, Pasquet A, et al. Iron deficiency is associated with adverse outcome in Eisenmenger patients. Eur Heart J 2011; 32: 2790-2799.
    • (2011) Eur Heart J , vol.32 , pp. 2790-2799
    • van de Bruaene, A.1    Delcroix, M.2    Pasquet, A.3
  • 40
    • 80052695805 scopus 로고    scopus 로고
    • Replacement therapy for iron deficiency improves exercise capacity and quality of life in patients with cyanotic congenital heart disease and/or the Eisenmenger syndrome
    • Tay EL, Peset A, Papaphylactou M, et al. Replacement therapy for iron deficiency improves exercise capacity and quality of life in patients with cyanotic congenital heart disease and/or the Eisenmenger syndrome. Int J Cardiol 2011; 151: 307-312.
    • (2011) Int J Cardiol , vol.151 , pp. 307-312
    • Tay, E.L.1    Peset, A.2    Papaphylactou, M.3
  • 41
    • 53349099575 scopus 로고    scopus 로고
    • Embolisation of systemicto-pulmonary collaterals in patients with the Eisenmenger reaction presenting with haemoptysis
    • Mamas MA, Clarke B, Mahadevan VS. Embolisation of systemicto-pulmonary collaterals in patients with the Eisenmenger reaction presenting with haemoptysis. Cardiol Young 2008; 18: 528-531.
    • (2008) Cardiol Young , vol.18 , pp. 528-531
    • Mamas, M.A.1    Clarke, B.2    Mahadevan, V.S.3
  • 42
    • 33746206340 scopus 로고    scopus 로고
    • Bosentan therapy in patients with Eisenmenger syndrome: A multicenter, double-blind, randomized, placebo-controlled study
    • Galie' N, Beghetti M, Gatzoulis MA, et al. Bosentan therapy in patients with Eisenmenger syndrome: a multicenter, double-blind, randomized, placebo-controlled study. Circulation 2006; 114: 48-54.
    • (2006) Circulation , vol.114 , pp. 48-54
    • Galie', N.1    Beghetti, M.2    Gatzoulis, M.A.3
  • 43
    • 43949107864 scopus 로고    scopus 로고
    • Longer-term bosentan therapy improves functional capacity in Eisenmenger syndrome: Results of the BREATHE-5 open-label extension study
    • Gatzoulis MA, Beghetti M, Galie' N, et al. Longer-term bosentan therapy improves functional capacity in Eisenmenger syndrome: results of the BREATHE-5 open-label extension study. Int J Cardiol 2008; 127: 27-32.
    • (2008) Int J Cardiol , vol.127 , pp. 27-32
    • Gatzoulis, M.A.1    Beghetti, M.2    Galie', N.3
  • 44
    • 77957860787 scopus 로고    scopus 로고
    • Atrial septal defects versus ventricular septal defects in BREATHE-5, a placebo-controlled study of pulmonary arterial hypertension related to Eisenmenger's syndrome: A subgroup analysis
    • Berger RM, Beghetti M, Galie' N, et al. Atrial septal defects versus ventricular septal defects in BREATHE-5, a placebo-controlled study of pulmonary arterial hypertension related to Eisenmenger's syndrome: a subgroup analysis. Int J Cardiol 2010; 144: 373-378.
    • (2010) Int J Cardiol , vol.144 , pp. 373-378
    • Berger, R.M.1    Beghetti, M.2    Galie', N.3
  • 45
    • 34547178938 scopus 로고    scopus 로고
    • Long-term safety, tolerability and efficacy of bosentan in adults with pulmonary arterial hypertension associated with congenital heart disease
    • Diller GP, Dimopoulos K, Kaya MG, et al. Long-term safety, tolerability and efficacy of bosentan in adults with pulmonary arterial hypertension associated with congenital heart disease. Heart 2007; 93: 974-976.
    • (2007) Heart , vol.93 , pp. 974-976
    • Diller, G.P.1    Dimopoulos, K.2    Kaya, M.G.3
  • 46
    • 70349247783 scopus 로고    scopus 로고
    • Longterm bosentan treatment of complex congenital heart disease and Eisenmenger's syndrome
    • Di{dotless}́az-Caraballo E, González-Garci{dotless}́a AE, Reñ ones M, et al. Longterm bosentan treatment of complex congenital heart disease and Eisenmenger's syndrome. Rev Esp Cardiol 2009; 62: 1046-1049.
    • (2009) Rev Esp Cardiol , vol.62 , pp. 1046-1049
    • Díaz-Caraballo, E.1    González-García, A.E.2    Reñ ones, M.3
  • 47
    • 80255123462 scopus 로고    scopus 로고
    • Efficacy and safety of bosentan for pulmonary arterial hypertension in adults with congenital heart disease
    • Monfredi O, Griffiths L, Clarke B, et al. Efficacy and safety of bosentan for pulmonary arterial hypertension in adults with congenital heart disease. Am J Cardiol 2011; 108: 1483-1488.
    • (2011) Am J Cardiol , vol.108 , pp. 1483-1488
    • Monfredi, O.1    Griffiths, L.2    Clarke, B.3
  • 48
    • 84884211344 scopus 로고    scopus 로고
    • Therapy for pulmonary arterial hypertension due to congenital heart disease and Down's syndrome
    • [Epub ahead of print DOI: 10.1016/ j.ijcard.2011.07.009]
    • D'Alto M, Romeo E, Argiento P, et al. Therapy for pulmonary arterial hypertension due to congenital heart disease and Down's syndrome. Int J Cardiol 2011; [Epub ahead of print DOI: 10.1016/ j.ijcard.2011.07.009].
    • (2011) Int J Cardiol
    • D'Alto, M.1    Romeo, E.2    Argiento, P.3
  • 49
    • 84875218879 scopus 로고    scopus 로고
    • Prolonged beneficial effect of bosentan treatment and 4-year survival rates in adult patients with pulmonary arterial hypertension associated with congenital heart disease
    • [Epub ahead of print DOI: 10.1016/ j.ijcard.2011.06.064]
    • Vis JC, Duffels MG, Mulder P, et al. Prolonged beneficial effect of bosentan treatment and 4-year survival rates in adult patients with pulmonary arterial hypertension associated with congenital heart disease. Int J Cardiol 2011; [Epub ahead of print DOI: 10.1016/ j.ijcard.2011.06.064].
    • (2011) Int J Cardiol
    • Vis, J.C.1    Duffels, M.G.2    Mulder, P.3
  • 50
    • 84860466195 scopus 로고    scopus 로고
    • Long-term effect of bosentan therapy on cardiac function and symptomatic benefits in adult patients with Eisenmenger syndrome
    • Kaya MG, Lam YY, Erer B, et al. Long-term effect of bosentan therapy on cardiac function and symptomatic benefits in adult patients with Eisenmenger syndrome. J Card Fail 2012; 18: 379-384.
    • (2012) J Card Fail , vol.18 , pp. 379-384
    • Kaya, M.G.1    Lam, Y.Y.2    Erer, B.3
  • 51
    • 0033551155 scopus 로고    scopus 로고
    • Long-term prostacyclin for pulmonary hypertension with associated congenital heart defects
    • Rosenzweig EB, Kerstein D, Barst RJ. Long-term prostacyclin for pulmonary hypertension with associated congenital heart defects. Circulation 1999; 99: 1858-1865.
    • (1999) Circulation , vol.99 , pp. 1858-1865
    • Rosenzweig, E.B.1    Kerstein, D.2    Barst, R.J.3
  • 52
    • 78449232122 scopus 로고    scopus 로고
    • Impact of sildenafil therapy on pulmonary arterial hypertension in adults with congenital heart disease
    • Lu XL, Xiong CM, Shan GL, et al. Impact of sildenafil therapy on pulmonary arterial hypertension in adults with congenital heart disease. Cardiovasc Ther 2010; 28: 350-355.
    • (2010) Cardiovasc Ther , vol.28 , pp. 350-355
    • Lu, X.L.1    Xiong, C.M.2    Shan, G.L.3
  • 53
    • 79958157049 scopus 로고    scopus 로고
    • Quality of life and functional capacity can be improved in patients with Eisenmenger syndrome with oral sildenafil therapy
    • Tay EL, Papaphylactou M, Diller GP, et al. Quality of life and functional capacity can be improved in patients with Eisenmenger syndrome with oral sildenafil therapy. Int J Cardiol 2011; 149: 372-376.
    • (2011) Int J Cardiol , vol.149 , pp. 372-376
    • Tay, E.L.1    Papaphylactou, M.2    Diller, G.P.3
  • 54
    • 80055114971 scopus 로고    scopus 로고
    • Oral sildenafil treatment for Eisenmenger syndrome: A prospective, open-label, multicentre study
    • Zhang ZN, Jiang X, Zhang R, et al. Oral sildenafil treatment for Eisenmenger syndrome: a prospective, open-label, multicentre study. Heart 2011; 97: 1876-1881.
    • (2011) Heart , vol.97 , pp. 1876-1881
    • Zhang, Z.N.1    Jiang, X.2    Zhang, R.3
  • 55
    • 34447550122 scopus 로고    scopus 로고
    • Effects of chronic sildenafil in patients with Eisenmenger syndrome versus idiopathic pulmonary arterial hypertension
    • Chau EM, Fan KY, Chow WH. Effects of chronic sildenafil in patients with Eisenmenger syndrome versus idiopathic pulmonary arterial hypertension. Int J Cardiol 2007; 120: 301-305.
    • (2007) Int J Cardiol , vol.120 , pp. 301-305
    • Chau, E.M.1    Fan, K.Y.2    Chow, W.H.3
  • 56
    • 80051549897 scopus 로고    scopus 로고
    • The efficacy and safety of sildenafil in patients with pulmonary arterial hypertension associated with the different types of congenital heart disease
    • Zeng WJ, Lu XL, Xiong CM, et al. The efficacy and safety of sildenafil in patients with pulmonary arterial hypertension associated with the different types of congenital heart disease. Clin Cardiol 2011; 34: 513-518.
    • (2011) Clin Cardiol , vol.34 , pp. 513-518
    • Zeng, W.J.1    Lu, X.L.2    Xiong, C.M.3
  • 57
    • 33750553816 scopus 로고    scopus 로고
    • Phosphodiesterase-5 inhibitor in Eisenmenger syndrome: A preliminary observational study
    • Mukhopadhyay S, Sharma M, Ramakrishnan S, et al. Phosphodiesterase-5 inhibitor in Eisenmenger syndrome: a preliminary observational study. Circulation 2006; 114: 1807-1810.
    • (2006) Circulation , vol.114 , pp. 1807-1810
    • Mukhopadhyay, S.1    Sharma, M.2    Ramakrishnan, S.3
  • 58
    • 79954609830 scopus 로고    scopus 로고
    • Ambrisentan for pulmonary arterial hypertension due to congenital heart disease
    • Zuckerman WA, Leaderer D, Rowan CA, et al. Ambrisentan for pulmonary arterial hypertension due to congenital heart disease. Am J Cardiol 2011; 107: 1381-1385.
    • (2011) Am J Cardiol , vol.107 , pp. 1381-1385
    • Zuckerman, W.A.1    Leaderer, D.2    Rowan, C.A.3
  • 59
    • 77952019637 scopus 로고    scopus 로고
    • Combination therapy with bosentan and sildenafil in Eisenmenger syndrome: A randomized, placebo-controlled, double-blinded trial
    • Iversen K, Jensen AS, Jensen TV, et al. Combination therapy with bosentan and sildenafil in Eisenmenger syndrome: a randomized, placebo-controlled, double-blinded trial. Eur Heart J 2010; 31: 1124-1131.
    • (2010) Eur Heart J , vol.31 , pp. 1124-1131
    • Iversen, K.1    Jensen, A.S.2    Jensen, T.V.3
  • 60
    • 74549213864 scopus 로고    scopus 로고
    • Improved survival among patients with Eisenmenger syndrome receiving advanced therapy for pulmonary arterial hypertension
    • Dimopoulos K, Inuzuka R, Goletto S, et al. Improved survival among patients with Eisenmenger syndrome receiving advanced therapy for pulmonary arterial hypertension. Circulation 2010; 121: 20-25.
    • (2010) Circulation , vol.121 , pp. 20-25
    • Dimopoulos, K.1    Inuzuka, R.2    Goletto, S.3
  • 61
    • 84880924617 scopus 로고    scopus 로고
    • Disease targeting therapies in patients with Eisenmenger syndrome: Response to treatment and long-term efficiency
    • [Epub ahead of print DOI: 10.1016/j.jicard.2012.02.007]
    • Diller GP, Alonso-Gonzalez R, Dimopoulos K, et al. Disease targeting therapies in patients with Eisenmenger syndrome: response to treatment and long-term efficiency. Int J Cardiol 2012; [Epub ahead of print DOI: 10.1016/j.jicard.2012.02.007].
    • (2012) Int J Cardiol
    • Diller, G.P.1    Alonso-Gonzalez, R.2    Dimopoulos, K.3
  • 62
    • 84856364845 scopus 로고    scopus 로고
    • Can "inoperable" congenital heart defects become operable in patients with pulmonary arterial hypertension? Dream or reality
    • Beghetti M, Galie' N, Bonnet D. Can "inoperable" congenital heart defects become operable in patients with pulmonary arterial hypertension? Dream or reality? Congenit Heart Dis 2012; 7: 3-11.
    • (2012) Congenit Heart Dis , vol.7 , pp. 3-11
    • Beghetti, M.1    Galie', N.2    Bonnet, D.3
  • 63
    • 60549112998 scopus 로고    scopus 로고
    • Circulating endothelial cells: A new candidate biomarker of irreversible pulmonary hypertension secondary to congenital heart disease
    • Smadja DM, Gaussem P, Mauge L, et al. Circulating endothelial cells: a new candidate biomarker of irreversible pulmonary hypertension secondary to congenital heart disease. Circulation 2009; 119: 374-381.
    • (2009) Circulation , vol.119 , pp. 374-381
    • Smadja, D.M.1    Gaussem, P.2    Mauge, L.3
  • 64
    • 71249104673 scopus 로고    scopus 로고
    • Trends in Down's syndrome live births and antenatal diagnoses in England and Wales from 1989 to 2008: Analysis of data from the National Down Syndrome Cytogenetic Register
    • Morris JK, Alberman E. Trends in Down's syndrome live births and antenatal diagnoses in England and Wales from 1989 to 2008: analysis of data from the National Down Syndrome Cytogenetic Register. BMJ 2009; 339: b3794.
    • (2009) BMJ , vol.339
    • Morris, J.K.1    Alberman, E.2
  • 65
    • 78649316663 scopus 로고    scopus 로고
    • Clinical practice. The care of children with Down syndrome
    • Weijerman ME, de Winter JP. Clinical practice. The care of children with Down syndrome. Eur J Pediatr 2010; 169: 1445-1452.
    • (2010) Eur J Pediatr , vol.169 , pp. 1445-1452
    • Weijerman, M.E.1    de Winter, J.P.2
  • 66
    • 0345490121 scopus 로고
    • The incidence of Mongolism in the general population
    • Penrose LS. The incidence of Mongolism in the general population. J Ment Sci 1949; 95: 685-688.
    • (1949) J Ment Sci , vol.95 , pp. 685-688
    • Penrose, L.S.1
  • 67
    • 0019942204 scopus 로고
    • Longevity and mortality in Down's syndrome
    • Thase ME. Longevity and mortality in Down's syndrome. J Ment Defic Res 1982; 26: 177-192.
    • (1982) J Ment Defic Res , vol.26 , pp. 177-192
    • Thase, M.E.1
  • 68
    • 0344837278 scopus 로고    scopus 로고
    • The changing survival profile of people with Down's syndrome: Implications for genetic counselling
    • Glasson EJ, Sullivan SG, Hussain R, et al. The changing survival profile of people with Down's syndrome: implications for genetic counselling. Clin Genet 2002; 62: 390-393.
    • (2002) Clin Genet , vol.62 , pp. 390-393
    • Glasson, E.J.1    Sullivan, S.G.2    Hussain, R.3
  • 69
    • 77956192047 scopus 로고    scopus 로고
    • Prevalence of congenital heart defects and persistent pulmonary hypertension of the neonate with Down syndrome
    • Weijerman ME, van Furth AM, van der Mooren MD, et al. Prevalence of congenital heart defects and persistent pulmonary hypertension of the neonate with Down syndrome. Eur J Pediatr 2010; 169: 1195-1199.
    • (2010) Eur J Pediatr , vol.169 , pp. 1195-1199
    • Weijerman, M.E.1    van Furth, A.M.2    van der Mooren, M.D.3
  • 70
    • 67849092000 scopus 로고    scopus 로고
    • Six-minute walk test in patients with Down syndrome: Validity and reproducibility
    • Vis JC, Thoonsen H, Duffels MG, et al. Six-minute walk test in patients with Down syndrome: validity and reproducibility. Arch Phys Med Rehabil 2009; 90: 1423-1427.
    • (2009) Arch Phys Med Rehabil , vol.90 , pp. 1423-1427
    • Vis, J.C.1    Thoonsen, H.2    Duffels, M.G.3
  • 71
    • 84859157810 scopus 로고    scopus 로고
    • Cardiovascular abnormalities in Down's syndrome: Spectrum, management and survival over 22 years
    • Irving CA, Chaudhari MP. Cardiovascular abnormalities in Down's syndrome: spectrum, management and survival over 22 years. Arch Dis Child 2012; 97: 326-330.
    • (2012) Arch Dis Child , vol.97 , pp. 326-330
    • Irving, C.A.1    Chaudhari, M.P.2
  • 72
    • 0034739306 scopus 로고    scopus 로고
    • Tracheal stenosis and congenital heart disease in patients with Down syndrome: Diagnostic approach and surgical options
    • Shapiro NL, Huang RY, Sangwan S, et al. Tracheal stenosis and congenital heart disease in patients with Down syndrome: diagnostic approach and surgical options. Int J Pediatr Otorhinolaryngol 2000; 54: 137-142.
    • (2000) Int J Pediatr Otorhinolaryngol , vol.54 , pp. 137-142
    • Shapiro, N.L.1    Huang, R.Y.2    Sangwan, S.3
  • 73
    • 34250820489 scopus 로고    scopus 로고
    • Increased incidence of idiopathic persistent pulmonary hypertension in Down syndrome neonates
    • Cua CL, Blankenship A, North AL, et al. Increased incidence of idiopathic persistent pulmonary hypertension in Down syndrome neonates. Pediatr Cardiol 2007; 28: 250-254.
    • (2007) Pediatr Cardiol , vol.28 , pp. 250-254
    • Cua, C.L.1    Blankenship, A.2    North, A.L.3
  • 74
    • 79958076089 scopus 로고    scopus 로고
    • The outcome of Eisenmenger patients with trisomy 21 does not differ from patients without trisomy 21
    • Troost E, Van De Bruaene A, Lampropoulos K, et al. The outcome of Eisenmenger patients with trisomy 21 does not differ from patients without trisomy 21. Acta Cardiol 2011; 66: 293-301.
    • (2011) Acta Cardiol , vol.66 , pp. 293-301
    • Troost, E.1    van de Bruaene, A.2    Lampropoulos, K.3
  • 75
    • 3242712429 scopus 로고    scopus 로고
    • Endothelial cell function in patients with Down's syndrome
    • Cappelli-Bigazzi M, Santoro G, Battaglia C, et al. Endothelial cell function in patients with Down's syndrome. Am J Cardiol 2004; 94: 392-395.
    • (2004) Am J Cardiol , vol.94 , pp. 392-395
    • Cappelli-Bigazzi, M.1    Santoro, G.2    Battaglia, C.3
  • 76
    • 0034663734 scopus 로고    scopus 로고
    • Pulmonary vascular disease in Down's syndrome with complete atrioventricular septal defect
    • Suzuki K, Yamaki S, Mimori S, et al. Pulmonary vascular disease in Down's syndrome with complete atrioventricular septal defect. Am J Cardiol 2000; 86: 434-437.
    • (2000) Am J Cardiol , vol.86 , pp. 434-437
    • Suzuki, K.1    Yamaki, S.2    Mimori, S.3
  • 77
    • 65249164987 scopus 로고    scopus 로고
    • Effect of bosentan on exercise capacity and quality of life of adults with pulmonary arterial hypertension associated with congenital heart disease with or without Downs syndrome
    • Duffels MG, Vis JC, Rosa LE, et al. Effect of bosentan on exercise capacity and quality of life of adults with pulmonary arterial hypertension associated with congenital heart disease with or without Downs syndrome. Am J Cardiol 2009; 103: 1309-1315.
    • (2009) Am J Cardiol , vol.103 , pp. 1309-1315
    • Duffels, M.G.1    Vis, J.C.2    Rosa, L.E.3


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